284 related articles for article (PubMed ID: 15748170)
1. Impaired proteasome activity and accumulation of ubiquitinated substrates in a hereditary neuropathy model.
Fortun J; Li J; Go J; Fenstermaker A; Fletcher BS; Notterpek L
J Neurochem; 2005 Mar; 92(6):1531-41. PubMed ID: 15748170
[TBL] [Abstract][Full Text] [Related]
2. Alterations in degradative pathways and protein aggregation in a neuropathy model based on PMP22 overexpression.
Fortun J; Go JC; Li J; Amici SA; Dunn WA; Notterpek L
Neurobiol Dis; 2006 Apr; 22(1):153-64. PubMed ID: 16326107
[TBL] [Abstract][Full Text] [Related]
3. PMP22 carrying the trembler or trembler-J mutation is intracellularly retained in myelinating Schwann cells.
Colby J; Nicholson R; Dickson KM; Orfali W; Naef R; Suter U; Snipes GJ
Neurobiol Dis; 2000 Dec; 7(6 Pt B):561-73. PubMed ID: 11114256
[TBL] [Abstract][Full Text] [Related]
4. The alpha-chemokine CXCL14 is up-regulated in the sciatic nerve of a mouse model of Charcot-Marie-Tooth disease type 1A and alters myelin gene expression in cultured Schwann cells.
Barbaria EM; Kohl B; Buhren BA; Hasenpusch-Theil K; Kruse F; Küry P; Martini R; Müller HW
Neurobiol Dis; 2009 Mar; 33(3):448-58. PubMed ID: 19111616
[TBL] [Abstract][Full Text] [Related]
5. Myelinating and demyelinating phenotype of Trembler-J mouse (a model of Charcot-Marie-Tooth human disease) analyzed by atomic force microscopy and confocal microscopy.
Rosso G; Negreira C; Sotelo JR; Kun A
J Mol Recognit; 2012 May; 25(5):247-55. PubMed ID: 22528185
[TBL] [Abstract][Full Text] [Related]
6. Molecular alterations resulting from frameshift mutations in peripheral myelin protein 22: implications for neuropathy severity.
Johnson JS; Roux KJ; Fletcher BS; Fortun J; Notterpek L
J Neurosci Res; 2005 Dec; 82(6):743-52. PubMed ID: 16273544
[TBL] [Abstract][Full Text] [Related]
7. Aggresome formation in neuropathy models based on peripheral myelin protein 22 mutations.
Ryan MC; Shooter EM; Notterpek L
Neurobiol Dis; 2002 Jul; 10(2):109-18. PubMed ID: 12127149
[TBL] [Abstract][Full Text] [Related]
8. Identification of the regulatory region of the peripheral myelin protein 22 (PMP22) gene that directs temporal and spatial expression in development and regeneration of peripheral nerves.
Maier M; Berger P; Nave KA; Suter U
Mol Cell Neurosci; 2002 May; 20(1):93-109. PubMed ID: 12056842
[TBL] [Abstract][Full Text] [Related]
9. Enhancement of Schwann cell myelin formation by K252a in the Trembler-J mouse dorsal root ganglion explant culture.
Liu N; Varma S; Shooter EM; Tolwani RJ
J Neurosci Res; 2005 Feb; 79(3):310-7. PubMed ID: 15605381
[TBL] [Abstract][Full Text] [Related]
10. Trembler as a mouse model of CMT1A?
Garbay B; Salles J; Knoll A; Boiron-Sargueil F; Heape AM; Bonnet J; Cassagne C
Ann N Y Acad Sci; 1999 Sep; 883():262-72. PubMed ID: 10586251
[TBL] [Abstract][Full Text] [Related]
11. Many facets of the peripheral myelin protein PMP22 in myelination and disease.
Naef R; Suter U
Microsc Res Tech; 1998 Jun; 41(5):359-71. PubMed ID: 9672419
[TBL] [Abstract][Full Text] [Related]
12. The formation of peripheral myelin protein 22 aggregates is hindered by the enhancement of autophagy and expression of cytoplasmic chaperones.
Fortun J; Verrier JD; Go JC; Madorsky I; Dunn WA; Notterpek L
Neurobiol Dis; 2007 Feb; 25(2):252-65. PubMed ID: 17174099
[TBL] [Abstract][Full Text] [Related]
13. Impairment of PMP22 transgenic Schwann cells differentiation in culture: implications for Charcot-Marie-Tooth type 1A disease.
Nobbio L; Vigo T; Abbruzzese M; Levi G; Brancolini C; Mantero S; Grandis M; Benedetti L; Mancardi G; Schenone A
Neurobiol Dis; 2004 Jun; 16(1):263-73. PubMed ID: 15207283
[TBL] [Abstract][Full Text] [Related]
14. Emerging role for autophagy in the removal of aggresomes in Schwann cells.
Fortun J; Dunn WA; Joy S; Li J; Notterpek L
J Neurosci; 2003 Nov; 23(33):10672-80. PubMed ID: 14627652
[TBL] [Abstract][Full Text] [Related]
15. Inducible HSP70 is critical in preventing the aggregation and enhancing the processing of PMP22.
Chittoor-Vinod VG; Lee S; Judge SM; Notterpek L
ASN Neuro; 2015; 7(1):. PubMed ID: 25694550
[TBL] [Abstract][Full Text] [Related]
16. Nerve conduction abnormalities and neuromyotonia in genetically engineered mouse models of human hereditary neuropathies.
Zielasek J; Toyka KV
Ann N Y Acad Sci; 1999 Sep; 883():310-20. PubMed ID: 10586256
[TBL] [Abstract][Full Text] [Related]
17. Major myelin protein gene (P0) mutation causes a novel form of axonal degeneration.
Li J; Bai Y; Ianakova E; Grandis M; Uchwat F; Trostinskaia A; Krajewski KM; Garbern J; Kupsky WJ; Shy ME
J Comp Neurol; 2006 Sep; 498(2):252-65. PubMed ID: 16856127
[TBL] [Abstract][Full Text] [Related]
18. Expression pattern of the peripheral myelin protein 22kDa (PMP22) in neural and non-neural tissue types of adult wildtype and Trembler mice--a comparative study.
Rautenstrauss B; Zechner U; Hameister H; Grehl H; Liehr T
J Peripher Nerv Syst; 1998; 3(2):117-24. PubMed ID: 10959245
[TBL] [Abstract][Full Text] [Related]
19. Hypermyelination and demyelinating peripheral neuropathy in Pmp22-deficient mice.
Adlkofer K; Martini R; Aguzzi A; Zielasek J; Toyka KV; Suter U
Nat Genet; 1995 Nov; 11(3):274-80. PubMed ID: 7581450
[TBL] [Abstract][Full Text] [Related]
20. Inflammatory demyelination in a patient with CMT1A.
Vital A; Vital C; Lagueny A; Ferrer X; Ribière-Bachelier C; Latour P; Petry KG
Muscle Nerve; 2003 Sep; 28(3):373-6. PubMed ID: 12929199
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]