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3. A European multicenter study of phenylalanine hydroxylase deficiency: classification of 105 mutations and a general system for genotype-based prediction of metabolic phenotype. Guldberg P; Rey F; Zschocke J; Romano V; François B; Michiels L; Ullrich K; Hoffmann GF; Burgard P; Schmidt H; Meli C; Riva E; Dianzani I; Ponzone A; Rey J; Güttler F Am J Hum Genet; 1998 Jul; 63(1):71-9. PubMed ID: 9634518 [TBL] [Abstract][Full Text] [Related]
4. Validation of PAH genotype-based predictions of metabolic phenylalanine hydroxylase deficiency phenotype: investigation of PKU/MHP patients from Lithuania. Kasnauskiene J; Cimbalistiene L; Kucinskas V Med Sci Monit; 2003 Mar; 9(3):CR142-6. PubMed ID: 12640344 [TBL] [Abstract][Full Text] [Related]
5. Mutation analysis in hyperphenylalaninemia patients from South Italy. Trunzo R; Santacroce R; D'Andrea G; Longo V; De Girolamo G; Dimatteo C; Leccese A; Lillo V; Papadia F; Margaglione M Clin Biochem; 2013 Dec; 46(18):1896-8. PubMed ID: 23792259 [TBL] [Abstract][Full Text] [Related]
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10. Relation between genotype and phenotype in Swedish phenylketonuria and hyperphenylalaninemia patients. Svensson E; von Döbeln U; Eisensmith RC; Hagenfeldt L; Woo SL Eur J Pediatr; 1993 Feb; 152(2):132-9. PubMed ID: 8444221 [TBL] [Abstract][Full Text] [Related]
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17. The phenylketonuria locus: current knowledge about alleles and mutations of the phenylalanine hydroxylase gene in various populations. Konecki DS; Lichter-Konecki U Hum Genet; 1991 Aug; 87(4):377-88. PubMed ID: 1679029 [TBL] [Abstract][Full Text] [Related]
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