213 related articles for article (PubMed ID: 15187777)
1. Lack of effect of oral 4-phenylbutyrate on serum alpha-1-antitrypsin in patients with alpha-1-antitrypsin deficiency: a preliminary study.
Teckman JH
J Pediatr Gastroenterol Nutr; 2004 Jul; 39(1):34-7. PubMed ID: 15187777
[TBL] [Abstract][Full Text] [Related]
2. [Alpha-1-antitrypsin deficiency].
Bouchecareilh M
Med Sci (Paris); 2014 Oct; 30(10):889-95. PubMed ID: 25311024
[TBL] [Abstract][Full Text] [Related]
3. Accumulation of mutant alpha1-antitrypsin Z in the endoplasmic reticulum activates caspases-4 and -12, NFkappaB, and BAP31 but not the unfolded protein response.
Hidvegi T; Schmidt BZ; Hale P; Perlmutter DH
J Biol Chem; 2005 Nov; 280(47):39002-15. PubMed ID: 16183649
[TBL] [Abstract][Full Text] [Related]
4. NorUDCA promotes degradation of α1-antitrypsin mutant Z protein by inducing autophagy through AMPK/ULK1 pathway.
Tang Y; Blomenkamp KS; Fickert P; Trauner M; Teckman JH
PLoS One; 2018; 13(8):e0200897. PubMed ID: 30067827
[TBL] [Abstract][Full Text] [Related]
5. Alpha1-antitrypsin deficiency: biological answers to clinical questions.
Coakley RJ; Taggart C; O'Neill S; McElvaney NG
Am J Med Sci; 2001 Jan; 321(1):33-41. PubMed ID: 11202478
[TBL] [Abstract][Full Text] [Related]
6. Intrapleural administration of an AAVrh.10 vector coding for human α1-antitrypsin for the treatment of α1-antitrypsin deficiency.
Chiuchiolo MJ; Kaminsky SM; Sondhi D; Hackett NR; Rosenberg JB; Frenk EZ; Hwang Y; Van de Graaf BG; Hutt JA; Wang G; Benson J; Crystal RG
Hum Gene Ther Clin Dev; 2013 Dec; 24(4):161-73. PubMed ID: 24191907
[TBL] [Abstract][Full Text] [Related]
7. alpha1-Antitrypsin deficiency is not an important cause of childhood liver diseases in a multi-ethnic Southeast Asian population.
Lee WS; Yap SF; Looi LM
J Paediatr Child Health; 2007 Sep; 43(9):636-9. PubMed ID: 17688648
[TBL] [Abstract][Full Text] [Related]
8. Chemical chaperones mediate increased secretion of mutant alpha 1-antitrypsin (alpha 1-AT) Z: A potential pharmacological strategy for prevention of liver injury and emphysema in alpha 1-AT deficiency.
Burrows JA; Willis LK; Perlmutter DH
Proc Natl Acad Sci U S A; 2000 Feb; 97(4):1796-801. PubMed ID: 10677536
[TBL] [Abstract][Full Text] [Related]
9. Alpha-1 antitrypsin and liver disease: mechanisms of injury and novel interventions.
Teckman JH; Mangalat N
Expert Rev Gastroenterol Hepatol; 2015 Feb; 9(2):261-8. PubMed ID: 25066184
[TBL] [Abstract][Full Text] [Related]
10. Histone deacetylase inhibitor (HDACi) suberoylanilide hydroxamic acid (SAHA)-mediated correction of α1-antitrypsin deficiency.
Bouchecareilh M; Hutt DM; Szajner P; Flotte TR; Balch WE
J Biol Chem; 2012 Nov; 287(45):38265-78. PubMed ID: 22995909
[TBL] [Abstract][Full Text] [Related]
11. Liver disease in alpha-1 antitrypsin deficiency: current understanding and future therapy.
Teckman JH
COPD; 2013 Mar; 10 Suppl 1():35-43. PubMed ID: 23527737
[TBL] [Abstract][Full Text] [Related]
12. Intrapleural administration of a serotype 5 adeno-associated virus coding for alpha1-antitrypsin mediates persistent, high lung and serum levels of alpha1-antitrypsin.
De B; Heguy A; Leopold PL; Wasif N; Korst RJ; Hackett NR; Crystal RG
Mol Ther; 2004 Dec; 10(6):1003-10. PubMed ID: 15564132
[TBL] [Abstract][Full Text] [Related]
13. Indomethacin increases liver damage in a murine model of liver injury from alpha-1-antitrypsin deficiency.
Rudnick DA; Shikapwashya O; Blomenkamp K; Teckman JH
Hepatology; 2006 Oct; 44(4):976-82. PubMed ID: 17006946
[TBL] [Abstract][Full Text] [Related]
14. Quantitative isolation of alphalAT mutant Z protein polymers from human and mouse livers and the effect of heat.
An JK; Blomenkamp K; Lindblad D; Teckman JH
Hepatology; 2005 Jan; 41(1):160-7. PubMed ID: 15619240
[TBL] [Abstract][Full Text] [Related]
15. ANCA-associated vasculitis is linked to carriage of the Z allele of α₁ antitrypsin and its polymers.
Morris H; Morgan MD; Wood AM; Smith SW; Ekeowa UI; Herrmann K; Holle JU; Guillevin L; Lomas DA; Perez J; Pusey CD; Salama AD; Stockley R; Wieczorek S; McKnight AJ; Maxwell AP; Miranda E; Williams J; Savage CO; Harper L
Ann Rheum Dis; 2011 Oct; 70(10):1851-6. PubMed ID: 21821620
[TBL] [Abstract][Full Text] [Related]
16. [From gene disease; alpha1-antitrypsine deficiency].
Hiemstra PS; Stolk J
Ned Tijdschr Geneeskd; 2003 Apr; 147(16):758-60. PubMed ID: 12731467
[TBL] [Abstract][Full Text] [Related]
17. Z-type alpha 1-antitrypsin is less competent than M1-type alpha 1-antitrypsin as an inhibitor of neutrophil elastase.
Ogushi F; Fells GA; Hubbard RC; Straus SD; Crystal RG
J Clin Invest; 1987 Nov; 80(5):1366-74. PubMed ID: 3500183
[TBL] [Abstract][Full Text] [Related]
18. Alpha-1-antitrypsin deficiency.
Bals R
Best Pract Res Clin Gastroenterol; 2010 Oct; 24(5):629-33. PubMed ID: 20955965
[TBL] [Abstract][Full Text] [Related]
19. Endoplasmic reticulum polymers impair luminal protein mobility and sensitize to cellular stress in alpha1-antitrypsin deficiency.
Ordóñez A; Snapp EL; Tan L; Miranda E; Marciniak SJ; Lomas DA
Hepatology; 2013 May; 57(5):2049-60. PubMed ID: 23197448
[TBL] [Abstract][Full Text] [Related]
20. Airways inflammation in chronic bronchitis: the effects of smoking and alpha1-antitrypsin deficiency.
Hill AT; Bayley DL; Campbell EJ; Hill SL; Stockley RA
Eur Respir J; 2000 May; 15(5):886-90. PubMed ID: 10853853
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
