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3. The Hermansky-Pudlak syndrome 1 (HPS1) and HPS2 genes independently contribute to the production and function of platelet dense granules, melanosomes, and lysosomes. Feng L; Novak EK; Hartnell LM; Bonifacino JS; Collinson LM; Swank RT Blood; 2002 Mar; 99(5):1651-8. PubMed ID: 11861280 [TBL] [Abstract][Full Text] [Related]
4. Cappuccino, a mouse model of Hermansky-Pudlak syndrome, encodes a novel protein that is part of the pallidin-muted complex (BLOC-1). Ciciotte SL; Gwynn B; Moriyama K; Huizing M; Gahl WA; Bonifacino JS; Peters LL Blood; 2003 Jun; 101(11):4402-7. PubMed ID: 12576321 [TBL] [Abstract][Full Text] [Related]
5. Mouse pale ear (ep) is homologous to human Hermansky-Pudlak syndrome and contains a rare 'AT-AC' intron. Feng GH; Bailin T; Oh J; Spritz RA Hum Mol Genet; 1997 May; 6(5):793-7. PubMed ID: 9158155 [TBL] [Abstract][Full Text] [Related]
6. Reduced pigmentation (rp), a mouse model of Hermansky-Pudlak syndrome, encodes a novel component of the BLOC-1 complex. Gwynn B; Martina JA; Bonifacino JS; Sviderskaya EV; Lamoreux ML; Bennett DC; Moriyama K; Huizing M; Helip-Wooley A; Gahl WA; Webb LS; Lambert AJ; Peters LL Blood; 2004 Nov; 104(10):3181-9. PubMed ID: 15265785 [TBL] [Abstract][Full Text] [Related]
8. Hermansky-Pudlak syndrome type 7 (HPS-7) results from mutant dysbindin, a member of the biogenesis of lysosome-related organelles complex 1 (BLOC-1). Li W; Zhang Q; Oiso N; Novak EK; Gautam R; O'Brien EP; Tinsley CL; Blake DJ; Spritz RA; Copeland NG; Jenkins NA; Amato D; Roe BA; Starcevic M; Dell'Angelica EC; Elliott RW; Mishra V; Kingsmore SF; Paylor RE; Swank RT Nat Genet; 2003 Sep; 35(1):84-9. PubMed ID: 12923531 [TBL] [Abstract][Full Text] [Related]
9. Melanoregulin, product of the dsu locus, links the BLOC-pathway and OA1 in organelle biogenesis. Rachel RA; Nagashima K; O'Sullivan TN; Frost LS; Stefano FP; Marigo V; Boesze-Battaglia K PLoS One; 2012; 7(9):e42446. PubMed ID: 22984402 [TBL] [Abstract][Full Text] [Related]
10. The mouse organellar biogenesis mutant buff results from a mutation in Vps33a, a homologue of yeast vps33 and Drosophila carnation. Suzuki T; Oiso N; Gautam R; Novak EK; Panthier JJ; Suprabha PG; Vida T; Swank RT; Spritz RA Proc Natl Acad Sci U S A; 2003 Feb; 100(3):1146-50. PubMed ID: 12538872 [TBL] [Abstract][Full Text] [Related]
11. Abnormal vesicular trafficking in mouse models of Hermansky-Pudlak syndrome. Swank RT; Novak EK; McGarry MP; Zhang Y; Li W; Zhang Q; Feng L Pigment Cell Res; 2000; 13 Suppl 8():59-67. PubMed ID: 11041359 [TBL] [Abstract][Full Text] [Related]
12. Characterization of melanosomes in murine Hermansky-Pudlak syndrome: mechanisms of hypopigmentation. Nguyen T; Wei ML J Invest Dermatol; 2004 Feb; 122(2):452-60. PubMed ID: 15009730 [TBL] [Abstract][Full Text] [Related]
13. SLC35D3 delivery from megakaryocyte early endosomes is required for platelet dense granule biogenesis and is differentially defective in Hermansky-Pudlak syndrome models. Meng R; Wang Y; Yao Y; Zhang Z; Harper DC; Heijnen HF; Sitaram A; Li W; Raposo G; Weiss MJ; Poncz M; Marks MS Blood; 2012 Jul; 120(2):404-14. PubMed ID: 22611153 [TBL] [Abstract][Full Text] [Related]
14. The regulation of platelet-dense granules by Rab27a in the ashen mouse, a model of Hermansky-Pudlak and Griscelli syndromes, is granule-specific and dependent on genetic background. Novak EK; Gautam R; Reddington M; Collinson LM; Copeland NG; Jenkins NA; McGarry MP; Swank RT Blood; 2002 Jul; 100(1):128-35. PubMed ID: 12070017 [TBL] [Abstract][Full Text] [Related]
15. Hermansky-Pudlak syndrome is caused by mutations in HPS4, the human homolog of the mouse light-ear gene. Suzuki T; Li W; Zhang Q; Karim A; Novak EK; Sviderskaya EV; Hill SP; Bennett DC; Levin AV; Nieuwenhuis HK; Fong CT; Castellan C; Miterski B; Swank RT; Spritz RA Nat Genet; 2002 Mar; 30(3):321-4. PubMed ID: 11836498 [TBL] [Abstract][Full Text] [Related]
16. no privacy, a Xenopus tropicalis mutant, is a model of human Hermansky-Pudlak Syndrome and allows visualization of internal organogenesis during tadpole development. Nakayama T; Nakajima K; Cox A; Fisher M; Howell M; Fish MB; Yaoita Y; Grainger RM Dev Biol; 2017 Jun; 426(2):472-486. PubMed ID: 27595926 [TBL] [Abstract][Full Text] [Related]
17. Identification of snapin and three novel proteins (BLOS1, BLOS2, and BLOS3/reduced pigmentation) as subunits of biogenesis of lysosome-related organelles complex-1 (BLOC-1). Starcevic M; Dell'Angelica EC J Biol Chem; 2004 Jul; 279(27):28393-401. PubMed ID: 15102850 [TBL] [Abstract][Full Text] [Related]
18. The Drosophila pigmentation gene pink (p) encodes a homologue of human Hermansky-Pudlak syndrome 5 (HPS5). Falcón-Pérez JM; Romero-Calderón R; Brooks ES; Krantz DE; Dell'Angelica EC Traffic; 2007 Feb; 8(2):154-68. PubMed ID: 17156100 [TBL] [Abstract][Full Text] [Related]
19. The mouse pale ear (ep) mutation is the homologue of human Hermansky-Pudlak syndrome. Gardner JM; Wildenberg SC; Keiper NM; Novak EK; Rusiniak ME; Swank RT; Puri N; Finger JN; Hagiwara N; Lehman AL; Gales TL; Bayer ME; King RA; Brilliant MH Proc Natl Acad Sci U S A; 1997 Aug; 94(17):9238-43. PubMed ID: 9256466 [TBL] [Abstract][Full Text] [Related]
20. Defects in the cappuccino (cno) gene on mouse chromosome 5 and human 4p cause Hermansky-Pudlak syndrome by an AP-3-independent mechanism. Gwynn B; Ciciotte SL; Hunter SJ; Washburn LL; Smith RS; Andersen SG; Swank RT; Dell'Angelica EC; Bonifacino JS; Eicher EM; Peters LL Blood; 2000 Dec; 96(13):4227-35. PubMed ID: 11110696 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]