104 related articles for article (PubMed ID: 10438129)
1. Developmental pattern of phenylalanine hydroxylase activity in the chicken.
Powell TL; Davis AJ; Yuan JH; Austic RE
Poult Sci; 1999 Jun; 78(6):855-60. PubMed ID: 10438129
[TBL] [Abstract][Full Text] [Related]
2. Phenylalanine requirement, imbalance, and dietary excess in one-week-old chicks: growth and phenylalanine hydroxylase activity.
Lartey FM; Austic RE
Poult Sci; 2008 Feb; 87(2):291-7. PubMed ID: 18212372
[TBL] [Abstract][Full Text] [Related]
3. Phenylalanine hydroxylase activity and expression in chicks subjected to phenylalanine imbalance or phenylalanine toxicity.
Lartey FM; Austic RE
Poult Sci; 2009 Apr; 88(4):774-83. PubMed ID: 19276420
[TBL] [Abstract][Full Text] [Related]
4. The activity of wild-type and mutant phenylalanine hydroxylase and its regulation by phenylalanine and tetrahydrobiopterin at physiological and pathological concentrations: an isothermal titration calorimetry study.
Pey AL; Martinez A
Mol Genet Metab; 2005 Dec; 86 Suppl 1():S43-53. PubMed ID: 15936235
[TBL] [Abstract][Full Text] [Related]
5. Quantification of phenylalanine hydroxylase activity by isotope-dilution liquid chromatography-electrospray ionization tandem mass spectrometry.
Heintz C; Troxler H; Martinez A; Thöny B; Blau N
Mol Genet Metab; 2012 Apr; 105(4):559-65. PubMed ID: 22300847
[TBL] [Abstract][Full Text] [Related]
6. Effect of alkaline pH on the activity of rat liver phenylalanine hydroxylase.
Parniak MA; Davis MD; Kaufman S
J Biol Chem; 1988 Jan; 263(3):1223-30. PubMed ID: 3335542
[TBL] [Abstract][Full Text] [Related]
7. Wild-type phenylalanine hydroxylase activity is enhanced by tetrahydrobiopterin supplementation in vivo: an implication for therapeutic basis of tetrahydrobiopterin-responsive phenylalanine hydroxylase deficiency.
Kure S; Sato K; Fujii K; Aoki Y; Suzuki Y; Kato S; Matsubara Y
Mol Genet Metab; 2004; 83(1-2):150-6. PubMed ID: 15464429
[TBL] [Abstract][Full Text] [Related]
8. Tetrahydrobiopterin protects phenylalanine hydroxylase activity in vivo: implications for tetrahydrobiopterin-responsive hyperphenylalaninemia.
Thöny B; Ding Z; Martínez A
FEBS Lett; 2004 Nov; 577(3):507-11. PubMed ID: 15556637
[TBL] [Abstract][Full Text] [Related]
9. Coordinate regulation of tetrahydrobiopterin turnover and phenylalanine hydroxylase activity in rat liver cells.
Mitnaul LJ; Shiman R
Proc Natl Acad Sci U S A; 1995 Jan; 92(3):885-9. PubMed ID: 7846072
[TBL] [Abstract][Full Text] [Related]
10. Developmental aspect of phenylalanine hydroxylase in the rat -- hormonal influences.
Dhondt JL; Dautrevaux M; Biserte G; Farriaux JP
Mech Ageing Dev; 1979 May; 10(3-4):219-24. PubMed ID: 222974
[TBL] [Abstract][Full Text] [Related]
11. L-[1-13C] phenylalanine breath test reflects phenylalanine hydroxylase activity of the whole liver.
Ishii Y; Suzuki S; Kohno T; Aoki M; Kohno T; Ito A; Takayama T; Asai S
J Surg Res; 2003 Jun; 112(1):38-42. PubMed ID: 12873431
[TBL] [Abstract][Full Text] [Related]
12. Radiation target analysis indicates that phenylalanine hydroxylase in rat liver extracts is a functional monomer.
Parniak MA; Davis M; Kaufman S; Kempner ES
FEBS Lett; 1999 Apr; 449(1):49-52. PubMed ID: 10225426
[TBL] [Abstract][Full Text] [Related]
13. Interaction with a monoclonal antibody alters the expression of co-operativity by phenylalanine hydroxylase from rat liver.
Parniak MA; Jennings IG; Cotton RG
Biochem J; 1989 Jan; 257(2):383-8. PubMed ID: 2930457
[TBL] [Abstract][Full Text] [Related]
14. Results of L-[1-13C]phenylalanine breath test with air isotope ratio mass spectrometry can reflect the activity of phenylalanine hydroxylase in cirrhotic rat liver.
Yan W; Xiong P; Liu Z; Huang G
Rapid Commun Mass Spectrom; 2006; 20(4):602-8. PubMed ID: 16429477
[TBL] [Abstract][Full Text] [Related]
15. Stimulation of hepatic phenylalanine hydroxylase activity but not Pah-mRNA expression upon oral loading of tetrahydrobiopterin in normal mice.
Scavelli R; Ding Z; Blau N; Haavik J; Martínez A; Thöny B
Mol Genet Metab; 2005 Dec; 86 Suppl 1():S153-5. PubMed ID: 16290004
[TBL] [Abstract][Full Text] [Related]
16. In vivo regulation of phenylalanine hydroxylase in the genetic mutant hph-1 mouse model.
Gunasekera RS; Hyland K
Mol Genet Metab; 2009 Nov; 98(3):264-72. PubMed ID: 19560382
[TBL] [Abstract][Full Text] [Related]
17. The mechanism of BH4 -responsive hyperphenylalaninemia--as it occurs in the ENU1/2 genetic mouse model.
Sarkissian CN; Ying M; Scherer T; Thöny B; Martinez A
Hum Mutat; 2012 Oct; 33(10):1464-73. PubMed ID: 22644647
[TBL] [Abstract][Full Text] [Related]
18. Expression of phenylalanine hydroxylase (PAH) in erythrogenic bone marrow does not correct hyperphenylalaninemia in Pah(enu2) mice.
Harding CO; Neff M; Jones K; Wild K; Wolff JA
J Gene Med; 2003 Nov; 5(11):984-93. PubMed ID: 14601136
[TBL] [Abstract][Full Text] [Related]
19. 7-Tetrahydrobiopterin is an uncoupled cofactor for rat hepatic phenylalanine hydroxylase.
Davis MD; Kaufman S
FEBS Lett; 1991 Jul; 285(1):17-20. PubMed ID: 2065777
[TBL] [Abstract][Full Text] [Related]
20. Recombinant human phenylalanine hydroxylase: novel regulatory and structural properties.
Kowlessur D; Citron BA; Kaufman S
Arch Biochem Biophys; 1996 Sep; 333(1):85-95. PubMed ID: 8806757
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]