232 related articles for article (PubMed ID: 15176725)
1. Functional studies of frataxin.
Isaya G; O'Neill HA; Gakh O; Park S; Mantcheva R; Mooney SM
Acta Paediatr Suppl; 2004 May; 93(445):68-71; discussion 72-3. PubMed ID: 15176725
[TBL] [Abstract][Full Text] [Related]
2. Yeast frataxin sequentially chaperones and stores iron by coupling protein assembly with iron oxidation.
Park S; Gakh O; O'Neill HA; Mangravita A; Nichol H; Ferreira GC; Isaya G
J Biol Chem; 2003 Aug; 278(33):31340-51. PubMed ID: 12732649
[TBL] [Abstract][Full Text] [Related]
3. Iron-dependent self-assembly of recombinant yeast frataxin: implications for Friedreich ataxia.
Adamec J; Rusnak F; Owen WG; Naylor S; Benson LM; Gacy AM; Isaya G
Am J Hum Genet; 2000 Sep; 67(3):549-62. PubMed ID: 10930361
[TBL] [Abstract][Full Text] [Related]
4. The ferroxidase activity of yeast frataxin.
Park S; Gakh O; Mooney SM; Isaya G
J Biol Chem; 2002 Oct; 277(41):38589-95. PubMed ID: 12149269
[TBL] [Abstract][Full Text] [Related]
5. Assembly and iron-binding properties of human frataxin, the protein deficient in Friedreich ataxia.
Cavadini P; O'Neill HA; Benada O; Isaya G
Hum Mol Genet; 2002 Feb; 11(3):217-27. PubMed ID: 11823441
[TBL] [Abstract][Full Text] [Related]
6. Changes in mitochondrial glutathione levels and protein thiol oxidation in ∆yfh1 yeast cells and the lymphoblasts of patients with Friedreich's ataxia.
Bulteau AL; Planamente S; Jornea L; Dur A; Lesuisse E; Camadro JM; Auchère F
Biochim Biophys Acta; 2012 Feb; 1822(2):212-25. PubMed ID: 22200491
[TBL] [Abstract][Full Text] [Related]
7. The yeast frataxin homolog Yfh1p plays a specific role in the maturation of cellular Fe/S proteins.
Mühlenhoff U; Richhardt N; Ristow M; Kispal G; Lill R
Hum Mol Genet; 2002 Aug; 11(17):2025-36. PubMed ID: 12165564
[TBL] [Abstract][Full Text] [Related]
8. The role of frataxin in fission yeast iron metabolism: implications for Friedreich's ataxia.
Wang Y; Wang Y; Marcus S; Busenlehner LS
Biochim Biophys Acta; 2014 Oct; 1840(10):3022-33. PubMed ID: 24997422
[TBL] [Abstract][Full Text] [Related]
9. Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia.
Rötig A; de Lonlay P; Chretien D; Foury F; Koenig M; Sidi D; Munnich A; Rustin P
Nat Genet; 1997 Oct; 17(2):215-7. PubMed ID: 9326946
[TBL] [Abstract][Full Text] [Related]
10. Hydrogen peroxide scavenging rescues frataxin deficiency in a Drosophila model of Friedreich's ataxia.
Anderson PR; Kirby K; Orr WC; Hilliker AJ; Phillips JP
Proc Natl Acad Sci U S A; 2008 Jan; 105(2):611-6. PubMed ID: 18184803
[TBL] [Abstract][Full Text] [Related]
11. Oxidative stress, mitochondrial dysfunction and cellular stress response in Friedreich's ataxia.
Calabrese V; Lodi R; Tonon C; D'Agata V; Sapienza M; Scapagnini G; Mangiameli A; Pennisi G; Stella AM; Butterfield DA
J Neurol Sci; 2005 Jun; 233(1-2):145-62. PubMed ID: 15896810
[TBL] [Abstract][Full Text] [Related]
12. No changes in heme synthesis in human Friedreich´s ataxia erythroid progenitor cells.
Steinkellner H; Singh HN; Muckenthaler MU; Goldenberg H; Moganty RR; Scheiber-Mojdehkar B; Sturm B
Gene; 2017 Jul; 621():5-11. PubMed ID: 28412459
[TBL] [Abstract][Full Text] [Related]
13. The Structure of the Complex between Yeast Frataxin and Ferrochelatase: CHARACTERIZATION AND PRE-STEADY STATE REACTION OF FERROUS IRON DELIVERY AND HEME SYNTHESIS.
Söderberg C; Gillam ME; Ahlgren EC; Hunter GA; Gakh O; Isaya G; Ferreira GC; Al-Karadaghi S
J Biol Chem; 2016 May; 291(22):11887-98. PubMed ID: 27026703
[TBL] [Abstract][Full Text] [Related]
14. 'Mitochondrial energy imbalance and lipid peroxidation cause cell death in Friedreich's ataxia'.
Abeti R; Parkinson MH; Hargreaves IP; Angelova PR; Sandi C; Pook MA; Giunti P; Abramov AY
Cell Death Dis; 2016 May; 7(5):e2237. PubMed ID: 27228352
[TBL] [Abstract][Full Text] [Related]
15. Iron metabolism and mitochondrial abnormalities in Friedreich ataxia.
Pandolfo M
Blood Cells Mol Dis; 2002; 29(3):536-47; discussion 548-52. PubMed ID: 12547248
[TBL] [Abstract][Full Text] [Related]
16. Overexpression of the yeast frataxin homolog (Yfh1): contrasting effects on iron-sulfur cluster assembly, heme synthesis and resistance to oxidative stress.
Seguin A; Bayot A; Dancis A; Rogowska-Wrzesinska A; Auchère F; Camadro JM; Bulteau AL; Lesuisse E
Mitochondrion; 2009 Apr; 9(2):130-8. PubMed ID: 19460301
[TBL] [Abstract][Full Text] [Related]
17. Friedreich's ataxia: past, present and future.
Marmolino D
Brain Res Rev; 2011 Jun; 67(1-2):311-30. PubMed ID: 21550666
[TBL] [Abstract][Full Text] [Related]
18. Lipophilic methylene blue analogues enhance mitochondrial function and increase frataxin levels in a cellular model of Friedreich's ataxia.
Khdour OM; Bandyopadhyay I; Chowdhury SR; Visavadiya NP; Hecht SM
Bioorg Med Chem; 2018 Jul; 26(12):3359-3369. PubMed ID: 29773347
[TBL] [Abstract][Full Text] [Related]
19. Friedreich ataxia: a paradigm for mitochondrial diseases.
Puccio H; Koenig M
Curr Opin Genet Dev; 2002 Jun; 12(3):272-7. PubMed ID: 12076669
[TBL] [Abstract][Full Text] [Related]
20. Iron Pathophysiology in Friedreich's Ataxia.
Li K
Adv Exp Med Biol; 2019; 1173():125-143. PubMed ID: 31456208
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
