These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.


BIOMARKERS

Molecular Biopsy of Human Tumors

- a resource for Precision Medicine *

137 related articles for article (PubMed ID: 10832732)

  • 1. Mucopolysaccharidosis type VII in the developing mouse fetus.
    Casal ML; Wolfe JH
    Pediatr Res; 2000 Jun; 47(6):750-6. PubMed ID: 10832732
    [TBL] [Abstract][Full Text] [Related]  

  • 2. Murine mucopolysaccharidosis type VII: the impact of therapies on the clinical course and pathology in a murine model of lysosomal storage disease.
    Vogler C; Sands MS; Galvin N; Levy B; Thorpe C; Barker J; Sly WS
    J Inherit Metab Dis; 1998 Aug; 21(5):575-86. PubMed ID: 9728337
    [TBL] [Abstract][Full Text] [Related]  

  • 3. Active site mutant transgene confers tolerance to human beta-glucuronidase without affecting the phenotype of MPS VII mice.
    Sly WS; Vogler C; Grubb JH; Zhou M; Jiang J; Zhou XY; Tomatsu S; Bi Y; Snella EM
    Proc Natl Acad Sci U S A; 2001 Feb; 98(5):2205-10. PubMed ID: 11226217
    [TBL] [Abstract][Full Text] [Related]  

  • 4. Early onset of lysosomal storage disease in a murine model of mucopolysaccharidosis type VII: undegraded substrate accumulates in many tissues in the fetus and very young MPS VII mouse.
    Vogler C; Levy B; Galvin N; Lessard M; Soper B; Barker J
    Pediatr Dev Pathol; 2005; 8(4):453-62. PubMed ID: 16222480
    [TBL] [Abstract][Full Text] [Related]  

  • 5. Enzyme replacement with recombinant beta-glucuronidase in murine mucopolysaccharidosis type VII: impact of therapy during the first six weeks of life on subsequent lysosomal storage, growth, and survival.
    Vogler C; Sands MS; Levy B; Galvin N; Birkenmeier EH; Sly WS
    Pediatr Res; 1996 Jun; 39(6):1050-4. PubMed ID: 8725268
    [TBL] [Abstract][Full Text] [Related]  

  • 6. Enzyme replacement in murine mucopolysaccharidosis type VII: neuronal and glial response to beta-glucuronidase requires early initiation of enzyme replacement therapy.
    Vogler C; Levy B; Galvin NJ; Thorpe C; Sands MS; Barker JE; Baty J; Birkenmeier EH; Sly WS
    Pediatr Res; 1999 Jun; 45(6):838-44. PubMed ID: 10367775
    [TBL] [Abstract][Full Text] [Related]  

  • 7. In utero fetal liver cell transplantation without toxic irradiation alleviates lysosomal storage in mice with mucopolysaccharidosis type VII.
    Barker JE; Deveau S; Lessard M; Hamblen N; Vogler C; Levy B
    Blood Cells Mol Dis; 2001; 27(5):861-73. PubMed ID: 11783949
    [TBL] [Abstract][Full Text] [Related]  

  • 8. Lentiviral-mediated gene therapy results in sustained expression of β-glucuronidase for up to 12 months in the gus(mps/mps) and up to 18 months in the gus(tm(L175F)Sly) mouse models of mucopolysaccharidosis type VII.
    Derrick-Roberts AL; Pyragius CE; Kaidonis XM; Jackson MR; Anson DS; Byers S
    Hum Gene Ther; 2014 Sep; 25(9):798-810. PubMed ID: 25003807
    [TBL] [Abstract][Full Text] [Related]  

  • 9. Enzyme replacement therapy for murine mucopolysaccharidosis type VII.
    Sands MS; Vogler C; Kyle JW; Grubb JH; Levy B; Galvin N; Sly WS; Birkenmeier EH
    J Clin Invest; 1994 Jun; 93(6):2324-31. PubMed ID: 8200966
    [TBL] [Abstract][Full Text] [Related]  

  • 10. Glycosaminoglycan storage in cultured neonatal murine mucopolysaccharidosis type VII neuroglial cells and correction by beta-glucuronidase gene transfer.
    Taylor RM; Wolfe JH
    J Neurochem; 1997 May; 68(5):2079-85. PubMed ID: 9109535
    [TBL] [Abstract][Full Text] [Related]  

  • 11. Molecular analysis of patients with beta-glucuronidase deficiency presenting as hydrops fetalis or as early mucopolysaccharidosis VII.
    Vervoort R; Islam MR; Sly WS; Zabot MT; Kleijer WJ; Chabas A; Fensom A; Young EP; Liebaers I; Lissens W
    Am J Hum Genet; 1996 Mar; 58(3):457-71. PubMed ID: 8644704
    [TBL] [Abstract][Full Text] [Related]  

  • 12. Gene therapy for murine mucopolysaccharidosis type VII.
    Sands MS; Wolfe JH; Birkenmeier EH; Barker JE; Vogler C; Sly WS; Okuyama T; Freeman B; Nicholes A; Muzyczka N; Chang PL; Axelrod HR
    Neuromuscul Disord; 1997 Jul; 7(5):352-60. PubMed ID: 9267850
    [TBL] [Abstract][Full Text] [Related]  

  • 13. Gene transfer of low levels of beta-glucuronidase corrects hepatic lysosomal storage in a large animal model of mucopolysaccharidosis VII.
    Wolfe JH; Sands MS; Harel N; Weil MA; Parente MK; Polesky AC; Reilly JJ; Hasson C; Weimelt S; Haskins ME
    Mol Ther; 2000 Dec; 2(6):552-61. PubMed ID: 11124056
    [TBL] [Abstract][Full Text] [Related]  

  • 14. Inner ear pathology in the mucopolysaccharidosis VII mouse.
    Ohlemiller KK; Hennig AK; Lett JM; Heidbreder AF; Sands MS
    Hear Res; 2002 Jul; 169(1-2):69-84. PubMed ID: 12121741
    [TBL] [Abstract][Full Text] [Related]  

  • 15. In utero transplantation of fetal liver cells in the mucopolysaccharidosis type VII mouse results in low-level chimerism, but overexpression of beta-glucuronidase can delay onset of clinical signs.
    Casal ML; Wolfe JH
    Blood; 2001 Mar; 97(6):1625-34. PubMed ID: 11238101
    [TBL] [Abstract][Full Text] [Related]  

  • 16. Mucopolysaccharidosis type VII as a cause of recurrent non-immune hydrops fetalis.
    Cheng Y; Verp MS; Knutel T; Hibbard JU
    J Perinat Med; 2003; 31(6):535-7. PubMed ID: 14711113
    [TBL] [Abstract][Full Text] [Related]  

  • 17. Clinical course of sly syndrome (mucopolysaccharidosis type VII).
    Montaño AM; Lock-Hock N; Steiner RD; Graham BH; Szlago M; Greenstein R; Pineda M; Gonzalez-Meneses A; Çoker M; Bartholomew D; Sands MS; Wang R; Giugliani R; Macaya A; Pastores G; Ketko AK; Ezgü F; Tanaka A; Arash L; Beck M; Falk RE; Bhattacharya K; Franco J; White KK; Mitchell GA; Cimbalistiene L; Holtz M; Sly WS
    J Med Genet; 2016 Jun; 53(6):403-18. PubMed ID: 26908836
    [TBL] [Abstract][Full Text] [Related]  

  • 18. Decreased lysosomal storage in the adult MPS VII mouse brain in the vicinity of grafts of retroviral vector-corrected fibroblasts secreting high levels of beta-glucuronidase.
    Taylor RM; Wolfe JH
    Nat Med; 1997 Jul; 3(7):771-4. PubMed ID: 9212105
    [TBL] [Abstract][Full Text] [Related]  

  • 19. Infused Fc-tagged beta-glucuronidase crosses the placenta and produces clearance of storage in utero in mucopolysaccharidosis VII mice.
    Grubb JH; Vogler C; Tan Y; Shah GN; MacRae AF; Sly WS
    Proc Natl Acad Sci U S A; 2008 Jun; 105(24):8375-80. PubMed ID: 18544647
    [TBL] [Abstract][Full Text] [Related]  

  • 20. Widespread correction of lysosomal storage following intrahepatic injection of a recombinant adeno-associated virus in the adult MPS VII mouse.
    Sferra TJ; Backstrom K; Wang C; Rennard R; Miller M; Hu Y
    Mol Ther; 2004 Sep; 10(3):478-91. PubMed ID: 15336648
    [TBL] [Abstract][Full Text] [Related]  

    [Next]    [New Search]
    of 7.