These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
1015 related articles for article (PubMed ID: 17032058)
1. Lentiviral gene transfer of RPE65 rescues survival and function of cones in a mouse model of Leber congenital amaurosis. Bemelmans AP; Kostic C; Crippa SV; Hauswirth WW; Lem J; Munier FL; Seeliger MW; Wenzel A; Arsenijevic Y PLoS Med; 2006 Oct; 3(10):e347. PubMed ID: 17032058 [TBL] [Abstract][Full Text] [Related]
2. Bax-induced apoptosis in Leber's congenital amaurosis: a dual role in rod and cone degeneration. Hamann S; Schorderet DF; Cottet S PLoS One; 2009 Aug; 4(8):e6616. PubMed ID: 19672311 [TBL] [Abstract][Full Text] [Related]
3. Intraperitoneal chromophore injections delay early-onset and rapid retinal cone degeneration in a mouse model of Leber congenital amaurosis. Dai X; Jin X; Ye Q; Huang H; Duo L; Lu C; Bao J; Chen H Exp Eye Res; 2021 Nov; 212():108776. PubMed ID: 34582935 [TBL] [Abstract][Full Text] [Related]
4. Gene therapy rescues cone structure and function in the 3-month-old rd12 mouse: a model for midcourse RPE65 leber congenital amaurosis. Li X; Li W; Dai X; Kong F; Zheng Q; Zhou X; Lü F; Chang B; Rohrer B; Hauswirth WW; Qu J; Pang JJ Invest Ophthalmol Vis Sci; 2011 Jan; 52(1):7-15. PubMed ID: 21169527 [TBL] [Abstract][Full Text] [Related]
5. Downregulation of cone-specific gene expression and degeneration of cone photoreceptors in the Rpe65-/- mouse at early ages. Znoiko SL; Rohrer B; Lu K; Lohr HR; Crouch RK; Ma JX Invest Ophthalmol Vis Sci; 2005 Apr; 46(4):1473-9. PubMed ID: 15790918 [TBL] [Abstract][Full Text] [Related]
6. Long-term restoration of rod and cone vision by single dose rAAV-mediated gene transfer to the retina in a canine model of childhood blindness. Acland GM; Aguirre GD; Bennett J; Aleman TS; Cideciyan AV; Bennicelli J; Dejneka NS; Pearce-Kelling SE; Maguire AM; Palczewski K; Hauswirth WW; Jacobson SG Mol Ther; 2005 Dec; 12(6):1072-82. PubMed ID: 16226919 [TBL] [Abstract][Full Text] [Related]
7. Light prevents exogenous 11-cis retinal from maintaining cone photoreceptors in chromophore-deficient mice. Fan J; Crouch RK; Kono M Invest Ophthalmol Vis Sci; 2011 Apr; 52(5):2412-6. PubMed ID: 21228385 [TBL] [Abstract][Full Text] [Related]
8. Loss of cone photoreceptors caused by chromophore depletion is partially prevented by the artificial chromophore pro-drug, 9-cis-retinyl acetate. Maeda T; Cideciyan AV; Maeda A; Golczak M; Aleman TS; Jacobson SG; Palczewski K Hum Mol Genet; 2009 Jun; 18(12):2277-87. PubMed ID: 19339306 [TBL] [Abstract][Full Text] [Related]
9. Pharmacological Amelioration of Cone Survival and Vision in a Mouse Model for Leber Congenital Amaurosis. Li S; Samardzija M; Yang Z; Grimm C; Jin M J Neurosci; 2016 May; 36(21):5808-19. PubMed ID: 27225770 [TBL] [Abstract][Full Text] [Related]
10. RPE65 gene delivery restores isomerohydrolase activity and prevents early cone loss in Rpe65-/- mice. Chen Y; Moiseyev G; Takahashi Y; Ma JX Invest Ophthalmol Vis Sci; 2006 Mar; 47(3):1177-84. PubMed ID: 16505056 [TBL] [Abstract][Full Text] [Related]
11. Protection of cone photoreceptor M-opsin degradation with 9-cis-β-carotene-rich alga Dunaliella bardawil in Rpe65(-/-) mouse retinal explant culture. Ozaki T; Nakazawa M; Kudo T; Hirano S; Suzuki K; Ishiguro S Curr Eye Res; 2014 Dec; 39(12):1221-31. PubMed ID: 25006880 [TBL] [Abstract][Full Text] [Related]
12. Lentiviral gene transfer-mediated cone vision restoration in RPE65 knockout mice. Bemelmans AP; Kostic C; Cachafeiro M; Crippa SV; Wanner D; Tekaya M; Wenzel A; Arsenijevic Y Adv Exp Med Biol; 2008; 613():89-95. PubMed ID: 18188932 [No Abstract] [Full Text] [Related]
13. Gene therapeutic prospects in early onset of severe retinal dystrophy: restoration of vision in RPE65 Briard dogs using an AAV serotype 4 vector that specifically targets the retinal pigmented epithelium. Rolling F; Le Meur G; Stieger K; Smith AJ; Weber M; Deschamps JY; Nivard D; Mendes-Madeira A; Provost N; Péréon Y; Cherel Y; Ali RR; Hamel C; Moullier P; Rolling F Bull Mem Acad R Med Belg; 2006; 161(10-12):497-508; discussion 508-9. PubMed ID: 17503728 [TBL] [Abstract][Full Text] [Related]
14. Retinal degeneration 12 (rd12): a new, spontaneously arising mouse model for human Leber congenital amaurosis (LCA). Pang JJ; Chang B; Hawes NL; Hurd RE; Davisson MT; Li J; Noorwez SM; Malhotra R; McDowell JH; Kaushal S; Hauswirth WW; Nusinowitz S; Thompson DA; Heckenlively JR Mol Vis; 2005 Feb; 11():152-62. PubMed ID: 15765048 [TBL] [Abstract][Full Text] [Related]
15. Gene therapy regenerates protein expression in cone photoreceptors in Rpe65(R91W/R91W) mice. Kostic C; Crippa SV; Pignat V; Bemelmans AP; Samardzija M; Grimm C; Wenzel A; Arsenijevic Y PLoS One; 2011 Feb; 6(2):e16588. PubMed ID: 21304899 [TBL] [Abstract][Full Text] [Related]
16. Trafficking of membrane-associated proteins to cone photoreceptor outer segments requires the chromophore 11-cis-retinal. Zhang H; Fan J; Li S; Karan S; Rohrer B; Palczewski K; Frederick JM; Crouch RK; Baehr W J Neurosci; 2008 Apr; 28(15):4008-14. PubMed ID: 18400900 [TBL] [Abstract][Full Text] [Related]
17. Human cone photoreceptor dependence on RPE65 isomerase. Jacobson SG; Aleman TS; Cideciyan AV; Heon E; Golczak M; Beltran WA; Sumaroka A; Schwartz SB; Roman AJ; Windsor EA; Wilson JM; Aguirre GD; Stone EM; Palczewski K Proc Natl Acad Sci U S A; 2007 Sep; 104(38):15123-8. PubMed ID: 17848510 [TBL] [Abstract][Full Text] [Related]
18. Self-complementary AAV-mediated gene therapy restores cone function and prevents cone degeneration in two models of Rpe65 deficiency. Pang J; Boye SE; Lei B; Boye SL; Everhart D; Ryals R; Umino Y; Rohrer B; Alexander J; Li J; Dai X; Li Q; Chang B; Barlow R; Hauswirth WW Gene Ther; 2010 Jul; 17(7):815-26. PubMed ID: 20237510 [TBL] [Abstract][Full Text] [Related]
19. Cone outer segment morphology and cone function in the Rpe65-/- Nrl-/- mouse retina are amenable to retinoid replacement. Kunchithapautham K; Coughlin B; Crouch RK; Rohrer B Invest Ophthalmol Vis Sci; 2009 Oct; 50(10):4858-64. PubMed ID: 19407011 [TBL] [Abstract][Full Text] [Related]
20. Identifying photoreceptors in blind eyes caused by RPE65 mutations: Prerequisite for human gene therapy success. Jacobson SG; Aleman TS; Cideciyan AV; Sumaroka A; Schwartz SB; Windsor EA; Traboulsi EI; Heon E; Pittler SJ; Milam AH; Maguire AM; Palczewski K; Stone EM; Bennett J Proc Natl Acad Sci U S A; 2005 Apr; 102(17):6177-82. PubMed ID: 15837919 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]