These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.


BIOMARKERS

Molecular Biopsy of Human Tumors

- a resource for Precision Medicine *

174 related articles for article (PubMed ID: 11196106)

  • 1. Branched-chain L-amino acid metabolism in classical maple syrup urine disease after orthotopic liver transplantation.
    Bodner-Leidecker A; Wendel U; Saudubray JM; Schadewaldt P
    J Inherit Metab Dis; 2000 Dec; 23(8):805-18. PubMed ID: 11196106
    [TBL] [Abstract][Full Text] [Related]  

  • 2. Domino liver transplantation in maple syrup urine disease.
    Khanna A; Hart M; Nyhan WL; Hassanein T; Panyard-Davis J; Barshop BA
    Liver Transpl; 2006 May; 12(5):876-82. PubMed ID: 16628687
    [TBL] [Abstract][Full Text] [Related]  

  • 3. Diagnosis and treatment of maple syrup disease: a study of 36 patients.
    Morton DH; Strauss KA; Robinson DL; Puffenberger EG; Kelley RI
    Pediatrics; 2002 Jun; 109(6):999-1008. PubMed ID: 12042535
    [TBL] [Abstract][Full Text] [Related]  

  • 4. Significance of L-alloisoleucine in plasma for diagnosis of maple syrup urine disease.
    Schadewaldt P; Bodner-Leidecker A; Hammen HW; Wendel U
    Clin Chem; 1999 Oct; 45(10):1734-40. PubMed ID: 10508118
    [TBL] [Abstract][Full Text] [Related]  

  • 5. On the mechanism of L-alloisoleucine formation: studies on a healthy subject and in fibroblasts from normals and patients with maple syrup urine disease.
    Schadewaldt P; Hammen HW; Dalle-Feste C; Wendel U
    J Inherit Metab Dis; 1990; 13(2):137-50. PubMed ID: 2116545
    [TBL] [Abstract][Full Text] [Related]  

  • 6. Assessment of whole body L-leucine oxidation by noninvasive L-[1-13C]leucine breath tests: a reappraisal in patients with maple syrup urine disease, obligate heterozygotes, and healthy subjects.
    Schadewaldt P; Bodner A; Brösicke H; Hammen HW; Wendel U
    Pediatr Res; 1998 May; 43(5):592-600. PubMed ID: 9585004
    [TBL] [Abstract][Full Text] [Related]  

  • 7. Whole-body L-leucine oxidation in patients with variant form of maple syrup urine disease.
    Schadewaldt P; Bodner-Leidecker A; Hammen HW; Wendel U
    Pediatr Res; 2001 May; 49(5):627-35. PubMed ID: 11328944
    [TBL] [Abstract][Full Text] [Related]  

  • 8. Oral L-alloisoleucine loading studies in healthy subjects and in patients with maple syrup urine disease.
    Schadewaldt P; Dalle-Feste C; Langenbeck U; Wendel U
    Pediatr Res; 1991 Nov; 30(5):430-4. PubMed ID: 1754297
    [TBL] [Abstract][Full Text] [Related]  

  • 9. Practical methods to estimate whole body leucine oxidation in maple syrup urine disease.
    Elsas LJ; Ellerine NP; Klein PD
    Pediatr Res; 1993 May; 33(5):445-51. PubMed ID: 8511017
    [TBL] [Abstract][Full Text] [Related]  

  • 10. Metabolism of branched-chain amino acids in maple syrup urine disease.
    Schadewaldt P; Wendel U
    Eur J Pediatr; 1997 Aug; 156 Suppl 1():S62-6. PubMed ID: 9266218
    [TBL] [Abstract][Full Text] [Related]  

  • 11. Alloisoleucine formation in maple syrup urine disease: isotopic evidence for the mechanism.
    Matthews DE; Ben-Galim E; Haymond MW; Bier DM
    Pediatr Res; 1980 Jul; 14(7):854-7. PubMed ID: 7413299
    [TBL] [Abstract][Full Text] [Related]  

  • 12. Functional differences in the catabolism of branched-chain L-amino acids in cultured normal and maple syrup urine disease fibroblasts.
    Schadewaldt P; Wendel U
    Biochem Med Metab Biol; 1989 Apr; 41(2):105-16. PubMed ID: 2719855
    [TBL] [Abstract][Full Text] [Related]  

  • 13. Living related versus deceased donor liver transplantation for maple syrup urine disease.
    Feier F; Schwartz IV; Benkert AR; Seda Neto J; Miura I; Chapchap P; da Fonseca EA; Vieira S; Zanotelli ML; Pinto e Vairo F; Camelo JS; Margutti AV; Mazariegos GV; Puffenberger EG; Strauss KA
    Mol Genet Metab; 2016 Mar; 117(3):336-43. PubMed ID: 26786177
    [TBL] [Abstract][Full Text] [Related]  

  • 14. Adipose transplant for inborn errors of branched chain amino acid metabolism in mice.
    Zimmerman HA; Olson KC; Chen G; Lynch CJ
    Mol Genet Metab; 2013 Aug; 109(4):345-53. PubMed ID: 23800641
    [TBL] [Abstract][Full Text] [Related]  

  • 15. Renal clearance of branched-chain L-amino and 2-oxo acids in maple syrup urine disease.
    Schadewaldt P; Hammen HW; Ott AC; Wendel U
    J Inherit Metab Dis; 1999 Aug; 22(6):706-22. PubMed ID: 10472531
    [TBL] [Abstract][Full Text] [Related]  

  • 16. Comparison of the catabolism of branched-chain L-amino acids in cultured human skin fibroblasts.
    Schadewaldt P; Wendel U
    Pediatr Res; 1987 Nov; 22(5):591-4. PubMed ID: 3684388
    [TBL] [Abstract][Full Text] [Related]  

  • 17. Total branched-chain amino acids requirement in patients with maple syrup urine disease by use of indicator amino acid oxidation with L-[1-13C]phenylalanine.
    Riazi R; Rafii M; Clarke JT; Wykes LJ; Ball RO; Pencharz PB
    Am J Physiol Endocrinol Metab; 2004 Jul; 287(1):E142-9. PubMed ID: 14970005
    [TBL] [Abstract][Full Text] [Related]  

  • 18. Determination of (S)- and (R)-2-oxo-3-methylvaleric acid in plasma of patients with maple syrup urine disease.
    Wendel U; Even G; Langenbeck U; Schadewaldt P; Hummel W
    Clin Chim Acta; 1992 Jun; 208(1-2):85-91. PubMed ID: 1638756
    [TBL] [Abstract][Full Text] [Related]  

  • 19. Maple syrup urine disease: branched-chain amino acid concentrations and metabolism in cultured human lymphoblasts.
    Skaper SD; Molden DP; Seegmiller JE
    Biochem Genet; 1976 Aug; 14(7-8):527-39. PubMed ID: 985377
    [TBL] [Abstract][Full Text] [Related]  

  • 20. Blood and tissue branched-chain amino and alpha-keto acid concentrations: effect of diet, starvation, and disease.
    Hutson SM; Harper AE
    Am J Clin Nutr; 1981 Feb; 34(2):173-83. PubMed ID: 7211722
    [TBL] [Abstract][Full Text] [Related]  

    [Next]    [New Search]
    of 9.