388 related articles for article (PubMed ID: 11603803)
21. The neuronal Golgi apparatus is fragmented in transgenic mice expressing a mutant human SOD1, but not in mice expressing the human NF-H gene.
Stieber A; Gonatas JO; Collard J; Meier J; Julien J; Schweitzer P; Gonatas NK
J Neurol Sci; 2000 Feb; 173(1):63-72. PubMed ID: 10675581
[TBL] [Abstract][Full Text] [Related]
22. Enhancing NAD+ Salvage Pathway Reverts the Toxicity of Primary Astrocytes Expressing Amyotrophic Lateral Sclerosis-linked Mutant Superoxide Dismutase 1 (SOD1).
Harlan BA; Pehar M; Sharma DR; Beeson G; Beeson CC; Vargas MR
J Biol Chem; 2016 May; 291(20):10836-46. PubMed ID: 27002158
[TBL] [Abstract][Full Text] [Related]
23. [Familial amyotrophic lateral sclerosis and mutations in the Cu/Zn superoxide dismutase gene].
Nakano R
Rinsho Shinkeigaku; 1995 Dec; 35(12):1546-8. PubMed ID: 8752459
[TBL] [Abstract][Full Text] [Related]
24. Aggregates of mutant protein appear progressively in dendrites, in periaxonal processes of oligodendrocytes, and in neuronal and astrocytic perikarya of mice expressing the SOD1(G93A) mutation of familial amyotrophic lateral sclerosis.
Stieber A; Gonatas JO; Gonatas NK
J Neurol Sci; 2000 Aug; 177(2):114-23. PubMed ID: 10980307
[TBL] [Abstract][Full Text] [Related]
25. Mutant SOD1 linked to familial amyotrophic lateral sclerosis, but not wild-type SOD1, induces ER stress in COS7 cells and transgenic mice.
Tobisawa S; Hozumi Y; Arawaka S; Koyama S; Wada M; Nagai M; Aoki M; Itoyama Y; Goto K; Kato T
Biochem Biophys Res Commun; 2003 Apr; 303(2):496-503. PubMed ID: 12659845
[TBL] [Abstract][Full Text] [Related]
26. In vivo pathogenic role of mutant SOD1 localized in the mitochondrial intermembrane space.
Igoudjil A; Magrané J; Fischer LR; Kim HJ; Hervias I; Dumont M; Cortez C; Glass JD; Starkov AA; Manfredi G
J Neurosci; 2011 Nov; 31(44):15826-37. PubMed ID: 22049426
[TBL] [Abstract][Full Text] [Related]
27. Wild-type nonneuronal cells extend survival of SOD1 mutant motor neurons in ALS mice.
Clement AM; Nguyen MD; Roberts EA; Garcia ML; Boillée S; Rule M; McMahon AP; Doucette W; Siwek D; Ferrante RJ; Brown RH; Julien JP; Goldstein LS; Cleveland DW
Science; 2003 Oct; 302(5642):113-7. PubMed ID: 14526083
[TBL] [Abstract][Full Text] [Related]
28. Selective loss of neurofilament expression in Cu/Zn superoxide dismutase (SOD1) linked amyotrophic lateral sclerosis.
Menzies FM; Grierson AJ; Cookson MR; Heath PR; Tomkins J; Figlewicz DA; Ince PG; Shaw PJ
J Neurochem; 2002 Sep; 82(5):1118-28. PubMed ID: 12358759
[TBL] [Abstract][Full Text] [Related]
29. Proteasomal inhibition by misfolded mutant superoxide dismutase 1 induces selective motor neuron death in familial amyotrophic lateral sclerosis.
Urushitani M; Kurisu J; Tsukita K; Takahashi R
J Neurochem; 2002 Dec; 83(5):1030-42. PubMed ID: 12437574
[TBL] [Abstract][Full Text] [Related]
30. Mitochondria-targeted catalase reverts the neurotoxicity of hSOD1G⁹³A astrocytes without extending the survival of ALS-linked mutant hSOD1 mice.
Pehar M; Beeson G; Beeson CC; Johnson JA; Vargas MR
PLoS One; 2014; 9(7):e103438. PubMed ID: 25054289
[TBL] [Abstract][Full Text] [Related]
31. Cell death in amyotrophic lateral sclerosis: interplay between neuronal and glial cells.
Ferri A; Nencini M; Casciati A; Cozzolino M; Angelini DF; Longone P; Spalloni A; Rotilio G; Carrì MT
FASEB J; 2004 Aug; 18(11):1261-3. PubMed ID: 15208263
[TBL] [Abstract][Full Text] [Related]
32. Knocking down metabotropic glutamate receptor 1 improves survival and disease progression in the SOD1(G93A) mouse model of amyotrophic lateral sclerosis.
Milanese M; Giribaldi F; Melone M; Bonifacino T; Musante I; Carminati E; Rossi PI; Vergani L; Voci A; Conti F; Puliti A; Bonanno G
Neurobiol Dis; 2014 Apr; 64():48-59. PubMed ID: 24361555
[TBL] [Abstract][Full Text] [Related]
33. Coincident thresholds of mutant protein for paralytic disease and protein aggregation caused by restrictively expressed superoxide dismutase cDNA.
Wang J; Xu G; Slunt HH; Gonzales V; Coonfield M; Fromholt D; Copeland NG; Jenkins NA; Borchelt DR
Neurobiol Dis; 2005 Dec; 20(3):943-52. PubMed ID: 16046140
[TBL] [Abstract][Full Text] [Related]
34. Metabolic dysfunction in familial, but not sporadic, amyotrophic lateral sclerosis.
Browne SE; Bowling AC; Baik MJ; Gurney M; Brown RH; Beal MF
J Neurochem; 1998 Jul; 71(1):281-7. PubMed ID: 9648876
[TBL] [Abstract][Full Text] [Related]
35. The mitochondrial permeability transition pore in motor neurons: involvement in the pathobiology of ALS mice.
Martin LJ; Gertz B; Pan Y; Price AC; Molkentin JD; Chang Q
Exp Neurol; 2009 Aug; 218(2):333-46. PubMed ID: 19272377
[TBL] [Abstract][Full Text] [Related]
36. Pathological Modification of TDP-43 in Amyotrophic Lateral Sclerosis with SOD1 Mutations.
Jeon GS; Shim YM; Lee DY; Kim JS; Kang M; Ahn SH; Shin JY; Geum D; Hong YH; Sung JJ
Mol Neurobiol; 2019 Mar; 56(3):2007-2021. PubMed ID: 29982983
[TBL] [Abstract][Full Text] [Related]
37. Recruitment of mitochondria into apoptotic signaling correlates with the presence of inclusions formed by amyotrophic lateral sclerosis-associated SOD1 mutations.
Soo KY; Atkin JD; Horne MK; Nagley P
J Neurochem; 2009 Feb; 108(3):578-90. PubMed ID: 19046404
[TBL] [Abstract][Full Text] [Related]
38. Mutant superoxide dismutase 1 forms aggregates in the brain mitochondrial matrix of amyotrophic lateral sclerosis mice.
Vijayvergiya C; Beal MF; Buck J; Manfredi G
J Neurosci; 2005 Mar; 25(10):2463-70. PubMed ID: 15758154
[TBL] [Abstract][Full Text] [Related]
39. Cytochrome c association with the inner mitochondrial membrane is impaired in the CNS of G93A-SOD1 mice.
Kirkinezos IG; Bacman SR; Hernandez D; Oca-Cossio J; Arias LJ; Perez-Pinzon MA; Bradley WG; Moraes CT
J Neurosci; 2005 Jan; 25(1):164-72. PubMed ID: 15634778
[TBL] [Abstract][Full Text] [Related]
40. Aggregation and motor neuron toxicity of an ALS-linked SOD1 mutant independent from wild-type SOD1.
Bruijn LI; Houseweart MK; Kato S; Anderson KL; Anderson SD; Ohama E; Reaume AG; Scott RW; Cleveland DW
Science; 1998 Sep; 281(5384):1851-4. PubMed ID: 9743498
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]
