These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
116 related articles for article (PubMed ID: 12013828)
21. Intact alpha-subunit is required for membrane-binding of human mitochondrial trifunctional beta-oxidation protein, but is not necessary for conferring 3-ketoacyl-CoA thiolase activity to the beta-subunit. Weinberger MJ; Rinaldo P; Strauss AW; Bennett MJ Biochem Biophys Res Commun; 1995 Apr; 209(1):47-52. PubMed ID: 7726862 [TBL] [Abstract][Full Text] [Related]
22. The crystal structure of human mitochondrial 3-ketoacyl-CoA thiolase (T1): insight into the reaction mechanism of its thiolase and thioesterase activities. Kiema TR; Harijan RK; Strozyk M; Fukao T; Alexson SE; Wierenga RK Acta Crystallogr D Biol Crystallogr; 2014 Dec; 70(Pt 12):3212-25. PubMed ID: 25478839 [TBL] [Abstract][Full Text] [Related]
23. Disorders of mitochondrial fatty acyl-CoA beta-oxidation. Wanders RJ; Vreken P; den Boer ME; Wijburg FA; van Gennip AH; IJlst L J Inherit Metab Dis; 1999 Jun; 22(4):442-87. PubMed ID: 10407780 [TBL] [Abstract][Full Text] [Related]
24. Defect in biosynthesis of mitochondrial acetoacetyl-coenzyme A thiolase in cultured fibroblasts from a boy with 3-ketothiolase deficiency. Yamaguchi S; Orii T; Sakura N; Miyazawa S; Hashimoto T J Clin Invest; 1988 Mar; 81(3):813-7. PubMed ID: 2893809 [TBL] [Abstract][Full Text] [Related]
25. Beneficial effects of trimetazidine in ex vivo working ischemic hearts are due to a stimulation of glucose oxidation secondary to inhibition of long-chain 3-ketoacyl coenzyme a thiolase. Lopaschuk GD; Barr R; Thomas PD; Dyck JR Circ Res; 2003 Aug; 93(3):e33-7. PubMed ID: 12869392 [TBL] [Abstract][Full Text] [Related]
26. Diagnosis of mitochondrial fatty acid oxidation defects. Duran M; Bruinvis L; Ketting D; Dorland L Padiatr Padol; 1993; 28(1):19-25. PubMed ID: 8446424 [TBL] [Abstract][Full Text] [Related]
27. Biochemical profiling in two siblings with mitochondrial 2-methylacetoacetyl-CoA thiolase deficiency. Ngu LH; Zabedah MY; Shanti B; Teh SH Malays J Pathol; 2008 Dec; 30(2):109-14. PubMed ID: 19291920 [TBL] [Abstract][Full Text] [Related]
28. Identification of three novel frameshift mutations (83delAT, 754insCT, and 435 + 1G to A) of mitochondrial acetoacetyl-coenzyme A thiolase gene in two Swiss patients with CRM-negative beta-ketothiolase deficiency. Fukao T; Song XQ; Yamaguchi S; Kondo N; Orii T; Matthieu JM; Bachmann C; Hashimoto T Hum Mutat; 1997; 9(3):277-9. PubMed ID: 9090533 [No Abstract] [Full Text] [Related]
33. The 1.8 A crystal structure of the dimeric peroxisomal 3-ketoacyl-CoA thiolase of Saccharomyces cerevisiae: implications for substrate binding and reaction mechanism. Mathieu M; Modis Y; Zeelen JP; Engel CK; Abagyan RA; Ahlberg A; Rasmussen B; Lamzin VS; Kunau WH; Wierenga RK J Mol Biol; 1997 Oct; 273(3):714-28. PubMed ID: 9402066 [TBL] [Abstract][Full Text] [Related]
34. Fatty acid beta-oxidation in peroxisomes and mitochondria: the first, unequivocal evidence for the involvement of carnitine in shuttling propionyl-CoA from peroxisomes to mitochondria. Jakobs BS; Wanders RJ Biochem Biophys Res Commun; 1995 Aug; 213(3):1035-41. PubMed ID: 7654220 [TBL] [Abstract][Full Text] [Related]
35. The promiscuous enzyme medium-chain 3-keto-acyl-CoA thiolase triggers a vicious cycle in fatty-acid beta-oxidation. Martines AMF; van Eunen K; Reijngoud DJ; Bakker BM PLoS Comput Biol; 2017 Apr; 13(4):e1005461. PubMed ID: 28369071 [TBL] [Abstract][Full Text] [Related]
36. Mitochondrial metabolism of 3-mercaptopropionic acid. Chemical synthesis of 3-mercaptopropionyl coenzyme A and some of its S-acyl derivatives. Cuebas D; Beckmann JD; Frerman FE; Schulz H J Biol Chem; 1985 Jun; 260(12):7330-6. PubMed ID: 3997872 [TBL] [Abstract][Full Text] [Related]
37. Inhibition of mitochondrial fatty acid elongation by antibodies to 3-ketoacyl-CoA thiolase. Staack H; Davidson B; Schulz H Lipids; 1980 Mar; 15(3):175-8. PubMed ID: 7374368 [TBL] [Abstract][Full Text] [Related]
38. Metabolism of 4-pentenoic acid and inhibition of thiolase by metabolites of 4-pentenoic acid. Schulz H Biochemistry; 1983 Apr; 22(8):1827-32. PubMed ID: 6133549 [TBL] [Abstract][Full Text] [Related]