These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
7. Mutant prion proteins in Gerstmann-Sträussler-Scheinker disease with neurofibrillary tangles. Hsiao K; Dlouhy SR; Farlow MR; Cass C; Da Costa M; Conneally PM; Hodes ME; Ghetti B; Prusiner SB Nat Genet; 1992 Apr; 1(1):68-71. PubMed ID: 1363810 [TBL] [Abstract][Full Text] [Related]
8. Dominantly inherited prion protein cerebral amyloidoses - a modern view of Gerstmann-Sträussler-Scheinker. Ghetti B; Piccardo P; Zanusso G Handb Clin Neurol; 2018; 153():243-269. PubMed ID: 29887140 [TBL] [Abstract][Full Text] [Related]
9. Prion proteins with different conformations accumulate in Gerstmann-Sträussler-Scheinker disease caused by A117V and F198S mutations. Piccardo P; Liepnieks JJ; William A; Dlouhy SR; Farlow MR; Young K; Nochlin D; Bird TD; Nixon RR; Ball MJ; DeCarli C; Bugiani O; Tagliavini F; Benson MD; Ghetti B Am J Pathol; 2001 Jun; 158(6):2201-7. PubMed ID: 11395398 [TBL] [Abstract][Full Text] [Related]
10. A 7-kDa prion protein (PrP) fragment, an integral component of the PrP region required for infectivity, is the major amyloid protein in Gerstmann-Sträussler-Scheinker disease A117V. Tagliavini F; Lievens PM; Tranchant C; Warter JM; Mohr M; Giaccone G; Perini F; Rossi G; Salmona M; Piccardo P; Ghetti B; Beavis RC; Bugiani O; Frangione B; Prelli F J Biol Chem; 2001 Feb; 276(8):6009-15. PubMed ID: 11087738 [TBL] [Abstract][Full Text] [Related]
11. Gerstmann-Sträussler-Scheinker Disease with F198S Mutation Induces Independent Tau and Prion Protein Pathologies in Bank Voles. Bruno R; Pirisinu L; Riccardi G; D'Agostino C; De Cecco E; Legname G; Cardone F; Gambetti P; Nonno R; Agrimi U; Di Bari MA Biomolecules; 2022 Oct; 12(10):. PubMed ID: 36291746 [TBL] [Abstract][Full Text] [Related]
12. Prion protein preamyloid and amyloid deposits in Gerstmann-Sträussler-Scheinker disease, Indiana kindred. Giaccone G; Verga L; Bugiani O; Frangione B; Serban D; Prusiner SB; Farlow MR; Ghetti B; Tagliavini F Proc Natl Acad Sci U S A; 1992 Oct; 89(19):9349-53. PubMed ID: 1357663 [TBL] [Abstract][Full Text] [Related]
18. Phenotypic variability of Gerstmann-Sträussler-Scheinker disease is associated with prion protein heterogeneity. Piccardo P; Dlouhy SR; Lievens PM; Young K; Bird TD; Nochlin D; Dickson DW; Vinters HV; Zimmerman TR; Mackenzie IR; Kish SJ; Ang LC; De Carli C; Pocchiari M; Brown P; Gibbs CJ; Gajdusek DC; Bugiani O; Ironside J; Tagliavini F; Ghetti B J Neuropathol Exp Neurol; 1998 Oct; 57(10):979-88. PubMed ID: 9786248 [TBL] [Abstract][Full Text] [Related]
19. A new point mutation of the PRNP gene in Gerstmann-Sträussler-Scheinker case in Poland. Bratosiewicz J; Barcikowska M; Cervenakowa L; Brown P; Gajdusek DC; Liberski PP Folia Neuropathol; 2000; 38(4):164-6. PubMed ID: 11693719 [TBL] [Abstract][Full Text] [Related]
20. A novel PRNP Y218N mutation in Gerstmann-Sträussler-Scheinker disease with neurofibrillary degeneration. Alzualde A; Indakoetxea B; Ferrer I; Moreno F; Barandiaran M; Gorostidi A; Estanga A; Ruiz I; Calero M; van Leeuwen FW; Atares B; Juste R; Rodriguez-Martínez AB; López de Munain A J Neuropathol Exp Neurol; 2010 Aug; 69(8):789-800. PubMed ID: 20613639 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]