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8. Leucine equivalency system in managing branched chain ketoaciduria. Smith BA; Waisman HA J Am Diet Assoc; 1971 Oct; 59(4):342-6. PubMed ID: 5095277 [No Abstract] [Full Text] [Related]
9. MAPLE SYRUP URINE DISEASE: A MANIFESTATION OF AN UNUSUAL METABOLIC ERROR. DANCIS J Clin Pediatr (Phila); 1964 Jun; 3():365-7. PubMed ID: 14154327 [No Abstract] [Full Text] [Related]
10. Semiquantitation of leucine, isoleucine, and valine by thin-layer chromatography in management of maple-syrup urine diseases. Allen RJ; Frey HJ; Fleming LM; Owings CL Clin Chem; 1972 May; 18(5):413-6. PubMed ID: 5019114 [No Abstract] [Full Text] [Related]
11. [Attempted diet therapy of a case of maple syrup disease]. Mainardi PC; Antener I Pediatria (Napoli); 1970 Jul; 78(3):540-60. PubMed ID: 5474982 [No Abstract] [Full Text] [Related]
12. [CLINICAL, BIOCHEMICAL, AND NEUROPATHOLOGIC ASPECTS OF MAPLE SYRUP URINE DISEASE. A KETOACIDURIA OF THE OPEN CHAIN AMINOACIDS LEUCINE, ISOLEUCINE AND VALINE]. SILBERMANSCHWARTZMAN J An Fac Med Lima; 1963 Sep; 46():339-65. PubMed ID: 14122039 [No Abstract] [Full Text] [Related]
14. The therapy of maple syrup urine disease. Snyderman SE Am J Dis Child; 1967 Jan; 113(1):68-73. PubMed ID: 6015908 [No Abstract] [Full Text] [Related]
15. Maple syrup urine disease. Four years' experience with dietary treatment of a case. Dickinson JP; Holton JB; Lewis GM; Littlewood JM; Steel AE Acta Paediatr Scand; 1969 Jul; 58(4):341-51. PubMed ID: 5824823 [No Abstract] [Full Text] [Related]
16. Maple syrup urine disease; an inborn error of the metabolism of valine, leucine, and isoleucine associated with gross mental deficiency. MACKENZIE DY; WOOLF LI Br Med J; 1959 Jan; 1(5114):90-1. PubMed ID: 13608087 [No Abstract] [Full Text] [Related]
17. A case of classical maple syrup urine disease "thiamine non-responsive". Wong PW; Justice P; Smith GF; Hsia DY Clin Genet; 1972; 3(1):27-33. PubMed ID: 5066975 [No Abstract] [Full Text] [Related]
18. [On the clinical picture and pathological anatomy of the maple syrup disease ("branded chain ketoaciduria"). Report on 2 cases in 1 family]. Sander C; Clotten R; Noetzel H; Wehinger H Dtsch Med Wochenschr; 1968 May; 93(18):895-903 passim. PubMed ID: 5650843 [No Abstract] [Full Text] [Related]
19. The need of essential amino acids in children. An evaluation based on the intake of phenylalanine, tyrosine, leucine, isoleucine, and valine in children with phenylketonuria, tyrosine amino transferase defect, and maple syrup urine disease. Kindt E; Halvorsen S Am J Clin Nutr; 1980 Feb; 33(2):279-86. PubMed ID: 6101930 [TBL] [Abstract][Full Text] [Related]
20. [Acrodermatitis enteropathica-like syndrome secondary to branched-chain amino acid deficiency during treatment of maple syrup urine disease]. Templier I; Reymond JL; Nguyen MA; Boujet C; Lantuejoul S; Beani JC; Leccia MT Ann Dermatol Venereol; 2006 Apr; 133(4):375-9. PubMed ID: 16733455 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]