55 related articles for article (PubMed ID: 12014008)
1. [Mitochondrial enoyl-CoA hydratase].
Yamaguchi S
Nihon Rinsho; 2002 Apr; 60 Suppl 4():98-100. PubMed ID: 12014008
[No Abstract] [Full Text] [Related]
2. [Mitochondrial acyl-CoA dehydrogenases (VLCAD, LCAD, MCAD, SCAD)].
Yamaguchi S
Nihon Rinsho; 2002 Apr; 60 Suppl 4():94-7. PubMed ID: 12014007
[No Abstract] [Full Text] [Related]
3. [Mitochondrial 3-ketoacyl-CoA thiolase].
Yamaguchi S; Kanai R
Nihon Rinsho; 2002 Apr; 60 Suppl 4():105-8. PubMed ID: 12013828
[No Abstract] [Full Text] [Related]
4. [Mitochondrial 3-hydroxyacyl-CoA dehydrogenase (SCHAD, LCHAD)].
Yamaguchi S
Nihon Rinsho; 2002 Apr; 60 Suppl 4():101-4. PubMed ID: 12013827
[No Abstract] [Full Text] [Related]
5. Combined enzyme defect of mitochondrial fatty acid oxidation.
Jackson S; Kler RS; Bartlett K; Briggs H; Bindoff LA; Pourfarzam M; Gardner-Medwin D; Turnbull DM
J Clin Invest; 1992 Oct; 90(4):1219-25. PubMed ID: 1401059
[TBL] [Abstract][Full Text] [Related]
6. Comparative inhibition studies of enoyl-CoA hydratase 1 and enoyl-CoA hydratase 2 in long-chain fatty acid oxidation.
Wu L; Lin S; Li D
Org Lett; 2008 Aug; 10(15):3355-8. PubMed ID: 18611036
[TBL] [Abstract][Full Text] [Related]
7. Combined defect of long-chain 3-hydroxyacyl-CoA dehydrogenase, 2-enoyl-CoA hydratase and 3-oxoacyl-CoA thiolase.
Jackson S; Kler RS; Bartlett K; Pourfarzam M; Aynsley-Green A; Bindoff LA; Turnbull DM
Prog Clin Biol Res; 1992; 375():327-37. PubMed ID: 1438378
[No Abstract] [Full Text] [Related]
8. Glutamate-119 of the large alpha-subunit is the catalytic base in the hydration of 2-trans-enoyl-coenzyme A catalyzed by the multienzyme complex of fatty acid oxidation from Escherichia coli.
He XY; Yang SY
Biochemistry; 1997 Sep; 36(36):11044-9. PubMed ID: 9283097
[TBL] [Abstract][Full Text] [Related]
9. Detection of acyl-CoA beta-oxidation enzymes in peroxisomes (microperoxisomes) of mouse heart.
Connock MJ; Perry SR
Biochem Int; 1983 Apr; 6(4):545-51. PubMed ID: 6679723
[TBL] [Abstract][Full Text] [Related]
10. [Recent progress of mitochondrial fatty acid oxidation system].
Uchida Y; Ushikubo S; Kamijo T; Aoyama T; Hashimoto T
Tanpakushitsu Kakusan Koso; 1993 Jul; 38(9):1466-74. PubMed ID: 8356216
[No Abstract] [Full Text] [Related]
11. Mitochondrial beta-oxidation.
Schulz H
Prog Clin Biol Res; 1990; 321():23-36. PubMed ID: 2183234
[No Abstract] [Full Text] [Related]
12. Mitochondrial trifunctional protein deficiency. Catalytic heterogeneity of the mutant enzyme in two patients.
Kamijo T; Wanders RJ; Saudubray JM; Aoyama T; Komiyama A; Hashimoto T
J Clin Invest; 1994 Apr; 93(4):1740-7. PubMed ID: 8163672
[TBL] [Abstract][Full Text] [Related]
13. Clinical, biochemical and metabolic characterisation of a mild form of human short-chain enoyl-CoA hydratase deficiency: significance of increased N-acetyl-S-(2-carboxypropyl)cysteine excretion.
Yamada K; Aiba K; Kitaura Y; Kondo Y; Nomura N; Nakamura Y; Fukushi D; Murayama K; Shimomura Y; Pitt J; Yamaguchi S; Yokochi K; Wakamatsu N
J Med Genet; 2015 Oct; 52(10):691-8. PubMed ID: 26251176
[TBL] [Abstract][Full Text] [Related]
14. The crystal structure of enoyl-CoA hydratase complexed with octanoyl-CoA reveals the structural adaptations required for binding of a long chain fatty acid-CoA molecule.
Engel CK; Kiema TR; Hiltunen JK; Wierenga RK
J Mol Biol; 1998 Feb; 275(5):847-59. PubMed ID: 9480773
[TBL] [Abstract][Full Text] [Related]
15. [Mitochondrial trifunctional protein].
Uchiyama A; Yamaguchi S
Nihon Rinsho; 2002 Apr; 60 Suppl 4():109-12. PubMed ID: 12013829
[No Abstract] [Full Text] [Related]
16. Synthesis of crotonyl-oxyCoA: a mechanistic probe of the reaction catalyzed by enoyl-CoA hydratase.
Dai M; Feng Y; Tonge PJ
J Am Chem Soc; 2001 Jan; 123(3):506-7. PubMed ID: 11456558
[No Abstract] [Full Text] [Related]
17. Mutation analysis in mitochondrial fatty acid oxidation defects: Exemplified by acyl-CoA dehydrogenase deficiencies, with special focus on genotype-phenotype relationship.
Gregersen N; Andresen BS; Corydon MJ; Corydon TJ; Olsen RK; Bolund L; Bross P
Hum Mutat; 2001 Sep; 18(3):169-89. PubMed ID: 11524729
[TBL] [Abstract][Full Text] [Related]
18. Role of short-chain hydroxyacyl CoA dehydrogenases in SCHAD deficiency.
Filling C; Keller B; Hirschberg D; Marschall HU; Jörnvall H; Bennett MJ; Oppermann U
Biochem Biophys Res Commun; 2008 Mar; 368(1):6-11. PubMed ID: 18036338
[TBL] [Abstract][Full Text] [Related]
19. beta-hydroxyisobutyryl coenzyme A deacylase deficiency: a defect in valine metabolism associated with physical malformations.
Brown GK; Hunt SM; Scholem R; Fowler K; Grimes A; Mercer JF; Truscott RM; Cotton RG; Rogers JG; Danks DM
Pediatrics; 1982 Oct; 70(4):532-8. PubMed ID: 7122152
[TBL] [Abstract][Full Text] [Related]
20. Peroxisomal and mitochondrial enzymes.
Hashimoto T
Prog Clin Biol Res; 1992; 375():19-32. PubMed ID: 1438364
[No Abstract] [Full Text] [Related]
[Next] [New Search]