165 related articles for article (PubMed ID: 15355973)
1. Crystal structure of T-protein of the glycine cleavage system. Cofactor binding, insights into H-protein recognition, and molecular basis for understanding nonketotic hyperglycinemia.
Lee HH; Kim DJ; Ahn HJ; Ha JY; Suh SW
J Biol Chem; 2004 Nov; 279(48):50514-23. PubMed ID: 15355973
[TBL] [Abstract][Full Text] [Related]
2. Crystal structure of human T-protein of glycine cleavage system at 2.0 A resolution and its implication for understanding non-ketotic hyperglycinemia.
Okamura-Ikeda K; Hosaka H; Yoshimura M; Yamashita E; Toma S; Nakagawa A; Fujiwara K; Motokawa Y; Taniguchi H
J Mol Biol; 2005 Sep; 351(5):1146-59. PubMed ID: 16051266
[TBL] [Abstract][Full Text] [Related]
3. Defective glycine cleavage system in nonketotic hyperglycinemia. Occurrence of a less active glycine decarboxylase and an abnormal aminomethyl carrier protein.
Hiraga K; Kochi H; Hayasaka K; Kikuchi G; Nyhan WL
J Clin Invest; 1981 Aug; 68(2):525-34. PubMed ID: 6790577
[TBL] [Abstract][Full Text] [Related]
4. Structure of P-protein of the glycine cleavage system: implications for nonketotic hyperglycinemia.
Nakai T; Nakagawa N; Maoka N; Masui R; Kuramitsu S; Kamiya N
EMBO J; 2005 Apr; 24(8):1523-36. PubMed ID: 15791207
[TBL] [Abstract][Full Text] [Related]
5. Nonketotic hyperglycinemia: two patients with primary defects of P-protein and T-protein, respectively, in the glycine cleavage system.
Hayasaka K; Tada K; Kikuchi G; Winter S; Nyhan WL
Pediatr Res; 1983 Dec; 17(12):967-70. PubMed ID: 6336599
[TBL] [Abstract][Full Text] [Related]
6. Recurrent mutations in P- and T-proteins of the glycine cleavage complex and a novel T-protein mutation (N145I): a strategy for the molecular investigation of patients with nonketotic hyperglycinemia (NKH).
Toone JR; Applegarth DA; Coulter-Mackie MB; James ER
Mol Genet Metab; 2001 Apr; 72(4):322-5. PubMed ID: 11286506
[TBL] [Abstract][Full Text] [Related]
7. The amino-terminal region of the Escherichia coli T-protein of the glycine cleavage system is essential for proper association with H-protein.
Okamura-Ikeda K; Fujiwara K; Motokawa Y
Eur J Biochem; 1999 Sep; 264(2):446-53. PubMed ID: 10491090
[TBL] [Abstract][Full Text] [Related]
8. Interaction between the lipoamide-containing H-protein and the lipoamide dehydrogenase (L-protein) of the glycine decarboxylase multienzyme system 2. Crystal structures of H- and L-proteins.
Faure M; Bourguignon J; Neuburger M; MacHerel D; Sieker L; Ober R; Kahn R; Cohen-Addad C; Douce R
Eur J Biochem; 2000 May; 267(10):2890-8. PubMed ID: 10806386
[TBL] [Abstract][Full Text] [Related]
9. Mechanism of the glycine cleavage reaction. Further characterization of the intermediate attached to H-protein and of the reaction catalyzed by T-protein.
Fujiwara K; Okamura-Ikeda K; Motokawa Y
J Biol Chem; 1984 Sep; 259(17):10664-8. PubMed ID: 6469978
[TBL] [Abstract][Full Text] [Related]
10. Probing the H-protein-induced conformational change and the function of the N-terminal region of Escherichia coli T-protein of the glycine cleavage system by limited proteolysis.
Okamura-Ikeda K; Kameoka N; Fujiwara K; Motokawa Y
J Biol Chem; 2003 Mar; 278(12):10067-72. PubMed ID: 12531904
[TBL] [Abstract][Full Text] [Related]
11. Identification of the first reported splice site mutation (IVS7-1G-->A) in the aminomethyltransferase (T-protein) gene (AMT) of the glycine cleavage complex in 3 unrelated families with nonketotic hyperglycinemia.
Toone JR; Applegarth DA; Coulter-Mackie MB; James ER
Hum Mutat; 2001; 17(1):76. PubMed ID: 11139253
[TBL] [Abstract][Full Text] [Related]
12. Mechanism of the glycine cleavage reaction. Properties of the reverse reaction catalyzed by T-protein.
Okamura-Ikeda K; Fujiwara K; Motokawa Y
J Biol Chem; 1987 May; 262(14):6746-9. PubMed ID: 3571285
[TBL] [Abstract][Full Text] [Related]
13. Glycine decarboxylase multienzyme complex. Purification and partial characterization from pea leaf mitochondria.
Walker JL; Oliver DJ
J Biol Chem; 1986 Feb; 261(5):2214-21. PubMed ID: 3080433
[TBL] [Abstract][Full Text] [Related]
14. Structure and expression of the glycine cleavage system in rat central nervous system.
Sakata Y; Owada Y; Sato K; Kojima K; Hisanaga K; Shinka T; Suzuki Y; Aoki Y; Satoh J; Kondo H; Matsubara Y; Kure S
Brain Res Mol Brain Res; 2001 Oct; 94(1-2):119-30. PubMed ID: 11597772
[TBL] [Abstract][Full Text] [Related]
15. Two novel missense mutations in nonketotic hyperglycinemia.
Yilmaz BS; Kor D; Ceylaner S; Mert GG; Incecik F; Kartal E; Mungan NO
J Child Neurol; 2015 May; 30(6):789-92. PubMed ID: 24838951
[TBL] [Abstract][Full Text] [Related]
16. Resolution and characterization of the glycine-cleavage reaction in pea leaf mitochondria. Properties of the forward reaction catalysed by glycine decarboxylase and serine hydroxymethyltransferase.
Bourguignon J; Neuburger M; Douce R
Biochem J; 1988 Oct; 255(1):169-78. PubMed ID: 3143355
[TBL] [Abstract][Full Text] [Related]
17. Crystal structure of aminomethyltransferase in complex with dihydrolipoyl-H-protein of the glycine cleavage system: implications for recognition of lipoyl protein substrate, disease-related mutations, and reaction mechanism.
Okamura-Ikeda K; Hosaka H; Maita N; Fujiwara K; Yoshizawa AC; Nakagawa A; Taniguchi H
J Biol Chem; 2010 Jun; 285(24):18684-92. PubMed ID: 20375021
[TBL] [Abstract][Full Text] [Related]
18. Nonketotic hyperglycinemia: analyses of glycine cleavage system in typical and atypical cases.
Hayasaka K; Tada K; Fueki N; Nakamura Y; Nyhan WL; Schmidt K; Packman S; Seashore MR; Haan E; Danks DM
J Pediatr; 1987 Jun; 110(6):873-7. PubMed ID: 3585602
[TBL] [Abstract][Full Text] [Related]
19. Structural studies of the glycine decarboxylase complex from pea leaf mitochondria.
Cohen-Addad C; Faure M; Neuburger M; Ober R; Sieker L; Bourguignon J; Macherel D; Douce R
Biochimie; 1997 Nov; 79(11):637-43. PubMed ID: 9479445
[TBL] [Abstract][Full Text] [Related]
20. Mechanism of the glycine cleavage reaction: retention of C-2 hydrogens of glycine on the intermediate attached to H-protein and evidence for the inability of serine hydroxymethyltransferase to catalyze the glycine decarboxylation.
Fujiwara K; Okamura-Ikeda K; Ohmura Y; Motokawa Y
Arch Biochem Biophys; 1986 Nov; 251(1):121-7. PubMed ID: 3098173
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
