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3. A novel natural product compound enhances cAMP-regulated chloride conductance of cells expressing CFTR[delta]F508. deCarvalho AC; Ndi CP; Tsopmo A; Tane P; Ayafor J; Connolly JD; Teem JL Mol Med; 2002 Feb; 8(2):75-87. PubMed ID: 12080183 [TBL] [Abstract][Full Text] [Related]
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8. Altered chloride ion channel kinetics associated with the delta F508 cystic fibrosis mutation. Dalemans W; Barbry P; Champigny G; Jallat S; Dott K; Dreyer D; Crystal RG; Pavirani A; Lecocq JP; Lazdunski M Nature; 1991 Dec 19-26; 354(6354):526-8. PubMed ID: 1722027 [TBL] [Abstract][Full Text] [Related]
9. In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR. Rubenstein RC; Egan ME; Zeitlin PL J Clin Invest; 1997 Nov; 100(10):2457-65. PubMed ID: 9366560 [TBL] [Abstract][Full Text] [Related]
10. Genistein potentiates wild-type and delta F508-CFTR channel activity. Hwang TC; Wang F; Yang IC; Reenstra WW Am J Physiol; 1997 Sep; 273(3 Pt 1):C988-98. PubMed ID: 9316420 [TBL] [Abstract][Full Text] [Related]
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17. The cystic fibrosis mutation (delta F508) does not influence the chloride channel activity of CFTR. Li C; Ramjeesingh M; Reyes E; Jensen T; Chang X; Rommens JM; Bear CE Nat Genet; 1993 Apr; 3(4):311-6. PubMed ID: 7526932 [TBL] [Abstract][Full Text] [Related]
18. Antihypertensive 1,4-dihydropyridines as correctors of the cystic fibrosis transmembrane conductance regulator channel gating defect caused by cystic fibrosis mutations. Pedemonte N; Diena T; Caci E; Nieddu E; Mazzei M; Ravazzolo R; Zegarra-Moran O; Galietta LJ Mol Pharmacol; 2005 Dec; 68(6):1736-46. PubMed ID: 16150931 [TBL] [Abstract][Full Text] [Related]
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