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22. A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP. Yang W; Cook J; Rassbach B; Lemus A; DeArmond SJ; Mastrianni JA J Neurosci; 2009 Aug; 29(32):10072-80. PubMed ID: 19675240 [TBL] [Abstract][Full Text] [Related]
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27. The epsilon isoform of 14-3-3 protein is a component of the prion protein amyloid deposits of Gerstmann-Sträussler-Scheinker disease. Di Fede G; Giaccone G; Limido L; Mangieri M; Suardi S; Puoti G; Morbin M; Mazzoleni G; Ghetti B; Tagliavini F J Neuropathol Exp Neurol; 2007 Feb; 66(2):124-30. PubMed ID: 17278997 [TBL] [Abstract][Full Text] [Related]
28. Allelic origin of protease-sensitive and protease-resistant prion protein isoforms in Gerstmann-Sträussler-Scheinker disease with the P102L mutation. Monaco S; Fiorini M; Farinazzo A; Ferrari S; Gelati M; Piccardo P; Zanusso G; Ghetti B PLoS One; 2012; 7(2):e32382. PubMed ID: 22384235 [TBL] [Abstract][Full Text] [Related]
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36. A novel PRNP Y218N mutation in Gerstmann-Sträussler-Scheinker disease with neurofibrillary degeneration. Alzualde A; Indakoetxea B; Ferrer I; Moreno F; Barandiaran M; Gorostidi A; Estanga A; Ruiz I; Calero M; van Leeuwen FW; Atares B; Juste R; Rodriguez-Martínez AB; López de Munain A J Neuropathol Exp Neurol; 2010 Aug; 69(8):789-800. PubMed ID: 20613639 [TBL] [Abstract][Full Text] [Related]
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40. [A trend of molecular genetics on prion diseases and prion protein]. Muramatsu Y; Shinagawa M Nihon Rinsho; 1993 Sep; 51(9):2494-502. PubMed ID: 8411733 [TBL] [Abstract][Full Text] [Related] [Previous] [Next] [New Search]