151 related articles for article (PubMed ID: 11484821)
1. Morphological alterations in the inner ear of the arylsulfatase A-deficient mouse.
Coenen R; Gieselmann V; Lüllmann-Rauch R
Acta Neuropathol; 2001 May; 101(5):491-8. PubMed ID: 11484821
[TBL] [Abstract][Full Text] [Related]
2. Lysosomal sulfatide storage in the brain of arylsulfatase A-deficient mice: cellular alterations and topographic distribution.
Wittke D; Hartmann D; Gieselmann V; Lüllmann-Rauch R
Acta Neuropathol; 2004 Oct; 108(4):261-71. PubMed ID: 15322834
[TBL] [Abstract][Full Text] [Related]
3. Increasing sulfatide synthesis in myelin-forming cells of arylsulfatase A-deficient mice causes demyelination and neurological symptoms reminiscent of human metachromatic leukodystrophy.
Ramakrishnan H; Hedayati KK; Lüllmann-Rauch R; Wessig C; Fewou SN; Maier H; Goebel HH; Gieselmann V; Eckhardt M
J Neurosci; 2007 Aug; 27(35):9482-90. PubMed ID: 17728461
[TBL] [Abstract][Full Text] [Related]
4. Decline in brainstem auditory-evoked potentials coincides with loss of spiral ganglion cells in arylsulfatase A-deficient mice.
D'Hooge R; Coenen R; Gieselmann V; Lüllmann-Rauch R; De Deyn PP
Brain Res; 1999 Nov; 847(2):352-6. PubMed ID: 10575108
[TBL] [Abstract][Full Text] [Related]
5. Spiral ganglion degeneration and hearing loss as a consequence of satellite cell death in saposin B-deficient mice.
Akil O; Sun Y; Vijayakumar S; Zhang W; Ku T; Lee CK; Jones S; Grabowski GA; Lustig LR
J Neurosci; 2015 Feb; 35(7):3263-75. PubMed ID: 25698761
[TBL] [Abstract][Full Text] [Related]
6. Time course of inner ear degeneration and deafness in mice lacking the Kir4.1 potassium channel subunit.
Rozengurt N; Lopez I; Chiu CS; Kofuji P; Lester HA; Neusch C
Hear Res; 2003 Mar; 177(1-2):71-80. PubMed ID: 12618319
[TBL] [Abstract][Full Text] [Related]
7. Modest phenotypic improvements in ASA-deficient mice with only one UDP-galactose:ceramide-galactosyltransferase gene.
Franken S; Wittke D; Mansson JE; D'Hooge R; De Deyn PP; Lüllmann-Rauch R; Matzner U; Gieselmann V
Lipids Health Dis; 2006 Aug; 5():21. PubMed ID: 16893448
[TBL] [Abstract][Full Text] [Related]
8. Sulfatide storage in visceral organs of arylsulfatase A-deficient mice.
Schott I; Hartmann D; Gieselmann V; Lüllmann-Rauch R
Virchows Arch; 2001 Jul; 439(1):90-6. PubMed ID: 11499846
[TBL] [Abstract][Full Text] [Related]
9. Sulfatide storage in neurons causes hyperexcitability and axonal degeneration in a mouse model of metachromatic leukodystrophy.
Eckhardt M; Hedayati KK; Pitsch J; Lüllmann-Rauch R; Beck H; Fewou SN; Gieselmann V
J Neurosci; 2007 Aug; 27(34):9009-21. PubMed ID: 17715338
[TBL] [Abstract][Full Text] [Related]
10. Early degeneration of sensory and ganglion cells in the inner ear of mice with uncomplicated genetic deafness (dn): preliminary observations.
Pujol R; Shnerson A; Lenoir M; Deol MS
Hear Res; 1983 Oct; 12(1):57-63. PubMed ID: 6662828
[TBL] [Abstract][Full Text] [Related]
11. A spontaneously immortalized Schwann cell line to study the molecular aspects of metachromatic leukodystrophy.
Saravanan K; Büssow H; Weiler N; Gieselmann V; Franken S
J Neurosci Methods; 2007 Apr; 161(2):223-33. PubMed ID: 17204333
[TBL] [Abstract][Full Text] [Related]
12. Hereditary deafness in the cat. An electron microscopic study of the spiral ganglion.
Elverland HH; Mair IW
Acta Otolaryngol; 1980; 90(5-6):360-9. PubMed ID: 7211330
[TBL] [Abstract][Full Text] [Related]
13. Deletion of fatty acid amide hydrolase reduces lyso-sulfatide levels but exacerbates metachromatic leukodystrophy in mice.
Yaghootfam C; Gehrig B; Sylvester M; Gieselmann V; Matzner U
J Biol Chem; 2021 Sep; 297(3):101064. PubMed ID: 34375644
[TBL] [Abstract][Full Text] [Related]
14. Structural and Ultrastructural Changes to Type I Spiral Ganglion Neurons and Schwann Cells in the Deafened Guinea Pig Cochlea.
Wise AK; Pujol R; Landry TG; Fallon JB; Shepherd RK
J Assoc Res Otolaryngol; 2017 Dec; 18(6):751-769. PubMed ID: 28717876
[TBL] [Abstract][Full Text] [Related]
15. Arylsulfatase A Overexpressing Human iPSC-derived Neural Cells Reduce CNS Sulfatide Storage in a Mouse Model of Metachromatic Leukodystrophy.
Doerr J; Böckenhoff A; Ewald B; Ladewig J; Eckhardt M; Gieselmann V; Matzner U; Brüstle O; Koch P
Mol Ther; 2015 Sep; 23(9):1519-31. PubMed ID: 26061647
[TBL] [Abstract][Full Text] [Related]
16. Apoptosis of inner hair cells caused by laser ablation of their spiral ganglion neurons in cultures of the mouse organ of Corti.
Sobkowicz HM; Slapnick SM; August BK
J Neurocytol; 1999; 28(10-11):939-54. PubMed ID: 10900096
[TBL] [Abstract][Full Text] [Related]
17. Expression of transient receptor potential channel mucolipin (TRPML) and polycystine (TRPP) in the mouse inner ear.
Takumida M; Anniko M
Acta Otolaryngol; 2010 Feb; 130(2):196-203. PubMed ID: 20095091
[TBL] [Abstract][Full Text] [Related]
18. [Pathophysiology of sulfatide metabolism in metachromatic leukodystrophy].
Wiesmann UN
Bull Schweiz Akad Med Wiss; 1978 Mar; 34(1-3):33-47. PubMed ID: 27269
[TBL] [Abstract][Full Text] [Related]
19. Cochlear pathology of the circling mouse: a new mouse model of DFNB6.
Chung WH; Kim KR; Cho YS; Cho DY; Woo JH; Ryoo ZY; Cho KI; Hong SH
Acta Otolaryngol; 2007 Mar; 127(3):244-51. PubMed ID: 17364360
[TBL] [Abstract][Full Text] [Related]
20. Reduced brain cholesterol content in arylsulfatase A-deficient mice.
Lütjohann D; Harzer K; Gieselmann V; Eckhardt M
Biochem Biophys Res Commun; 2006 Jun; 344(2):647-50. PubMed ID: 16630546
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]