These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
2. FHL1B Interacts with Lamin A/C and Emerin at the Nuclear Lamina and is Misregulated in Emery-Dreifuss Muscular Dystrophy. Ziat E; Mamchaoui K; Beuvin M; Nelson I; Azibani F; Spuler S; Bonne G; Bertrand AT J Neuromuscul Dis; 2016 Nov; 3(4):497-510. PubMed ID: 27911330 [TBL] [Abstract][Full Text] [Related]
4. Expression and localization of nuclear proteins in autosomal-dominant Emery-Dreifuss muscular dystrophy with LMNA R377H mutation. Reichart B; Klafke R; Dreger C; Krüger E; Motsch I; Ewald A; Schäfer J; Reichmann H; Müller CR; Dabauvalle MC BMC Cell Biol; 2004 Mar; 5():12. PubMed ID: 15053843 [TBL] [Abstract][Full Text] [Related]
5. Multitissular involvement in a family with LMNA and EMD mutations: Role of digenic mechanism? Ben Yaou R; Toutain A; Arimura T; Demay L; Massart C; Peccate C; Muchir A; Llense S; Deburgrave N; Leturcq F; Litim KE; Rahmoun-Chiali N; Richard P; Babuty D; Récan-Budiartha D; Bonne G Neurology; 2007 May; 68(22):1883-94. PubMed ID: 17536044 [TBL] [Abstract][Full Text] [Related]
6. The role of the nuclear envelope in Emery-Dreifuss muscular dystrophy. Morris GE Trends Mol Med; 2001 Dec; 7(12):572-7. PubMed ID: 11733221 [TBL] [Abstract][Full Text] [Related]
7. Activation of MAPK in hearts of EMD null mice: similarities between mouse models of X-linked and autosomal dominant Emery Dreifuss muscular dystrophy. Muchir A; Pavlidis P; Bonne G; Hayashi YK; Worman HJ Hum Mol Genet; 2007 Aug; 16(15):1884-95. PubMed ID: 17567779 [TBL] [Abstract][Full Text] [Related]
8. Nuclear envelope dystrophies show a transcriptional fingerprint suggesting disruption of Rb-MyoD pathways in muscle regeneration. Bakay M; Wang Z; Melcon G; Schiltz L; Xuan J; Zhao P; Sartorelli V; Seo J; Pegoraro E; Angelini C; Shneiderman B; Escolar D; Chen YW; Winokur ST; Pachman LM; Fan C; Mandler R; Nevo Y; Gordon E; Zhu Y; Dong Y; Wang Y; Hoffman EP Brain; 2006 Apr; 129(Pt 4):996-1013. PubMed ID: 16478798 [TBL] [Abstract][Full Text] [Related]
9. [Clinical, genealogical and molecular genetic study of Emery-Dreifuss muscular dystrophy]. Rudenskaia GE; Tverskaia SM; Chukhrova AL; Zakliaz'minskaia EV; Kuropatkina IuV; Dadali EL; Perminov VS; Poliakov AV Zh Nevrol Psikhiatr Im S S Korsakova; 2006; 106(10):58-65. PubMed ID: 17117676 [TBL] [Abstract][Full Text] [Related]
10. Nesprin-1 and -2 are involved in the pathogenesis of Emery Dreifuss muscular dystrophy and are critical for nuclear envelope integrity. Zhang Q; Bethmann C; Worth NF; Davies JD; Wasner C; Feuer A; Ragnauth CD; Yi Q; Mellad JA; Warren DT; Wheeler MA; Ellis JA; Skepper JN; Vorgerd M; Schlotter-Weigel B; Weissberg PL; Roberts RG; Wehnert M; Shanahan CM Hum Mol Genet; 2007 Dec; 16(23):2816-33. PubMed ID: 17761684 [TBL] [Abstract][Full Text] [Related]
11. Emery-Dreifuss muscular dystrophy. Puckelwartz M; McNally EM Handb Clin Neurol; 2011; 101():155-66. PubMed ID: 21496632 [TBL] [Abstract][Full Text] [Related]
12. Clinical and molecular genetic spectrum of autosomal dominant Emery-Dreifuss muscular dystrophy due to mutations of the lamin A/C gene. Bonne G; Mercuri E; Muchir A; Urtizberea A; Bécane HM; Recan D; Merlini L; Wehnert M; Boor R; Reuner U; Vorgerd M; Wicklein EM; Eymard B; Duboc D; Penisson-Besnier I; Cuisset JM; Ferrer X; Desguerre I; Lacombe D; Bushby K; Pollitt C; Toniolo D; Fardeau M; Schwartz K; Muntoni F Ann Neurol; 2000 Aug; 48(2):170-80. PubMed ID: 10939567 [TBL] [Abstract][Full Text] [Related]
13. Selective muscle involvement on magnetic resonance imaging in autosomal dominant Emery-Dreifuss muscular dystrophy. Mercuri E; Counsell S; Allsop J; Jungbluth H; Kinali M; Bonne G; Schwartz K; Bydder G; Dubowitz V; Muntoni F Neuropediatrics; 2002 Feb; 33(1):10-4. PubMed ID: 11930270 [TBL] [Abstract][Full Text] [Related]
14. Multiple roles for emerin: implications for Emery-Dreifuss muscular dystrophy. Holaska JM; Wilson KL Anat Rec A Discov Mol Cell Evol Biol; 2006 Jul; 288(7):676-80. PubMed ID: 16761279 [TBL] [Abstract][Full Text] [Related]
15. Clinical aspects of Emery-Dreifuss muscular dystrophy. Madej-Pilarczyk A Nucleus; 2018 Jan; 9(1):268-274. PubMed ID: 29633897 [TBL] [Abstract][Full Text] [Related]
16. Lamin A/C Assembly Defects in Bertrand AT; Brull A; Azibani F; Benarroch L; Chikhaoui K; Stewart CL; Medalia O; Ben Yaou R; Bonne G Cells; 2020 Mar; 9(4):. PubMed ID: 32244403 [No Abstract] [Full Text] [Related]
17. Emerin deficiency does not exacerbate cardiomyopathy in a murine model of Emery-Dreifuss muscular dystrophy caused by an LMNA gene mutation. Wada E; Matsumoto K; Susumu N; Kato M; Hayashi YK J Physiol Sci; 2023 Nov; 73(1):27. PubMed ID: 37940872 [TBL] [Abstract][Full Text] [Related]
18. LINC complex alterations in DMD and EDMD/CMT fibroblasts. Taranum S; Vaylann E; Meinke P; Abraham S; Yang L; Neumann S; Karakesisoglou I; Wehnert M; Noegel AA Eur J Cell Biol; 2012 Aug; 91(8):614-28. PubMed ID: 22555292 [TBL] [Abstract][Full Text] [Related]