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23. Carbohydrate-deficient glycoprotein syndrome type IA (phosphomannomutase-deficiency). Carchon H; Van Schaftingen E; Matthijs G; Jaeken J Biochim Biophys Acta; 1999 Oct; 1455(2-3):155-65. PubMed ID: 10571009 [TBL] [Abstract][Full Text] [Related]
24. Congenital disorder of glycosylation type 1a in a macrosomic 16-month-old boy with an atypical phenotype and homozygosity of the N216I mutation. Neumann LM; von Moers A; Kunze J; Blankenstein O; Marquardt T Eur J Pediatr; 2003 Oct; 162(10):710-3. PubMed ID: 12905014 [TBL] [Abstract][Full Text] [Related]
25. Mutations in the MGAT2 gene controlling complex N-glycan synthesis cause carbohydrate-deficient glycoprotein syndrome type II, an autosomal recessive disease with defective brain development. Tan J; Dunn J; Jaeken J; Schachter H Am J Hum Genet; 1996 Oct; 59(4):810-7. PubMed ID: 8808595 [TBL] [Abstract][Full Text] [Related]
27. Carbohydrate-deficient glycoprotein syndrome type 1: correction of the glycosylation defect by deprivation of glucose or supplementation of mannose. Körner C; Lehle L; von Figura K Glycoconj J; 1998 May; 15(5):499-505. PubMed ID: 9881752 [TBL] [Abstract][Full Text] [Related]
28. Carbohydrate-deficient glycoprotein syndrome type V: deficiency of dolichyl-P-Glc:Man9GlcNAc2-PP-dolichyl glucosyltransferase. Körner C; Knauer R; Holzbach U; Hanefeld F; Lehle L; von Figura K Proc Natl Acad Sci U S A; 1998 Oct; 95(22):13200-5. PubMed ID: 9789065 [TBL] [Abstract][Full Text] [Related]
29. Yeast Models of Phosphomannomutase 2 Deficiency, a Congenital Disorder of Glycosylation. Lao JP; DiPrimio N; Prangley M; Sam FS; Mast JD; Perlstein EO G3 (Bethesda); 2019 Feb; 9(2):413-423. PubMed ID: 30530630 [TBL] [Abstract][Full Text] [Related]
30. A mutation in the human ortholog of the Saccharomyces cerevisiae ALG6 gene causes carbohydrate-deficient glycoprotein syndrome type-Ic. Imbach T; Burda P; Kuhnert P; Wevers RA; Aebi M; Berger EG; Hennet T Proc Natl Acad Sci U S A; 1999 Jun; 96(12):6982-7. PubMed ID: 10359825 [TBL] [Abstract][Full Text] [Related]
31. Prenatal diagnosis and the subsequent mutation analysis in a family with carbohydrate-deficient glycoprotein type I syndrome: growing evidence to support founder effects within CDG1 populations. Crosby A; Jeffery S; Homfray T; Taylor R; Patton M Genet Test; 1999; 3(3):305-7. PubMed ID: 10495932 [TBL] [Abstract][Full Text] [Related]
33. A novel disorder of N-glycosylation due to phosphomannose isomerase deficiency. de Koning TJ; Dorland L; van Diggelen OP; Boonman AM; de Jong GJ; van Noort WL; De Schryver J; Duran M; van den Berg IE; Gerwig GJ; Berger R; Poll-The BT Biochem Biophys Res Commun; 1998 Apr; 245(1):38-42. PubMed ID: 9535779 [TBL] [Abstract][Full Text] [Related]
34. Congenital nephrotic syndrome: a novel phenotype of type I carbohydrate-deficient glycoprotein syndrome. van der Knaap MS; Wevers RA; Monnens L; Jakobs C; Jaeken J; van Wijk JA J Inherit Metab Dis; 1996; 19(6):787-91. PubMed ID: 8982953 [TBL] [Abstract][Full Text] [Related]
35. Isoforms and levels of transferrin, antithrombin, alpha(1)-antitrypsin and thyroxine-binding globulin in 48 patients with carbohydrate-deficient glycoprotein syndrome type I. Stibler H; Holzbach U; Kristiansson B Scand J Clin Lab Invest; 1998 Feb; 58(1):55-61. PubMed ID: 9516657 [TBL] [Abstract][Full Text] [Related]
36. A frequent mild mutation in ALG6 may exacerbate the clinical severity of patients with congenital disorder of glycosylation Ia (CDG-Ia) caused by phosphomannomutase deficiency. Westphal V; Kjaergaard S; Schollen E; Martens K; Grunewald S; Schwartz M; Matthijs G; Freeze HH Hum Mol Genet; 2002 Mar; 11(5):599-604. PubMed ID: 11875054 [TBL] [Abstract][Full Text] [Related]
37. Abnormal synthesis of dolichol-linked oligosaccharides in carbohydrate-deficient glycoprotein syndrome. Krasnewich DM; Holt GD; Brantly M; Skovby F; Redwine J; Gahl WA Glycobiology; 1995 Jul; 5(5):503-10. PubMed ID: 8563136 [TBL] [Abstract][Full Text] [Related]
38. Deficiency of dolichol-phosphate-mannose synthase-1 causes congenital disorder of glycosylation type Ie. Imbach T; Schenk B; Schollen E; Burda P; Stutz A; Grunewald S; Bailie NM; King MD; Jaeken J; Matthijs G; Berger EG; Aebi M; Hennet T J Clin Invest; 2000 Jan; 105(2):233-9. PubMed ID: 10642602 [TBL] [Abstract][Full Text] [Related]
39. Carbohydrate-deficient glycoprotein syndrome type 1a: a variant phenotype with borderline cognitive dysfunction, cerebellar hypoplasia, and coagulation disturbances. van Ommen CH; Peters M; Barth PG; Vreken P; Wanders RJ; Jaeken J J Pediatr; 2000 Mar; 136(3):400-3. PubMed ID: 10700701 [TBL] [Abstract][Full Text] [Related]
40. Missense mutations in phosphomannomutase 2 gene in two Japanese families with carbohydrate-deficient glycoprotein syndrome type 1. Kondo I; Mizugishi K; Yoneda Y; Hashimoto T; Kuwajima K; Yuasa I; Shigemoto K; Kuroda Y Clin Genet; 1999 Jan; 55(1):50-4. PubMed ID: 10066032 [TBL] [Abstract][Full Text] [Related] [Previous] [Next] [New Search]