271 related articles for article (PubMed ID: 11018468)
1. Difference in substrate specificity between human and mouse lysosomal acid lipase: low affinity for cholesteryl ester in mouse lysosomal acid lipase.
Groener JE; Bax W; Stuani C; Pagani F
Biochim Biophys Acta; 2000 Sep; 1487(2-3):155-62. PubMed ID: 11018468
[TBL] [Abstract][Full Text] [Related]
2. Cysteine residues in human lysosomal acid lipase are involved in selective cholesteryl esterase activity.
Pagani F; Pariyarath R; Stuani C; Garcia R; Baralle FE
Biochem J; 1997 Aug; 326 ( Pt 1)(Pt 1):265-9. PubMed ID: 9337878
[TBL] [Abstract][Full Text] [Related]
3. Expression and functional characterization of human lysosomal acid lipase gene (LIPA) mutation responsible for cholesteryl ester storage disease (CESD) phenotype.
Rajamohan F; Reyes AR; Ruangsiriluk W; Hoth LR; Han S; Caspers N; Tu M; Ward J; Kurumbail RG
Protein Expr Purif; 2015 Jun; 110():22-9. PubMed ID: 25620107
[TBL] [Abstract][Full Text] [Related]
4. Degradation of low density lipoprotein cholesterol esters by lysosomal lipase in vitro. Effect of core physical state and basis of species selectivity.
Lusa S; Somerharju P
Biochim Biophys Acta; 1998 Jan; 1389(2):112-22. PubMed ID: 9461252
[TBL] [Abstract][Full Text] [Related]
5. Hepatic cholesteryl ester accumulation in lysosomal acid lipase deficiency: non-invasive identification and treatment monitoring by magnetic resonance.
Thelwall PE; Smith FE; Leavitt MC; Canty D; Hu W; Hollingsworth KG; Thoma C; Trenell MI; Taylor R; Rutkowski JV; Blamire AM; Quinn AG
J Hepatol; 2013 Sep; 59(3):543-9. PubMed ID: 23624251
[TBL] [Abstract][Full Text] [Related]
6. Hepatocyte-specific deletion of lysosomal acid lipase leads to cholesteryl ester but not triglyceride or retinyl ester accumulation.
Pajed L; Wagner C; Taschler U; Schreiber R; Kolleritsch S; Fawzy N; Pototschnig I; Schoiswohl G; Pusch LM; Wieser BI; Vesely P; Hoefler G; Eichmann TO; Zimmermann R; Lass A
J Biol Chem; 2019 Jun; 294(23):9118-9133. PubMed ID: 31023823
[TBL] [Abstract][Full Text] [Related]
7. Role of lysosomal acid lipase in the metabolism of plasma low density lipoprotein. Observations in cultured fibroblasts from a patient with cholesteryl ester storage disease.
Goldstein JL; Dana SE; Faust JR; Beaudet AL; Brown MS
J Biol Chem; 1975 Nov; 250(21):8487-95. PubMed ID: 172501
[TBL] [Abstract][Full Text] [Related]
8. Role of lysosomal acid lipase in the intracellular metabolism of LDL-transported dehydroepiandrosterone-fatty acyl esters.
Wang F; Wang W; Wähälä K; Adlercreutz H; Ikonen E; Tikkanen MJ
Am J Physiol Endocrinol Metab; 2008 Dec; 295(6):E1455-61. PubMed ID: 18796546
[TBL] [Abstract][Full Text] [Related]
9. Restoration of a regulatory response to low density lipoprotein in acid lipase-deficient human fibroblasts.
Brown MS; Sobhani MK; Brunschede GY; Goldstein JL
J Biol Chem; 1976 Jun; 251(11):3277-86. PubMed ID: 179993
[TBL] [Abstract][Full Text] [Related]
10. Direct observation of lipoprotein cholesterol ester degradation in lysosomes.
Lusa S; Tanhuanpää K; Ezra T; Somerharju P
Biochem J; 1998 Jun; 332 ( Pt 2)(Pt 2):451-7. PubMed ID: 9601074
[TBL] [Abstract][Full Text] [Related]
11. The role of mannosylated enzyme and the mannose receptor in enzyme replacement therapy.
Du H; Levine M; Ganesa C; Witte DP; Cole ES; Grabowski GA
Am J Hum Genet; 2005 Dec; 77(6):1061-74. PubMed ID: 16380916
[TBL] [Abstract][Full Text] [Related]
12. Human lysosomal acid lipase/cholesteryl ester hydrolase and human gastric lipase: site-directed mutagenesis of Cys227 and Cys236 results in substrate-dependent reduction of enzymatic activity.
Lohse P; Lohse P; Chahrokh-Zadeh S; Seidel D
J Lipid Res; 1997 Sep; 38(9):1896-905. PubMed ID: 9323599
[TBL] [Abstract][Full Text] [Related]
13. CRISPR/Cas9-Mediated Gene Editing in Human iPSC-Derived Macrophage Reveals Lysosomal Acid Lipase Function in Human Macrophages-Brief Report.
Zhang H; Shi J; Hachet MA; Xue C; Bauer RC; Jiang H; Li W; Tohyama J; Millar J; Billheimer J; Phillips MC; Razani B; Rader DJ; Reilly MP
Arterioscler Thromb Vasc Biol; 2017 Nov; 37(11):2156-2160. PubMed ID: 28882870
[TBL] [Abstract][Full Text] [Related]
14. Lysosomal acid lipase does not have a propeptide and should not be considered being a proprotein.
Strøm TB; Vinje T; Bjune K; da Costa LT; Laerdahl JK; Leren TP
Proteins; 2020 Mar; 88(3):440-448. PubMed ID: 31587363
[TBL] [Abstract][Full Text] [Related]
15. Ezetimibe markedly attenuates hepatic cholesterol accumulation and improves liver function in the lysosomal acid lipase-deficient mouse, a model for cholesteryl ester storage disease.
Chuang JC; Lopez AM; Posey KS; Turley SD
Biochem Biophys Res Commun; 2014 Jan; 443(3):1073-7. PubMed ID: 24370824
[TBL] [Abstract][Full Text] [Related]
16. Cholesteryl ester and triglyceride hydrolysis by an acid lipase from rabbit aorta.
Brecher P; Pyun HY; Chobanian AV
Biochim Biophys Acta; 1978 Jul; 530(1):112-23. PubMed ID: 28783
[TBL] [Abstract][Full Text] [Related]
17. Extended use of a selective inhibitor of acid lipase for the diagnosis of Wolman disease and cholesteryl ester storage disease.
Civallero G; De Mari J; Bittar C; Burin M; Giugliani R
Gene; 2014 Apr; 539(1):154-6. PubMed ID: 24508470
[TBL] [Abstract][Full Text] [Related]
18. Lysosomal lipid hydrolysis provides substrates for lipid mediator synthesis in murine macrophages.
Schlager S; Vujic N; Korbelius M; Duta-Mare M; Dorow J; Leopold C; Rainer S; Wegscheider M; Reicher H; Ceglarek U; Sattler W; Radovic B; Kratky D
Oncotarget; 2017 Jun; 8(25):40037-40051. PubMed ID: 28402950
[TBL] [Abstract][Full Text] [Related]
19. Study of the hydrolysis of 4-methylumbelliferyl oleate by acid lipase and cholesteryl oleate by acid cholesteryl esterase in human leucocytes, fibroblasts and liver.
Koster JF; Vaandrager H; van Berkel TJ
Biochim Biophys Acta; 1980 Apr; 618(1):98-105. PubMed ID: 6892888
[No Abstract] [Full Text] [Related]
20. Genetic variation of lysosomal acid lipase.
Cortner JA; Coates PM; Swoboda E; Schnatz JD
Pediatr Res; 1976 Nov; 10(11):927-32. PubMed ID: 10546
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
