These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
2. Human mitochondrial diseases associated with tRNA wobble modification deficiency. Kirino Y; Suzuki T RNA Biol; 2005 Apr; 2(2):41-4. PubMed ID: 17132941 [TBL] [Abstract][Full Text] [Related]
3. Acquisition of the wobble modification in mitochondrial tRNALeu(CUN) bearing the G12300A mutation suppresses the MELAS molecular defect. Kirino Y; Yasukawa T; Marjavaara SK; Jacobs HT; Holt IJ; Watanabe K; Suzuki T Hum Mol Genet; 2006 Mar; 15(6):897-904. PubMed ID: 16446307 [TBL] [Abstract][Full Text] [Related]
4. Human mitochondrial diseases caused by lack of taurine modification in mitochondrial tRNAs. Suzuki T; Nagao A; Suzuki T Wiley Interdiscip Rev RNA; 2011; 2(3):376-86. PubMed ID: 21957023 [TBL] [Abstract][Full Text] [Related]
5. Codon-specific translational defect caused by a wobble modification deficiency in mutant tRNA from a human mitochondrial disease. Kirino Y; Yasukawa T; Ohta S; Akira S; Ishihara K; Watanabe K; Suzuki T Proc Natl Acad Sci U S A; 2004 Oct; 101(42):15070-5. PubMed ID: 15477592 [TBL] [Abstract][Full Text] [Related]
6. Mitochondria-specific RNA-modifying enzymes responsible for the biosynthesis of the wobble base in mitochondrial tRNAs. Implications for the molecular pathogenesis of human mitochondrial diseases. Umeda N; Suzuki T; Yukawa M; Ohya Y; Shindo H; Watanabe K; Suzuki T J Biol Chem; 2005 Jan; 280(2):1613-24. PubMed ID: 15509579 [TBL] [Abstract][Full Text] [Related]
7. Specific correlation between the wobble modification deficiency in mutant tRNAs and the clinical features of a human mitochondrial disease. Kirino Y; Goto Y; Campos Y; Arenas J; Suzuki T Proc Natl Acad Sci U S A; 2005 May; 102(20):7127-32. PubMed ID: 15870203 [TBL] [Abstract][Full Text] [Related]
8. Chemical synthesis of the 5-taurinomethyl(-2-thio)uridine modified anticodon arm of the human mitochondrial tRNA(Leu(UUR)) and tRNA(Lys). Leszczynska G; Leonczak P; Wozniak K; Malkiewicz A RNA; 2014 Jun; 20(6):938-47. PubMed ID: 24757169 [TBL] [Abstract][Full Text] [Related]
9. Modification defect at anticodon wobble nucleotide of mitochondrial tRNAs(Leu)(UUR) with pathogenic mutations of mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episodes. Yasukawa T; Suzuki T; Ueda T; Ohta S; Watanabe K J Biol Chem; 2000 Feb; 275(6):4251-7. PubMed ID: 10660592 [TBL] [Abstract][Full Text] [Related]
10. Defect in modification at the anticodon wobble nucleotide of mitochondrial tRNA(Lys) with the MERRF encephalomyopathy pathogenic mutation. Yasukawa T; Suzuki T; Ishii N; Ueda T; Ohta S; Watanabe K FEBS Lett; 2000 Feb; 467(2-3):175-8. PubMed ID: 10675533 [TBL] [Abstract][Full Text] [Related]
11. Novel taurine-containing uridine derivatives and mitochondrial human diseases. Suzuki T; Suzuki T; Wada T; Saigo K; Watanabe K Nucleic Acids Res Suppl; 2001; (1):257-8. PubMed ID: 12836362 [TBL] [Abstract][Full Text] [Related]
12. Wobble modification defect in tRNA disturbs codon-anticodon interaction in a mitochondrial disease. Yasukawa T; Suzuki T; Ishii N; Ohta S; Watanabe K EMBO J; 2001 Sep; 20(17):4794-802. PubMed ID: 11532943 [TBL] [Abstract][Full Text] [Related]
13. Wobble modification defect suppresses translational activity of tRNAs with MERRF and MELAS mutations. Yasukawa T; Suzuki T; Ohta S; Watanabe K Mitochondrion; 2002 Nov; 2(1-2):129-41. PubMed ID: 16120315 [TBL] [Abstract][Full Text] [Related]
14. Modified uridines with C5-methylene substituents at the first position of the tRNA anticodon stabilize U.G wobble pairing during decoding. Kurata S; Weixlbaumer A; Ohtsuki T; Shimazaki T; Wada T; Kirino Y; Takai K; Watanabe K; Ramakrishnan V; Suzuki T J Biol Chem; 2008 Jul; 283(27):18801-11. PubMed ID: 18456657 [TBL] [Abstract][Full Text] [Related]
15. Decoding property of C5 uridine modification at the wobble position of tRNA anticodon. Kurata S; Ohtsuki T; Wada T; Kirino Y; Takai K; Saigo K; Watanabe K; Suzuki T Nucleic Acids Res Suppl; 2003; (3):245-6. PubMed ID: 14510472 [TBL] [Abstract][Full Text] [Related]
16. Taurine as a constituent of mitochondrial tRNAs: new insights into the functions of taurine and human mitochondrial diseases. Suzuki T; Suzuki T; Wada T; Saigo K; Watanabe K EMBO J; 2002 Dec; 21(23):6581-9. PubMed ID: 12456664 [TBL] [Abstract][Full Text] [Related]
17. The ROS-sensitive microRNA-9/9* controls the expression of mitochondrial tRNA-modifying enzymes and is involved in the molecular mechanism of MELAS syndrome. Meseguer S; Martínez-Zamora A; García-Arumí E; Andreu AL; Armengod ME Hum Mol Genet; 2015 Jan; 24(1):167-84. PubMed ID: 25149473 [TBL] [Abstract][Full Text] [Related]