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4. Molecular screening of 980 cases of suspected hereditary optic neuropathy with a report on 77 novel OPA1 mutations. Ferré M; Bonneau D; Milea D; Chevrollier A; Verny C; Dollfus H; Ayuso C; Defoort S; Vignal C; Zanlonghi X; Charlin JF; Kaplan J; Odent S; Hamel CP; Procaccio V; Reynier P; Amati-Bonneau P Hum Mutat; 2009 Jul; 30(7):E692-705. PubMed ID: 19319978 [TBL] [Abstract][Full Text] [Related]
5. The natural history of OPA1-related autosomal dominant optic atrophy. Cohn AC; Toomes C; Hewitt AW; Kearns LS; Inglehearn CF; Craig JE; Mackey DA Br J Ophthalmol; 2008 Oct; 92(10):1333-6. PubMed ID: 18653586 [TBL] [Abstract][Full Text] [Related]
6. Fourteen novel OPA1 mutations in autosomal dominant optic atrophy including two de novo mutations in sporadic optic atrophy. Baris O; Delettre C; Amati-Bonneau P; Surget MO; Charlin JF; Catier A; Derieux L; Guyomard JL; Dollfus H; Jonveaux P; Ayuso C; Maumenee I; Lorenz B; Mohammed S; Tourmen Y; Bonneau D; Malthièry Y; Hamel C; Reynier P Hum Mutat; 2003 Jun; 21(6):656. PubMed ID: 14961560 [TBL] [Abstract][Full Text] [Related]
7. Autosomal dominant optic atrophy: penetrance and expressivity in patients with OPA1 mutations. Cohn AC; Toomes C; Potter C; Towns KV; Hewitt AW; Inglehearn CF; Craig JE; Mackey DA Am J Ophthalmol; 2007 Apr; 143(4):656-62. PubMed ID: 17306754 [TBL] [Abstract][Full Text] [Related]
8. Structural model of the OPA1 GTPase domain may explain the molecular consequences of a novel mutation in a family with autosomal dominant optic atrophy. Dadgar S; Hagens O; Dadgar SR; Haghighi EN; Schimpf S; Wissinger B; Garshasbi M Exp Eye Res; 2006 Sep; 83(3):702-6. PubMed ID: 16698014 [TBL] [Abstract][Full Text] [Related]
9. Comprehensive cDNA study and quantitative transcript analysis of mutant OPA1 transcripts containing premature termination codons. Schimpf S; Fuhrmann N; Schaich S; Wissinger B Hum Mutat; 2008 Jan; 29(1):106-12. PubMed ID: 17722006 [TBL] [Abstract][Full Text] [Related]
10. Reduction of inner retinal thickness in patients with autosomal dominant optic atrophy associated with OPA1 mutations. Ito Y; Nakamura M; Yamakoshi T; Lin J; Yatsuya H; Terasaki H Invest Ophthalmol Vis Sci; 2007 Sep; 48(9):4079-86. PubMed ID: 17724190 [TBL] [Abstract][Full Text] [Related]
11. OPA1-associated disorders: phenotypes and pathophysiology. Amati-Bonneau P; Milea D; Bonneau D; Chevrollier A; Ferré M; Guillet V; Gueguen N; Loiseau D; de Crescenzo MA; Verny C; Procaccio V; Lenaers G; Reynier P Int J Biochem Cell Biol; 2009 Oct; 41(10):1855-65. PubMed ID: 19389487 [TBL] [Abstract][Full Text] [Related]
12. OPA1, encoding a dynamin-related GTPase, is mutated in autosomal dominant optic atrophy linked to chromosome 3q28. Alexander C; Votruba M; Pesch UE; Thiselton DL; Mayer S; Moore A; Rodriguez M; Kellner U; Leo-Kottler B; Auburger G; Bhattacharya SS; Wissinger B Nat Genet; 2000 Oct; 26(2):211-5. PubMed ID: 11017080 [TBL] [Abstract][Full Text] [Related]
14. Mitochondrial DNA content is decreased in autosomal dominant optic atrophy. Kim JY; Hwang JM; Ko HS; Seong MW; Park BJ; Park SS Neurology; 2005 Mar; 64(6):966-72. PubMed ID: 15781809 [TBL] [Abstract][Full Text] [Related]
16. The G401D mutation of OPA1 causes autosomal dominant optic atrophy and hearing loss in a Chinese family. Ke T; Nie SW; Yang QB; Liu JP; Zhou LN; Ren X; Liu JY; Wang Q; Liu MG Zhonghua Yi Xue Yi Chuan Xue Za Zhi; 2006 Oct; 23(5):481-5. PubMed ID: 17029191 [TBL] [Abstract][Full Text] [Related]
17. Dominant optic atrophy, sensorineural hearing loss, ptosis, and ophthalmoplegia: a syndrome caused by a missense mutation in OPA1. Payne M; Yang Z; Katz BJ; Warner JE; Weight CJ; Zhao Y; Pearson ED; Treft RL; Hillman T; Kennedy RJ; Meire FM; Zhang K Am J Ophthalmol; 2004 Nov; 138(5):749-55. PubMed ID: 15531309 [TBL] [Abstract][Full Text] [Related]
18. Reduction of oscillatory potentials and photopic negative response in patients with autosomal dominant optic atrophy with OPA1 mutations. Miyata K; Nakamura M; Kondo M; Lin J; Ueno S; Miyake Y; Terasaki H Invest Ophthalmol Vis Sci; 2007 Feb; 48(2):820-4. PubMed ID: 17251483 [TBL] [Abstract][Full Text] [Related]
19. A frameshift mutation in exon 28 of the OPA1 gene explains the high prevalence of dominant optic atrophy in the Danish population: evidence for a founder effect. Thiselton DL; Alexander C; Morris A; Brooks S; Rosenberg T; Eiberg H; Kjer B; Kjer P; Bhattacharya SS; Votruba M Hum Genet; 2001 Nov; 109(5):498-502. PubMed ID: 11735024 [TBL] [Abstract][Full Text] [Related]