174 related articles for article (PubMed ID: 11756421)
1. Cellular phenotyping of secretory and nuclear prion proteins associated with inherited prion diseases.
Lorenz H; Windl O; Kretzschmar HA
J Biol Chem; 2002 Mar; 277(10):8508-16. PubMed ID: 11756421
[TBL] [Abstract][Full Text] [Related]
2. Aggresome formation by mutant prion proteins: the unfolding role of proteasomes in familial prion disorders.
Mishra RS; Bose S; Gu Y; Li R; Singh N
J Alzheimers Dis; 2003 Feb; 5(1):15-23. PubMed ID: 12590162
[TBL] [Abstract][Full Text] [Related]
3. Recombinant human prion protein mutants huPrP D178N/M129 (FFI) and huPrP+9OR (fCJD) reveal proteinase K resistance.
Gauczynski S; Krasemann S; Bodemer W; Weiss S
J Cell Sci; 2002 Nov; 115(Pt 21):4025-36. PubMed ID: 12356908
[TBL] [Abstract][Full Text] [Related]
4. Allelic origin of the abnormal prion protein isoform in familial prion diseases.
Chen SG; Parchi P; Brown P; Capellari S; Zou W; Cochran EJ; Vnencak-Jones CL; Julien J; Vital C; Mikol J; Lugaresi E; Autilio-Gambetti L; Gambetti P
Nat Med; 1997 Sep; 3(9):1009-15. PubMed ID: 9288728
[TBL] [Abstract][Full Text] [Related]
5. PrP(ST), a soluble, protease resistant and truncated PrP form features in the pathogenesis of a genetic prion disease.
Friedman-Levi Y; Mizrahi M; Frid K; Binyamin O; Gabizon R
PLoS One; 2013; 8(7):e69583. PubMed ID: 23922744
[TBL] [Abstract][Full Text] [Related]
6. Selective processing and metabolism of disease-causing mutant prion proteins.
Ashok A; Hegde RS
PLoS Pathog; 2009 Jun; 5(6):e1000479. PubMed ID: 19543376
[TBL] [Abstract][Full Text] [Related]
7. Phenotypic heterogeneity in inherited prion disease (P102L) is associated with differential propagation of protease-resistant wild-type and mutant prion protein.
Wadsworth JD; Joiner S; Linehan JM; Cooper S; Powell C; Mallinson G; Buckell J; Gowland I; Asante EA; Budka H; Brandner S; Collinge J
Brain; 2006 Jun; 129(Pt 6):1557-69. PubMed ID: 16597650
[TBL] [Abstract][Full Text] [Related]
8. Association of prion protein genotype and scrapie prion protein type with cellular prion protein charge isoform profiles in cerebrospinal fluid of humans with sporadic or familial prion diseases.
Schmitz M; Lüllmann K; Zafar S; Ebert E; Wohlhage M; Oikonomou P; Schlomm M; Mitrova E; Beekes M; Zerr I
Neurobiol Aging; 2014 May; 35(5):1177-88. PubMed ID: 24360565
[TBL] [Abstract][Full Text] [Related]
9. Distinct glycoform ratios of protease resistant prion protein associated with PRNP point mutations.
Hill AF; Joiner S; Beck JA; Campbell TA; Dickinson A; Poulter M; Wadsworth JD; Collinge J
Brain; 2006 Mar; 129(Pt 3):676-85. PubMed ID: 16415305
[TBL] [Abstract][Full Text] [Related]
10. Two mutant prion proteins expressed in cultured cells acquire biochemical properties reminiscent of the scrapie isoform.
Lehmann S; Harris DA
Proc Natl Acad Sci U S A; 1996 May; 93(11):5610-4. PubMed ID: 8643624
[TBL] [Abstract][Full Text] [Related]
11. Nanopore analysis of wild-type and mutant prion protein (PrP(C)): single molecule discrimination and PrP(C) kinetics.
Jetha NN; Semenchenko V; Wishart DS; Cashman NR; Marziali A
PLoS One; 2013; 8(2):e54982. PubMed ID: 23393562
[TBL] [Abstract][Full Text] [Related]
12. Prion neurotoxicity: insights from prion protein mutants.
Solomon IH; Schepker JA; Harris DA
Curr Issues Mol Biol; 2010; 12(2):51-61. PubMed ID: 19767650
[TBL] [Abstract][Full Text] [Related]
13. Epitope scanning indicates structural differences in brain-derived monomeric and aggregated mutant prion proteins related to genetic prion diseases.
Tapella L; Stravalaci M; Bastone A; Biasini E; Gobbi M; Chiesa R
Biochem J; 2013 Sep; 454(3):417-25. PubMed ID: 23808898
[TBL] [Abstract][Full Text] [Related]
14. Roles of methionine oxidation in E200K prion protein misfolding: Implications for the mechanism of pathogenesis in E200K linked familial Creutzfeldt-Jakob disease.
Wang Z; Feng B; Xiao G; Zhou Z
Biochim Biophys Acta; 2016 Apr; 1864(4):346-58. PubMed ID: 26779934
[TBL] [Abstract][Full Text] [Related]
15. Towards authentic transgenic mouse models of heritable PrP prion diseases.
Watts JC; Giles K; Bourkas ME; Patel S; Oehler A; Gavidia M; Bhardwaj S; Lee J; Prusiner SB
Acta Neuropathol; 2016 Oct; 132(4):593-610. PubMed ID: 27350609
[TBL] [Abstract][Full Text] [Related]
16. Prion Strain Characterization of a Novel Subtype of Creutzfeldt-Jakob Disease.
Galeno R; Di Bari MA; Nonno R; Cardone F; Sbriccoli M; Graziano S; Ingrosso L; Fiorini M; Valanzano A; Pasini G; Poleggi A; Vinci R; Ladogana A; Puopolo M; Monaco S; Agrimi U; Zanusso G; Pocchiari M
J Virol; 2017 Jun; 91(11):. PubMed ID: 28298604
[TBL] [Abstract][Full Text] [Related]
17. Prion encephalopathies of animals and humans.
Prusiner SB
Dev Biol Stand; 1993; 80():31-44. PubMed ID: 8270114
[TBL] [Abstract][Full Text] [Related]
18. Requirements for mutant and wild-type prion protein misfolding in vitro.
Noble GP; Walsh DJ; Miller MB; Jackson WS; Supattapone S
Biochemistry; 2015 Feb; 54(5):1180-7. PubMed ID: 25584902
[TBL] [Abstract][Full Text] [Related]
19. Prion protein transgenes and the neuropathology in prion diseases.
DeArmond SJ; Prusiner SB
Brain Pathol; 1995 Jan; 5(1):77-89. PubMed ID: 7767493
[TBL] [Abstract][Full Text] [Related]
20. Anti-prion drugs do not improve survival in novel knock-in models of inherited prion disease.
Walsh DJ; Rees JR; Mehra S; Bourkas MEC; Kaczmarczyk L; Stuart E; Jackson WS; Watts JC; Supattapone S
PLoS Pathog; 2024 Apr; 20(4):e1012087. PubMed ID: 38557815
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]