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3. New insight into the molecular basis of 3beta-hydroxysteroid dehydrogenase deficiency: identification of eight mutations in the HSD3B2 gene eleven patients from seven new families and comparison of the functional properties of twenty-five mutant enzymes. Moisan AM; Ricketts ML; Tardy V; Desrochers M; Mébarki F; Chaussain JL; Cabrol S; Raux-Demay MC; Forest MG; Sippell WG; Peter M; Morel Y; Simard J J Clin Endocrinol Metab; 1999 Dec; 84(12):4410-25. PubMed ID: 10599696 [TBL] [Abstract][Full Text] [Related]
4. A new insight into the molecular basis of 3beta-hydroxysteroid dehydrogenase deficiency. Simard J; Ricketts ML; Moisan AM; Tardy V; Peter M; Van Vliet G; Morel Y Endocr Res; 2000 Nov; 26(4):761-70. PubMed ID: 11196452 [TBL] [Abstract][Full Text] [Related]
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6. Congenital adrenal hyperplasia due to point mutations in the type II 3 beta-hydroxysteroid dehydrogenase gene. Rhéaume E; Simard J; Morel Y; Mebarki F; Zachmann M; Forest MG; New MI; Labrie F Nat Genet; 1992 Jul; 1(4):239-45. PubMed ID: 1363812 [TBL] [Abstract][Full Text] [Related]
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8. Newly proposed hormonal criteria via genotypic proof for type II 3beta-hydroxysteroid dehydrogenase deficiency. Lutfallah C; Wang W; Mason JI; Chang YT; Haider A; Rich B; Castro-Magana M; Copeland KC; David R; Pang S J Clin Endocrinol Metab; 2002 Jun; 87(6):2611-22. PubMed ID: 12050224 [TBL] [Abstract][Full Text] [Related]
9. A novel nonstop mutation in the stop codon and a novel missense mutation in the type II 3beta-hydroxysteroid dehydrogenase (3beta-HSD) gene causing, respectively, nonclassic and classic 3beta-HSD deficiency congenital adrenal hyperplasia. Pang S; Wang W; Rich B; David R; Chang YT; Carbunaru G; Myers SE; Howie AF; Smillie KJ; Mason JI J Clin Endocrinol Metab; 2002 Jun; 87(6):2556-63. PubMed ID: 12050213 [TBL] [Abstract][Full Text] [Related]
10. Carboxyl-terminal mutations in 3beta-hydroxysteroid dehydrogenase type II cause severe salt-wasting congenital adrenal hyperplasia. Welzel M; Wüstemann N; Simic-Schleicher G; Dörr HG; Schulze E; Shaikh G; Clayton P; Grötzinger J; Holterhus PM; Riepe FG J Clin Endocrinol Metab; 2008 Apr; 93(4):1418-25. PubMed ID: 18252794 [TBL] [Abstract][Full Text] [Related]
11. A novel homozygous nonsense mutations E135* in the type II 3beta-hydroxysteroid dehydrogenase gene in a girl with salt-losing congenital adrenal hyperplasia. Mutations in brief no. 168. Online. Marui S; Torrealba IM; Russell AJ; Latronico AC; Sutcliffe RG; Mendonca BB Hum Mutat; 1998; 12(2):139. PubMed ID: 10694926 [TBL] [Abstract][Full Text] [Related]
12. Refining hormonal diagnosis of type II 3beta-hydroxysteroid dehydrogenase deficiency in patients with premature pubarche and hirsutism based on HSD3B2 genotyping. Mermejo LM; Elias LL; Marui S; Moreira AC; Mendonca BB; de Castro M J Clin Endocrinol Metab; 2005 Mar; 90(3):1287-93. PubMed ID: 15585552 [TBL] [Abstract][Full Text] [Related]
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14. A case of 3beta-hydroxysteroid dehydrogenase type II (HSD3B2) deficiency picked up by neonatal screening for 21-hydroxylase deficiency: difficulties and delay in etiologic diagnosis. Nordenström A; Forest MG; Wedell A Horm Res; 2007; 68(4):204-8. PubMed ID: 17496421 [TBL] [Abstract][Full Text] [Related]
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16. Structure and expression of a new complementary DNA encoding the almost exclusive 3 beta-hydroxysteroid dehydrogenase/delta 5-delta 4-isomerase in human adrenals and gonads. Rhéaume E; Lachance Y; Zhao HF; Breton N; Dumont M; de Launoit Y; Trudel C; Luu-The V; Simard J; Labrie F Mol Endocrinol; 1991 Aug; 5(8):1147-57. PubMed ID: 1944309 [TBL] [Abstract][Full Text] [Related]
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18. Detection and functional characterization of the novel missense mutation Y254D in type II 3 beta-hydroxysteroid dehydrogenase (3 beta HSD) gene of a female patient with nonsalt-losing 3 beta HSD deficiency. Sanchez R; Rhéaume E; Laflamme N; Rosenfield RL; Labrie F; Simard J J Clin Endocrinol Metab; 1994 Mar; 78(3):561-7. PubMed ID: 8126127 [TBL] [Abstract][Full Text] [Related]
19. A new compound heterozygous frameshift mutation in the type II 3 beta-hydroxysteroid dehydrogenase (3 beta-HSD) gene causes salt-wasting 3 beta-HSD deficiency congenital adrenal hyperplasia. Zhang L; Sakkal-Alkaddour H; Chang YT; Yang X; Pang S J Clin Endocrinol Metab; 1996 Jan; 81(1):291-5. PubMed ID: 8550766 [TBL] [Abstract][Full Text] [Related]