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4. Characterization of the testis and epididymis in mouse models of human Tay Sachs and Sandhoff diseases and partial determination of accumulated gangliosides. Trasler J; Saberi F; Somani IH; Adamali HI; Huang JQ; Fortunato SR; Ritter G; Gu M; Aebersold R; Gravel RA; Hermo L Endocrinology; 1998 Jul; 139(7):3280-8. PubMed ID: 9645704 [TBL] [Abstract][Full Text] [Related]
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7. Biochemistry and genetics of gangliosidoses. Sandhoff K; Christomanou H Hum Genet; 1979; 50(2):107-43. PubMed ID: 116955 [TBL] [Abstract][Full Text] [Related]
8. Biology and potential strategies for the treatment of GM2 gangliosidoses. Chavany C; Jendoubi M Mol Med Today; 1998 Apr; 4(4):158-65. PubMed ID: 9572057 [TBL] [Abstract][Full Text] [Related]
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10. Glycosphingolipid degradation and animal models of GM2-gangliosidoses. Kolter T; Sandhoff K J Inherit Metab Dis; 1998 Aug; 21(5):548-63. PubMed ID: 9728335 [TBL] [Abstract][Full Text] [Related]
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12. Gangliosidoses and the fetal retina. Cogan DG; Kuwabara T; Kolodny E; Driscoll S Ophthalmology; 1984 May; 91(5):508-12. PubMed ID: 6330639 [TBL] [Abstract][Full Text] [Related]
13. Natural history study of glycan accumulation in large animal models of GM2 gangliosidoses. Cavender C; Mangini L; Van Vleet JL; Corado C; McCullagh E; Gray-Edwards HL; Martin DR; Crawford BE; Lawrence R PLoS One; 2020; 15(12):e0243006. PubMed ID: 33259552 [TBL] [Abstract][Full Text] [Related]
14. Biomarkers of central nervous system inflammation in infantile and juvenile gangliosidoses. Utz JR; Crutcher T; Schneider J; Sorgen P; Whitley CB Mol Genet Metab; 2015 Feb; 114(2):274-80. PubMed ID: 25557439 [TBL] [Abstract][Full Text] [Related]
15. Lysosomal acid hydrolases in established lymphoblastoid cell lines, transformed by Epstein-Barr virus, from patients with genetic lysosomal storage diseases. Minami R; Watanabe Y; Kudoh T; Suzuki M; Oyanagi K; Orii T; Nakao T Hum Genet; 1978 Oct; 44(1):79-87. PubMed ID: 213379 [TBL] [Abstract][Full Text] [Related]
16. Gangliosides and gangliosidoses: principles of molecular and metabolic pathogenesis. Sandhoff K; Harzer K J Neurosci; 2013 Jun; 33(25):10195-208. PubMed ID: 23785136 [TBL] [Abstract][Full Text] [Related]
17. The biochemical basis of gangliosidoses. Sandhoff K; Conzelmann E Neuropediatrics; 1984 Sep; 15 Suppl():85-92. PubMed ID: 6242704 [No Abstract] [Full Text] [Related]