176 related articles for article (PubMed ID: 10675581)
1. The neuronal Golgi apparatus is fragmented in transgenic mice expressing a mutant human SOD1, but not in mice expressing the human NF-H gene.
Stieber A; Gonatas JO; Collard J; Meier J; Julien J; Schweitzer P; Gonatas NK
J Neurol Sci; 2000 Feb; 173(1):63-72. PubMed ID: 10675581
[TBL] [Abstract][Full Text] [Related]
2. The Golgi apparatus of spinal cord motor neurons in transgenic mice expressing mutant Cu,Zn superoxide dismutase becomes fragmented in early, preclinical stages of the disease.
Mourelatos Z; Gonatas NK; Stieber A; Gurney ME; Dal Canto MC
Proc Natl Acad Sci U S A; 1996 May; 93(11):5472-7. PubMed ID: 8643599
[TBL] [Abstract][Full Text] [Related]
3. Aggregates of mutant protein appear progressively in dendrites, in periaxonal processes of oligodendrocytes, and in neuronal and astrocytic perikarya of mice expressing the SOD1(G93A) mutation of familial amyotrophic lateral sclerosis.
Stieber A; Gonatas JO; Gonatas NK
J Neurol Sci; 2000 Aug; 177(2):114-23. PubMed ID: 10980307
[TBL] [Abstract][Full Text] [Related]
4. Aggregation of ubiquitin and a mutant ALS-linked SOD1 protein correlate with disease progression and fragmentation of the Golgi apparatus.
Stieber A; Gonatas JO; Gonatas NK
J Neurol Sci; 2000 Feb; 173(1):53-62. PubMed ID: 10675580
[TBL] [Abstract][Full Text] [Related]
5. The fragmented neuronal Golgi apparatus in amyotrophic lateral sclerosis includes the trans-Golgi-network: functional implications.
Stieber A; Chen Y; Wei S; Mourelatos Z; Gonatas J; Okamoto K; Gonatas NK
Acta Neuropathol; 1998 Mar; 95(3):245-53. PubMed ID: 9542589
[TBL] [Abstract][Full Text] [Related]
6. Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mutant SOD1.
Jaarsma D; Haasdijk ED; Grashorn JA; Hawkins R; van Duijn W; Verspaget HW; London J; Holstege JC
Neurobiol Dis; 2000 Dec; 7(6 Pt B):623-43. PubMed ID: 11114261
[TBL] [Abstract][Full Text] [Related]
7. The Golgi apparatus is fragmented in spinal cord motor neurons of amyotrophic lateral sclerosis with basophilic inclusions.
Fujita Y; Okamoto K; Sakurai A; Kusaka H; Aizawa H; Mihara B; Gonatas NK
Acta Neuropathol; 2002 Mar; 103(3):243-7. PubMed ID: 11907804
[TBL] [Abstract][Full Text] [Related]
8. Neurofilaments and orthograde transport are reduced in ventral root axons of transgenic mice that express human SOD1 with a G93A mutation.
Zhang B; Tu P; Abtahian F; Trojanowski JQ; Lee VM
J Cell Biol; 1997 Dec; 139(5):1307-15. PubMed ID: 9382875
[TBL] [Abstract][Full Text] [Related]
9. Fragmentation of the Golgi apparatus of Betz cells in patients with amyotrophic lateral sclerosis.
Fujita Y; Okamoto K; Sakurai A; Amari M; Nakazato Y; Gonatas NK
J Neurol Sci; 1999 Feb; 163(1):81-5. PubMed ID: 10223416
[TBL] [Abstract][Full Text] [Related]
10. Transgenic mice carrying a human mutant superoxide dismutase transgene develop neuronal cytoskeletal pathology resembling human amyotrophic lateral sclerosis lesions.
Tu PH; Raju P; Robinson KA; Gurney ME; Trojanowski JQ; Lee VM
Proc Natl Acad Sci U S A; 1996 Apr; 93(7):3155-60. PubMed ID: 8610185
[TBL] [Abstract][Full Text] [Related]
11. Transgenic mice in the study of ALS: the role of neurofilaments.
Julien JP; Couillard-Després S; Meier J
Brain Pathol; 1998 Oct; 8(4):759-69. PubMed ID: 9804382
[TBL] [Abstract][Full Text] [Related]
12. Oxidative stress, mutant SOD1, and neurofilament pathology in transgenic mouse models of human motor neuron disease.
Tu PH; Gurney ME; Julien JP; Lee VM; Trojanowski JQ
Lab Invest; 1997 Apr; 76(4):441-56. PubMed ID: 9111507
[TBL] [Abstract][Full Text] [Related]
13. Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by a familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutant.
Williamson TL; Bruijn LI; Zhu Q; Anderson KL; Anderson SD; Julien JP; Cleveland DW
Proc Natl Acad Sci U S A; 1998 Aug; 95(16):9631-6. PubMed ID: 9689132
[TBL] [Abstract][Full Text] [Related]
14. Fragmentation of the Golgi apparatus of motor neurons in amyotrophic lateral sclerosis (ALS). Clinical studies in ALS of Guam and experimental studies in deafferented neurons and in beta,beta'-iminodipropionitrile axonopathy.
Mourelatos Z; Hirano A; Rosenquist AC; Gonatas NK
Am J Pathol; 1994 Jun; 144(6):1288-300. PubMed ID: 8203467
[TBL] [Abstract][Full Text] [Related]
15. Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues.
Watanabe M; Dykes-Hoberg M; Culotta VC; Price DL; Wong PC; Rothstein JD
Neurobiol Dis; 2001 Dec; 8(6):933-41. PubMed ID: 11741389
[TBL] [Abstract][Full Text] [Related]
16. Wild-type nonneuronal cells extend survival of SOD1 mutant motor neurons in ALS mice.
Clement AM; Nguyen MD; Roberts EA; Garcia ML; Boillée S; Rule M; McMahon AP; Doucette W; Siwek D; Ferrante RJ; Brown RH; Julien JP; Goldstein LS; Cleveland DW
Science; 2003 Oct; 302(5642):113-7. PubMed ID: 14526083
[TBL] [Abstract][Full Text] [Related]
17. Fragmentation of the Golgi apparatus of the anterior horn cells in patients with familial amyotrophic lateral sclerosis with SOD1 mutations and posterior column involvement.
Fujita Y; Okamoto K; Sakurai A; Gonatas NK; Hirano A
J Neurol Sci; 2000 Mar; 174(2):137-40. PubMed ID: 10727699
[TBL] [Abstract][Full Text] [Related]
18. Amyotrophic lateral sclerosis associated with genetic abnormalities in the gene encoding Cu/Zn superoxide dismutase: molecular pathology of five new cases, and comparison with previous reports and 73 sporadic cases of ALS.
Ince PG; Tomkins J; Slade JY; Thatcher NM; Shaw PJ
J Neuropathol Exp Neurol; 1998 Oct; 57(10):895-904. PubMed ID: 9786240
[TBL] [Abstract][Full Text] [Related]
19. Selective loss of neurofilament expression in Cu/Zn superoxide dismutase (SOD1) linked amyotrophic lateral sclerosis.
Menzies FM; Grierson AJ; Cookson MR; Heath PR; Tomkins J; Figlewicz DA; Ince PG; Shaw PJ
J Neurochem; 2002 Sep; 82(5):1118-28. PubMed ID: 12358759
[TBL] [Abstract][Full Text] [Related]
20. Absence of p53: no effect in a transgenic mouse model of familial amyotrophic lateral sclerosis.
Kuntz C; Kinoshita Y; Beal MF; Donehower LA; Morrison RS
Exp Neurol; 2000 Sep; 165(1):184-90. PubMed ID: 10964497
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
