224 related articles for article (PubMed ID: 12165555)
1. Polyglutamine and transcription: gene expression changes shared by DRPLA and Huntington's disease mouse models reveal context-independent effects.
Luthi-Carter R; Strand AD; Hanson SA; Kooperberg C; Schilling G; La Spada AR; Merry DE; Young AB; Ross CA; Borchelt DR; Olson JM
Hum Mol Genet; 2002 Aug; 11(17):1927-37. PubMed ID: 12165555
[TBL] [Abstract][Full Text] [Related]
2. Increased huntingtin protein length reduces the number of polyglutamine-induced gene expression changes in mouse models of Huntington's disease.
Chan EY; Luthi-Carter R; Strand A; Solano SM; Hanson SA; DeJohn MM; Kooperberg C; Chase KO; DiFiglia M; Young AB; Leavitt BR; Cha JH; Aronin N; Hayden MR; Olson JM
Hum Mol Genet; 2002 Aug; 11(17):1939-51. PubMed ID: 12165556
[TBL] [Abstract][Full Text] [Related]
3. Polyglutamine pathogenesis.
Ross CA; Wood JD; Schilling G; Peters MF; Nucifora FC; Cooper JK; Sharp AH; Margolis RL; Borchelt DR
Philos Trans R Soc Lond B Biol Sci; 1999 Jun; 354(1386):1005-11. PubMed ID: 10434299
[TBL] [Abstract][Full Text] [Related]
4. Dysregulation of gene expression in the R6/2 model of polyglutamine disease: parallel changes in muscle and brain.
Luthi-Carter R; Hanson SA; Strand AD; Bergstrom DA; Chun W; Peters NL; Woods AM; Chan EY; Kooperberg C; Krainc D; Young AB; Tapscott SJ; Olson JM
Hum Mol Genet; 2002 Aug; 11(17):1911-26. PubMed ID: 12165554
[TBL] [Abstract][Full Text] [Related]
5. FAT10 protein binds to polyglutamine proteins and modulates their solubility.
Nagashima Y; Kowa H; Tsuji S; Iwata A
J Biol Chem; 2011 Aug; 286(34):29594-600. PubMed ID: 21757738
[TBL] [Abstract][Full Text] [Related]
6. Targeting several CAG expansion diseases by a single antisense oligonucleotide.
Evers MM; Pepers BA; van Deutekom JC; Mulders SA; den Dunnen JT; Aartsma-Rus A; van Ommen GJ; van Roon-Mom WM
PLoS One; 2011; 6(9):e24308. PubMed ID: 21909428
[TBL] [Abstract][Full Text] [Related]
7. Nuclear localization of a non-caspase truncation product of atrophin-1, with an expanded polyglutamine repeat, increases cellular toxicity.
Nucifora FC; Ellerby LM; Wellington CL; Wood JD; Herring WJ; Sawa A; Hayden MR; Dawson VL; Dawson TM; Ross CA
J Biol Chem; 2003 Apr; 278(15):13047-55. PubMed ID: 12464607
[TBL] [Abstract][Full Text] [Related]
8. Proteolytic processing regulates pathological accumulation in dentatorubral-pallidoluysian atrophy.
Suzuki Y; Nakayama K; Hashimoto N; Yazawa I
FEBS J; 2010 Dec; 277(23):4873-87. PubMed ID: 20977674
[TBL] [Abstract][Full Text] [Related]
9. Increased aggregation of polyleucine compared with that of polyglutamine in dentatorubral-pallidoluysian atrophy protein.
Suzuki Y; Jin C; Yazawa I
Neurosci Lett; 2013 Sep; 552():156-61. PubMed ID: 23933208
[TBL] [Abstract][Full Text] [Related]
10. Disease progression despite early loss of polyglutamine protein expression in SCA7 mouse model.
Helmlinger D; Abou-Sleymane G; Yvert G; Rousseau S; Weber C; Trottier Y; Mandel JL; Devys D
J Neurosci; 2004 Feb; 24(8):1881-7. PubMed ID: 14985428
[TBL] [Abstract][Full Text] [Related]
11. Interrogation of brain miRNA and mRNA expression profiles reveals a molecular regulatory network that is perturbed by mutant huntingtin.
Jin J; Cheng Y; Zhang Y; Wood W; Peng Q; Hutchison E; Mattson MP; Becker KG; Duan W
J Neurochem; 2012 Nov; 123(4):477-90. PubMed ID: 22906125
[TBL] [Abstract][Full Text] [Related]
12. SUMO-1 co-localized with mutant atrophin-1 with expanded polyglutamines accelerates intranuclear aggregation and cell death.
Terashima T; Kawai H; Fujitani M; Maeda K; Yasuda H
Neuroreport; 2002 Dec; 13(17):2359-64. PubMed ID: 12488827
[TBL] [Abstract][Full Text] [Related]
13. Comparative analyses of Purkinje cell gene expression profiles reveal shared molecular abnormalities in models of different polyglutamine diseases.
Friedrich B; Euler P; Ziegler R; Kuhn A; Landwehrmeyer BG; Luthi-Carter R; Weiller C; Hellwig S; Zucker B
Brain Res; 2012 Oct; 1481():37-48. PubMed ID: 22917585
[TBL] [Abstract][Full Text] [Related]
14. Neuroprotective effects of PPAR-γ agonist rosiglitazone in N171-82Q mouse model of Huntington's disease.
Jin J; Albertz J; Guo Z; Peng Q; Rudow G; Troncoso JC; Ross CA; Duan W
J Neurochem; 2013 May; 125(3):410-9. PubMed ID: 23373812
[TBL] [Abstract][Full Text] [Related]
15. Altered selenium status in Huntington's disease: neuroprotection by selenite in the N171-82Q mouse model.
Lu Z; Marks E; Chen J; Moline J; Barrows L; Raisbeck M; Volitakis I; Cherny RA; Chopra V; Bush AI; Hersch S; Fox JH
Neurobiol Dis; 2014 Nov; 71():34-42. PubMed ID: 25014023
[TBL] [Abstract][Full Text] [Related]
16. Pathological accumulation of atrophin-1 in dentatorubralpallidoluysian atrophy.
Suzuki Y; Yazawa I
Int J Clin Exp Pathol; 2011 Apr; 4(4):378-84. PubMed ID: 21577324
[TBL] [Abstract][Full Text] [Related]
17. Allele-selective inhibition of mutant atrophin-1 expression by duplex and single-stranded RNAs.
Hu J; Liu J; Narayanannair KJ; Lackey JG; Kuchimanchi S; Rajeev KG; Manoharan M; Swayze EE; Lima WF; Prakash TP; Xiang Q; Martinez C; Corey DR
Biochemistry; 2014 Jul; 53(28):4510-8. PubMed ID: 24981774
[TBL] [Abstract][Full Text] [Related]
18. Severe neurological phenotypes of Q129 DRPLA transgenic mice serendipitously created by en masse expansion of CAG repeats in Q76 DRPLA mice.
Sato T; Miura M; Yamada M; Yoshida T; Wood JD; Yazawa I; Masuda M; Suzuki T; Shin RM; Yau HJ; Liu FC; Shimohata T; Onodera O; Ross CA; Katsuki M; Takahashi H; Kano M; Aosaki T; Tsuji S
Hum Mol Genet; 2009 Feb; 18(4):723-36. PubMed ID: 19039037
[TBL] [Abstract][Full Text] [Related]
19. Polyglutamine disease: recent advances in the neuropathology of dentatorubral-pallidoluysian atrophy.
Yamada M; Shimohata M; Sato T; Tsuji S; Takahashi H
Neuropathology; 2006 Aug; 26(4):346-51. PubMed ID: 16961072
[TBL] [Abstract][Full Text] [Related]
20. Decreased expression of striatal signaling genes in a mouse model of Huntington's disease.
Luthi-Carter R; Strand A; Peters NL; Solano SM; Hollingsworth ZR; Menon AS; Frey AS; Spektor BS; Penney EB; Schilling G; Ross CA; Borchelt DR; Tapscott SJ; Young AB; Cha JH; Olson JM
Hum Mol Genet; 2000 May; 9(9):1259-71. PubMed ID: 10814708
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]