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4. Targeted transgenic expression of the mutation causing Hutchinson-Gilford progeria syndrome leads to proliferative and degenerative epidermal disease. Sagelius H; Rosengardten Y; Hanif M; Erdos MR; Rozell B; Collins FS; Eriksson M J Cell Sci; 2008 Apr; 121(Pt 7):969-78. PubMed ID: 18334552 [TBL] [Abstract][Full Text] [Related]
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6. A homozygous ZMPSTE24 null mutation in combination with a heterozygous mutation in the LMNA gene causes Hutchinson-Gilford progeria syndrome (HGPS): insights into the pathophysiology of HGPS. Denecke J; Brune T; Feldhaus T; Robenek H; Kranz C; Auchus RJ; Agarwal AK; Marquardt T Hum Mutat; 2006 Jun; 27(6):524-31. PubMed ID: 16671095 [TBL] [Abstract][Full Text] [Related]
7. Aging of Hutchinson-Gilford progeria syndrome fibroblasts is characterised by hyperproliferation and increased apoptosis. Bridger JM; Kill IR Exp Gerontol; 2004 May; 39(5):717-24. PubMed ID: 15130666 [TBL] [Abstract][Full Text] [Related]
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9. Hutchinson-Gilford progeria syndrome: clinical findings in three patients carrying the G608G mutation in LMNA and review of the literature. Mazereeuw-Hautier J; Wilson LC; Mohammed S; Smallwood D; Shackleton S; Atherton DJ; Harper JI Br J Dermatol; 2007 Jun; 156(6):1308-14. PubMed ID: 17459035 [TBL] [Abstract][Full Text] [Related]
10. Incomplete processing of mutant lamin A in Hutchinson-Gilford progeria leads to nuclear abnormalities, which are reversed by farnesyltransferase inhibition. Glynn MW; Glover TW Hum Mol Genet; 2005 Oct; 14(20):2959-69. PubMed ID: 16126733 [TBL] [Abstract][Full Text] [Related]
11. Aging and nuclear organization: lamins and progeria. Mounkes LC; Stewart CL Curr Opin Cell Biol; 2004 Jun; 16(3):322-7. PubMed ID: 15145358 [TBL] [Abstract][Full Text] [Related]
12. HGPS and related premature aging disorders: from genomic identification to the first therapeutic approaches. Pereira S; Bourgeois P; Navarro C; Esteves-Vieira V; Cau P; De Sandre-Giovannoli A; Lévy N Mech Ageing Dev; 2008; 129(7-8):449-59. PubMed ID: 18513784 [TBL] [Abstract][Full Text] [Related]
13. The truncated prelamin A in Hutchinson-Gilford progeria syndrome alters segregation of A-type and B-type lamin homopolymers. Delbarre E; Tramier M; Coppey-Moisan M; Gaillard C; Courvalin JC; Buendia B Hum Mol Genet; 2006 Apr; 15(7):1113-22. PubMed ID: 16481358 [TBL] [Abstract][Full Text] [Related]
14. Mutations in the mouse Lmna gene causing progeria, muscular dystrophy and cardiomyopathy. Kozlov S; Mounkes L; Cutler D; Sullivan T; Hernandez L; Levy N; Rottman J; Stewart CL Novartis Found Symp; 2005; 264():246-58; discussion 258-63. PubMed ID: 15773758 [TBL] [Abstract][Full Text] [Related]
15. The neonatal progeroid syndrome (Wiedemann-Rautenstrauch): a model for the study of human aging? Arboleda G; Ramírez N; Arboleda H Exp Gerontol; 2007 Oct; 42(10):939-43. PubMed ID: 17728088 [TBL] [Abstract][Full Text] [Related]