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4. Mutations in COX10 result in a defect in mitochondrial heme A biosynthesis and account for multiple, early-onset clinical phenotypes associated with isolated COX deficiency. Antonicka H; Leary SC; Guercin GH; Agar JN; Horvath R; Kennaway NG; Harding CO; Jaksch M; Shoubridge EA Hum Mol Genet; 2003 Oct; 12(20):2693-702. PubMed ID: 12928484 [TBL] [Abstract][Full Text] [Related]
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