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4. Lung disease associated with periventricular nodular heterotopia and an FLNA mutation. Masurel-Paulet A; Haan E; Thompson EM; Goizet C; Thauvin-Robinet C; Tai A; Kennedy D; Smith G; Khong TY; Solé G; Guerineau E; Coupry I; Huet F; Robertson S; Faivre L Eur J Med Genet; 2011; 54(1):25-8. PubMed ID: 20888935 [TBL] [Abstract][Full Text] [Related]
5. Skeletal dysplasias due to filamin A mutations result from a gain-of-function mechanism distinct from allelic neurological disorders. Clark AR; Sawyer GM; Robertson SP; Sutherland-Smith AJ Hum Mol Genet; 2009 Dec; 18(24):4791-800. PubMed ID: 19773341 [TBL] [Abstract][Full Text] [Related]
6. A novel filamin A D203Y mutation in a female patient with otopalatodigital type 1 syndrome and extremely skewed X chromosome inactivation. Hidalgo-Bravo A; Pompa-Mera EN; Kofman-Alfaro S; Gonzalez-Bonilla CR; Zenteno JC Am J Med Genet A; 2005 Jul; 136(2):190-3. PubMed ID: 15940695 [TBL] [Abstract][Full Text] [Related]
7. Mutational analysis of two boys with the severe perinatally lethal Melnick-Needles syndrome. Santos HH; Garcia PP; Pereira L; Leão LL; Aguiar RA; Lana AM; Carvalho MR; Aguiar MJ Am J Med Genet A; 2010 Mar; 152A(3):726-31. PubMed ID: 20186808 [TBL] [Abstract][Full Text] [Related]
8. Genotype-epigenotype-phenotype correlations in females with frontometaphyseal dysplasia. Zenker M; Nährlich L; Sticht H; Reis A; Horn D Am J Med Genet A; 2006 May; 140(10):1069-73. PubMed ID: 16596676 [TBL] [Abstract][Full Text] [Related]
9. A filamin A splice mutation resulting in a syndrome of facial dysmorphism, periventricular nodular heterotopia, and severe constipation reminiscent of cerebro-fronto-facial syndrome. Hehr U; Hehr A; Uyanik G; Phelan E; Winkler J; Reardon W J Med Genet; 2006 Jun; 43(6):541-4. PubMed ID: 16299064 [TBL] [Abstract][Full Text] [Related]
10. Mutations in the gene encoding filamin B disrupt vertebral segmentation, joint formation and skeletogenesis. Krakow D; Robertson SP; King LM; Morgan T; Sebald ET; Bertolotto C; Wachsmann-Hogiu S; Acuna D; Shapiro SS; Takafuta T; Aftimos S; Kim CA; Firth H; Steiner CE; Cormier-Daire V; Superti-Furga A; Bonafe L; Graham JM; Grix A; Bacino CA; Allanson J; Bialer MG; Lachman RS; Rimoin DL; Cohn DH Nat Genet; 2004 Apr; 36(4):405-10. PubMed ID: 14991055 [TBL] [Abstract][Full Text] [Related]
11. Otopalatodigital syndrome type 2 in two siblings with a novel filamin A 629G>T mutation: clinical, pathological, and molecular findings. Mariño-Enríquez A; Lapunzina P; Robertson SP; Rodríguez JI Am J Med Genet A; 2007 May; 143A(10):1120-5. PubMed ID: 17431908 [TBL] [Abstract][Full Text] [Related]
12. Structure of the human filamin A actin-binding domain. Ruskamo S; Ylänne J Acta Crystallogr D Biol Crystallogr; 2009 Nov; 65(Pt 11):1217-21. PubMed ID: 19923718 [TBL] [Abstract][Full Text] [Related]
14. Postzygotic mutation and germline mosaicism in the otopalatodigital syndrome spectrum disorders. Robertson SP; Thompson S; Morgan T; Holder-Espinasse M; Martinot-Duquenoy V; Wilkie AO; Manouvrier-Hanu S Eur J Hum Genet; 2006 May; 14(5):549-54. PubMed ID: 16538226 [TBL] [Abstract][Full Text] [Related]
15. Disease-associated substitutions in the filamin B actin binding domain confer enhanced actin binding affinity in the absence of major structural disturbance: Insights from the crystal structures of filamin B actin binding domains. Sawyer GM; Clark AR; Robertson SP; Sutherland-Smith AJ J Mol Biol; 2009 Jul; 390(5):1030-47. PubMed ID: 19505475 [TBL] [Abstract][Full Text] [Related]
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18. FLNA p.V528M substitution is neither associated with bilateral periventricular nodular heterotopia nor with macrothrombocytopenia. Kunishima S; Ito-Yamamura Y; Hayakawa A; Yamamoto T; Saito H J Hum Genet; 2010 Dec; 55(12):844-6. PubMed ID: 20844545 [TBL] [Abstract][Full Text] [Related]
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20. Filamin A mutations cause periventricular heterotopia with Ehlers-Danlos syndrome. Sheen VL; Jansen A; Chen MH; Parrini E; Morgan T; Ravenscroft R; Ganesh V; Underwood T; Wiley J; Leventer R; Vaid RR; Ruiz DE; Hutchins GM; Menasha J; Willner J; Geng Y; Gripp KW; Nicholson L; Berry-Kravis E; Bodell A; Apse K; Hill RS; Dubeau F; Andermann F; Barkovich J; Andermann E; Shugart YY; Thomas P; Viri M; Veggiotti P; Robertson S; Guerrini R; Walsh CA Neurology; 2005 Jan; 64(2):254-62. PubMed ID: 15668422 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]