147 related articles for article (PubMed ID: 127973)
1. Effect of 2-methylcitrate on citrate metabolism: implications for the management of patients with propionic acidemia and methylmalonic aciduria.
Cheema-Dhadli S; Leznoff CC; Halperin ML
Pediatr Res; 1975 Dec; 9(12):905-8. PubMed ID: 127973
[TBL] [Abstract][Full Text] [Related]
2. Inhibition by propionyl-coenzyme A of N-acetylglutamate synthetase in rat liver mitochondria. A possible explanation for hyperammonemia in propionic and methylmalonic acidemia.
Coude FX; Sweetman L; Nyhan WL
J Clin Invest; 1979 Dec; 64(6):1544-51. PubMed ID: 500823
[TBL] [Abstract][Full Text] [Related]
3. The inhibition by methylmalonic acid of malate transport by the dicarboxylate carrier in rat liver mitochondria. A possible explantation for hypoglycemia in methylmalonic aciduria.
Halperin ML; Schiller CM; Fritz IB
J Clin Invest; 1971 Nov; 50(11):2276-82. PubMed ID: 4398537
[TBL] [Abstract][Full Text] [Related]
4. Assessment of methylcitrate and methylcitrate to citrate ratio in dried blood spots as biomarkers for inborn errors of propionate metabolism.
Al-Dirbashi OY; Alfadhel M; Al-Thihli K; Al Dhahouri N; Langhans CD; Al Hammadi Z; Al-Shamsi A; Hertecant J; Okun JG; Hoffmann GF; Al-Jasmi F
Sci Rep; 2019 Aug; 9(1):12366. PubMed ID: 31451751
[TBL] [Abstract][Full Text] [Related]
5. Inhibition of enzymes which interact with citrate by (--)hydroxycitrate and 1,2,3,-tricarboxybenzene.
Cheema-Dhadli S; Halperin ML; Leznoff CC
Eur J Biochem; 1973 Sep; 38(1):98-102. PubMed ID: 4149431
[No Abstract] [Full Text] [Related]
6. [Citrate metabolism during the consolidation of experimental fractures].
Vlasov BIa; Khrustselevskaia AM
Vopr Med Khim; 1986; 32(5):44-7. PubMed ID: 3776117
[TBL] [Abstract][Full Text] [Related]
7. The identification of (E)-2-methylglutaconic acid, a new isoleucine metabolite, in the urine of patients with beta-ketothiolase deficiency, propionic acidaemia and methylmalonic acidaemia.
Duran M; Bruinvis L; Ketting D; Kamerling JP; Wadman SK; Schutgens RB
Biomed Mass Spectrom; 1982 Jan; 9(1):1-5. PubMed ID: 7059658
[TBL] [Abstract][Full Text] [Related]
8. Effect of (-)hydroxycitrate on the activities of ATP citrate lyase and the enzymes of acetyl-CoA metabolism in rat brain.
Szutowicz A; Stepień M; Lysiak W; Angielski S
Acta Biochim Pol; 1976; 23(2-3):227-34. PubMed ID: 970036
[TBL] [Abstract][Full Text] [Related]
9. [The neonatal form of propionic acidemia].
Figueras Aloy J; Ribes Rubio A; Vilaseca Busca MA; Lluch Mir M; Brines Godino P; Jiménez González R; Cruz Hernández M
An Esp Pediatr; 1988 Dec; 29(6):459-62. PubMed ID: 3245641
[TBL] [Abstract][Full Text] [Related]
10. 3-hydroxypropionate: significance of -oxidation of propionate in patients with propionic acidemia and methylmalonic acidemia.
Ando T; Rasmussen K; Nyhan WL; Hull D
Proc Natl Acad Sci U S A; 1972 Oct; 69(10):2807-11. PubMed ID: 4507604
[TBL] [Abstract][Full Text] [Related]
11. Blockage of methylcitrate cycle inhibits polyketide production in Aspergillus nidulans.
Zhang YQ; Keller NP
Mol Microbiol; 2004 Apr; 52(2):541-50. PubMed ID: 15066039
[TBL] [Abstract][Full Text] [Related]
12. Failure of the normal ureagenic response to amino acids in organic acid-loaded rats. Proposed mechanism for the hyperammonemia of propionic and methylmalonic acidemia.
Stewart PM; Walser M
J Clin Invest; 1980 Sep; 66(3):484-92. PubMed ID: 7400325
[TBL] [Abstract][Full Text] [Related]
13. Comparison of cytosolic and mitochondrial enzyme alterations in the livers of propionic or methylmalonic acidemia: a reduction of cytochrome oxidase activity.
Hayasaka K; Metoki K; Satoh T; Narisawa K; Tada K; Kawakami T; Matsuo N; Aoki T
Tohoku J Exp Med; 1982 Jul; 137(3):329-34. PubMed ID: 6287671
[TBL] [Abstract][Full Text] [Related]
14. Experience with prenatal diagnosis of propionic acidaemia and methylmalonic aciduria.
Fensom AH; Benson PF; Chalmers RA; Tracey BM; Watson D; King GS; Pettit BR; Rodeck CH
J Inherit Metab Dis; 1984; 7 Suppl 2():127-8. PubMed ID: 6434864
[No Abstract] [Full Text] [Related]
15. Dual role of isocitrate lyase 1 in the glyoxylate and methylcitrate cycles in Mycobacterium tuberculosis.
Gould TA; van de Langemheen H; Muñoz-Elías EJ; McKinney JD; Sacchettini JC
Mol Microbiol; 2006 Aug; 61(4):940-7. PubMed ID: 16879647
[TBL] [Abstract][Full Text] [Related]
16. Functional comparison of citrate synthase isoforms from S. cerevisiae.
Graybill ER; Rouhier MF; Kirby CE; Hawes JW
Arch Biochem Biophys; 2007 Sep; 465(1):26-37. PubMed ID: 17570335
[TBL] [Abstract][Full Text] [Related]
17. Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups.
Roe CR; Hoppel CL; Stacey TE; Chalmers RA; Tracey BM; Millington DS
Arch Dis Child; 1983 Nov; 58(11):916-20. PubMed ID: 6651329
[TBL] [Abstract][Full Text] [Related]
18. [Mechanisms regulating citric acid metabolism in the brain].
Eshchenko ND; Prokhorova MI
Vopr Biokhim Mozga; 1976; 11():78-88. PubMed ID: 23609
[TBL] [Abstract][Full Text] [Related]
19. [Enzymes of citrate and isocitrate conversion in the heart and skeletal muscle mitochondria of embryos and adult rabbits].
Sharkova EV
Vopr Med Khim; 1980; 26(5):694-8. PubMed ID: 7423888
[TBL] [Abstract][Full Text] [Related]
20. Identification of methyl-branched chain dicarboxylic acids in amniotic fluid and urine in propionic and methylmalonic acidemia.
Jakobs C; Dorland L; Sweetman L; Duran M; Nyhan WL; Wadman SK
Pediatr Res; 1984 Nov; 18(11):1185-91. PubMed ID: 6514446
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
