195 related articles for article (PubMed ID: 11214912)
1. A transgenic model of a familial prion disease.
Harris DA; Chiesa R; Drisaldi B; Quaglio E; Migheli A; Piccardo P; Ghetti B
Arch Virol Suppl; 2000; (16):103-12. PubMed ID: 11214912
[TBL] [Abstract][Full Text] [Related]
2. Accumulation of protease-resistant prion protein (PrP) and apoptosis of cerebellar granule cells in transgenic mice expressing a PrP insertional mutation.
Chiesa R; Drisaldi B; Quaglio E; Migheli A; Piccardo P; Ghetti B; Harris DA
Proc Natl Acad Sci U S A; 2000 May; 97(10):5574-9. PubMed ID: 10805813
[TBL] [Abstract][Full Text] [Related]
3. Neurological illness in transgenic mice expressing a prion protein with an insertional mutation.
Chiesa R; Piccardo P; Ghetti B; Harris DA
Neuron; 1998 Dec; 21(6):1339-51. PubMed ID: 9883727
[TBL] [Abstract][Full Text] [Related]
4. Pathogenic mutations within the hydrophobic domain of the prion protein lead to the formation of protease-sensitive prion species with increased lethality.
Coleman BM; Harrison CF; Guo B; Masters CL; Barnham KJ; Lawson VA; Hill AF
J Virol; 2014 Mar; 88(5):2690-703. PubMed ID: 24352465
[TBL] [Abstract][Full Text] [Related]
5. Transgenic models of prion disease.
Scott MR; Supattapone S; Nguyen HO; DeArmond SJ; Prusiner SB
Arch Virol Suppl; 2000; (16):113-24. PubMed ID: 11214913
[TBL] [Abstract][Full Text] [Related]
6. Prion protein transgenes and the neuropathology in prion diseases.
DeArmond SJ; Prusiner SB
Brain Pathol; 1995 Jan; 5(1):77-89. PubMed ID: 7767493
[TBL] [Abstract][Full Text] [Related]
7. Mutant PrPSc conformers induced by a synthetic peptide and several prion strains.
Tremblay P; Ball HL; Kaneko K; Groth D; Hegde RS; Cohen FE; DeArmond SJ; Prusiner SB; Safar JG
J Virol; 2004 Feb; 78(4):2088-99. PubMed ID: 14747574
[TBL] [Abstract][Full Text] [Related]
8. Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene.
Korth C; Kaneko K; Groth D; Heye N; Telling G; Mastrianni J; Parchi P; Gambetti P; Will R; Ironside J; Heinrich C; Tremblay P; DeArmond SJ; Prusiner SB
Proc Natl Acad Sci U S A; 2003 Apr; 100(8):4784-9. PubMed ID: 12684540
[TBL] [Abstract][Full Text] [Related]
9. Primary myopathy and accumulation of PrPSc-like molecules in peripheral tissues of transgenic mice expressing a prion protein insertional mutation.
Chiesa R; Pestronk A; Schmidt RE; Tourtellotte WG; Ghetti B; Piccardo P; Harris DA
Neurobiol Dis; 2001 Apr; 8(2):279-88. PubMed ID: 11300723
[TBL] [Abstract][Full Text] [Related]
10. A murine model of a familial prion disease.
Harris DA; Chiesa R; Drisaldi B; Quaglio E; Migheli A; Piccardo P; Ghetti B
Clin Lab Med; 2003 Mar; 23(1):175-86. PubMed ID: 12733431
[TBL] [Abstract][Full Text] [Related]
11. Sc237 hamster PrPSc and Sc237-derived mouse PrPSc generated by interspecies in vitro amplification exhibit distinct pathological and biochemical properties in tga20 transgenic mice.
Yoshioka M; Imamura M; Okada H; Shimozaki N; Murayama Y; Yokoyama T; Mohri S
Microbiol Immunol; 2011 May; 55(5):331-40. PubMed ID: 21362027
[TBL] [Abstract][Full Text] [Related]
12. A novel PRNP-P105S mutation associated with atypical prion disease and a rare PrPSc conformation.
Tunnell E; Wollman R; Mallik S; Cortes CJ; Dearmond SJ; Mastrianni JA
Neurology; 2008 Oct; 71(18):1431-8. PubMed ID: 18955686
[TBL] [Abstract][Full Text] [Related]
13. Prion protein with an octapeptide insertion has impaired neuroprotective activity in transgenic mice.
Li A; Piccardo P; Barmada SJ; Ghetti B; Harris DA
EMBO J; 2007 Jun; 26(11):2777-85. PubMed ID: 17510630
[TBL] [Abstract][Full Text] [Related]
14. The neuropathological phenotype in transgenic mice expressing different prion protein constructs.
DeArmond SJ; Yang SL; Cayetano-Canlas J; Groth D; Prusiner SB
Philos Trans R Soc Lond B Biol Sci; 1994 Mar; 343(1306):415-23. PubMed ID: 7913760
[TBL] [Abstract][Full Text] [Related]
15. Genetic and infectious prion diseases.
Prusiner SB
Arch Neurol; 1993 Nov; 50(11):1129-53. PubMed ID: 8105771
[TBL] [Abstract][Full Text] [Related]
16. Prion protein with an insertional mutation accumulates on axonal and dendritic plasmalemma and is associated with distinctive ultrastructural changes.
Jeffrey M; Goodsir C; McGovern G; Barmada SJ; Medrano AZ; Harris DA
Am J Pathol; 2009 Sep; 175(3):1208-17. PubMed ID: 19700753
[TBL] [Abstract][Full Text] [Related]
17. Anchorless prion protein results in infectious amyloid disease without clinical scrapie.
Chesebro B; Trifilo M; Race R; Meade-White K; Teng C; LaCasse R; Raymond L; Favara C; Baron G; Priola S; Caughey B; Masliah E; Oldstone M
Science; 2005 Jun; 308(5727):1435-9. PubMed ID: 15933194
[TBL] [Abstract][Full Text] [Related]
18. Neurodegenerative illness in transgenic mice expressing a transmembrane form of the prion protein.
Stewart RS; Piccardo P; Ghetti B; Harris DA
J Neurosci; 2005 Mar; 25(13):3469-77. PubMed ID: 15800202
[TBL] [Abstract][Full Text] [Related]
19. Prion protein functions and dysfunction in prion diseases.
Sakudo A; Ikuta K
Curr Med Chem; 2009; 16(3):380-9. PubMed ID: 19149584
[TBL] [Abstract][Full Text] [Related]
20. Experimental Models of Inherited PrP Prion Diseases.
Watts JC; Prusiner SB
Cold Spring Harb Perspect Med; 2017 Nov; 7(11):. PubMed ID: 28096244
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]