These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
3. Inborn errors of cholesterol biosynthesis. Kelley RI Adv Pediatr; 2000; 47():1-53. PubMed ID: 10959439 [TBL] [Abstract][Full Text] [Related]
4. Genetic disorders of cholesterol biosynthesis in mice and humans. Nwokoro NA; Wassif CA; Porter FD Mol Genet Metab; 2001; 74(1-2):105-19. PubMed ID: 11592808 [TBL] [Abstract][Full Text] [Related]
5. [Identification of the gene for hyper-IgD syndrome: a model of modern genetics]. Drenth JP; Waterham HR; Kuis W; Houten SM; Frenkel J; Wanders RJ; Poll-The BT; van der Meer JW Ned Tijdschr Geneeskd; 2000 Apr; 144(17):782-5. PubMed ID: 10800545 [TBL] [Abstract][Full Text] [Related]
6. Mevalonate kinase deficiencies: from mevalonic aciduria to hyperimmunoglobulinemia D syndrome. Haas D; Hoffmann GF Orphanet J Rare Dis; 2006 Apr; 1():13. PubMed ID: 16722536 [TBL] [Abstract][Full Text] [Related]
7. Precholesterol sterols accumulate in lipid rafts of patients with Smith-Lemli-Opitz syndrome and X-linked dominant chondrodysplasia punctata. Rakheja D; Boriack RL Pediatr Dev Pathol; 2008; 11(2):128-32. PubMed ID: 17378665 [TBL] [Abstract][Full Text] [Related]
8. Inborn errors of sterol biosynthesis. Kelley RI; Herman GE Annu Rev Genomics Hum Genet; 2001; 2():299-341. PubMed ID: 11701653 [TBL] [Abstract][Full Text] [Related]
9. Mevalonic aciduria--an inborn error of cholesterol and nonsterol isoprene biosynthesis. Hoffmann G; Gibson KM; Brandt IK; Bader PI; Wappner RS; Sweetman L N Engl J Med; 1986 Jun; 314(25):1610-4. PubMed ID: 3012338 [TBL] [Abstract][Full Text] [Related]
10. Disorders of post-squalene cholesterol biosynthesis leading to human dysmorphogenesis. Andersson HC Cell Mol Biol (Noisy-le-grand); 2002 Mar; 48(2):173-7. PubMed ID: 11990452 [TBL] [Abstract][Full Text] [Related]
11. Sterol metabolism disorders and neurodevelopment-an update. Kanungo S; Soares N; He M; Steiner RD Dev Disabil Res Rev; 2013; 17(3):197-210. PubMed ID: 23798009 [TBL] [Abstract][Full Text] [Related]
12. Disorders of sterol synthesis: beyond Smith-Lemli-Opitz syndrome. Herman GE; Kratz L Am J Med Genet C Semin Med Genet; 2012 Nov; 160C(4):301-21. PubMed ID: 23042573 [TBL] [Abstract][Full Text] [Related]
13. Living with inborn errors of cholesterol biosynthesis: lessons from adult patients. Cardoso ML; Barbosa M; Serra D; Martins E; Fortuna A; Reis-Lima M; Bandeira A; Balreira A; Marques F Clin Genet; 2014 Feb; 85(2):184-8. PubMed ID: 23509885 [TBL] [Abstract][Full Text] [Related]
14. Maternal apo E genotype is a modifier of the Smith-Lemli-Opitz syndrome. Witsch-Baumgartner M; Gruber M; Kraft HG; Rossi M; Clayton P; Giros M; Haas D; Kelley RI; Krajewska-Walasek M; Utermann G J Med Genet; 2004 Aug; 41(8):577-84. PubMed ID: 15286151 [TBL] [Abstract][Full Text] [Related]
16. Clinical and biochemical phenotype in 11 patients with mevalonic aciduria. Hoffmann GF; Charpentier C; Mayatepek E; Mancini J; Leichsenring M; Gibson KM; Divry P; Hrebicek M; Lehnert W; Sartor K Pediatrics; 1993 May; 91(5):915-21. PubMed ID: 8386351 [TBL] [Abstract][Full Text] [Related]
17. Molecular analysis of the MVK and TNFRSF1A genes in patients with a clinical presentation typical of the hyperimmunoglobulinemia D with periodic fever syndrome: a low-penetrance TNFRSF1A variant in a heterozygous MVK carrier possibly influences the phenotype of hyperimmunoglobulinemia D with periodic fever syndrome or vice versa. Stojanov S; Lohse P; Lohse P; Hoffmann F; Renner ED; Zellerer S; Kéry A; Shin YS; Haas D; Hoffmann GF; Belohradsky BH Arthritis Rheum; 2004 Jun; 50(6):1951-8. PubMed ID: 15188372 [TBL] [Abstract][Full Text] [Related]
18. Severe Smith-Lemli-Opitz syndrome with prolonged survival and lipid abnormalities. Pierquin G; Peeters P; Roels F; Vamos E; Brucher JM; Tint GS; Honda A; Van Regemorter N Am J Med Genet; 1995 Apr; 56(3):276-80. PubMed ID: 7778589 [TBL] [Abstract][Full Text] [Related]
19. Smith-Lemli-Opitz syndrome: the first malformation syndrome associated with defective cholesterol synthesis. Battaile KP; Steiner RD Mol Genet Metab; 2000; 71(1-2):154-62. PubMed ID: 11001806 [TBL] [Abstract][Full Text] [Related]
20. Malformation syndromes caused by disorders of cholesterol synthesis. Porter FD; Herman GE J Lipid Res; 2011 Jan; 52(1):6-34. PubMed ID: 20929975 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]