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2. Characterization of the LARGE family of putative glycosyltransferases associated with dystroglycanopathies. Grewal PK; McLaughlan JM; Moore CJ; Browning CA; Hewitt JE Glycobiology; 2005 Oct; 15(10):912-23. PubMed ID: 15958417 [TBL] [Abstract][Full Text] [Related]
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5. Mutations in the human LARGE gene cause MDC1D, a novel form of congenital muscular dystrophy with severe mental retardation and abnormal glycosylation of alpha-dystroglycan. Longman C; Brockington M; Torelli S; Jimenez-Mallebrera C; Kennedy C; Khalil N; Feng L; Saran RK; Voit T; Merlini L; Sewry CA; Brown SC; Muntoni F Hum Mol Genet; 2003 Nov; 12(21):2853-61. PubMed ID: 12966029 [TBL] [Abstract][Full Text] [Related]
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9. Adeno-associated viral-mediated LARGE gene therapy rescues the muscular dystrophic phenotype in mouse models of dystroglycanopathy. Yu M; He Y; Wang K; Zhang P; Zhang S; Hu H Hum Gene Ther; 2013 Mar; 24(3):317-30. PubMed ID: 23379513 [TBL] [Abstract][Full Text] [Related]
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11. Protein glycosylation in disease: new insights into the congenital muscular dystrophies. Martin-Rendon E; Blake DJ Trends Pharmacol Sci; 2003 Apr; 24(4):178-83. PubMed ID: 12707004 [TBL] [Abstract][Full Text] [Related]
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13. Differential glycosylation of α-dystroglycan and proteins other than α-dystroglycan by like-glycosyltransferase. Zhang P; Hu H Glycobiology; 2012 Feb; 22(2):235-47. PubMed ID: 21930648 [TBL] [Abstract][Full Text] [Related]
14. Defective glycosylation in muscular dystrophy. Muntoni F; Brockington M; Blake DJ; Torelli S; Brown SC Lancet; 2002 Nov; 360(9343):1419-21. PubMed ID: 12424008 [TBL] [Abstract][Full Text] [Related]
15. The role of defective glycosylation in congenital muscular dystrophy. Schachter H; Vajsar J; Zhang W Glycoconj J; 2004; 20(5):291-300. PubMed ID: 15229394 [TBL] [Abstract][Full Text] [Related]
16. Localization and functional analysis of the LARGE family of glycosyltransferases: significance for muscular dystrophy. Brockington M; Torelli S; Prandini P; Boito C; Dolatshad NF; Longman C; Brown SC; Muntoni F Hum Mol Genet; 2005 Mar; 14(5):657-65. PubMed ID: 15661757 [TBL] [Abstract][Full Text] [Related]
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19. LARGE expression augments the glycosylation of glycoproteins in addition to α-dystroglycan conferring laminin binding. Zhang Z; Zhang P; Hu H PLoS One; 2011 Apr; 6(4):e19080. PubMed ID: 21533062 [TBL] [Abstract][Full Text] [Related]
20. Fukutin is prerequisite to ameliorate muscular dystrophic phenotype by myofiber-selective LARGE expression. Ohtsuka Y; Kanagawa M; Yu CC; Ito C; Chiyo T; Kobayashi K; Okada T; Takeda S; Toda T Sci Rep; 2015 Feb; 5():8316. PubMed ID: 25661440 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]