147 related articles for article (PubMed ID: 1726721)
1. Probing the basic defect in cystic fibrosis.
Tsui LC
Curr Opin Genet Dev; 1991 Jun; 1(1):4-10. PubMed ID: 1726721
[TBL] [Abstract][Full Text] [Related]
2. cAMP-inducible chloride conductance in mouse fibroblast lines stably expressing the human cystic fibrosis transmembrane conductance regulator.
Rommens JM; Dho S; Bear CE; Kartner N; Kennedy D; Riordan JR; Tsui LC; Foskett JK
Proc Natl Acad Sci U S A; 1991 Sep; 88(17):7500-4. PubMed ID: 1715567
[TBL] [Abstract][Full Text] [Related]
3. Human lymphocytes transcribe the cystic fibrosis transmembrane conductance regulator gene and exhibit CF-defective cAMP-regulated chloride current.
McDonald TV; Nghiem PT; Gardner P; Martens CL
J Biol Chem; 1992 Feb; 267(5):3242-8. PubMed ID: 1371114
[TBL] [Abstract][Full Text] [Related]
4. Cystic fibrosis transmembrane conductance regulator (CFTR).
Higgins CF
Br Med Bull; 1992 Oct; 48(4):754-65. PubMed ID: 1281034
[TBL] [Abstract][Full Text] [Related]
5. Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells.
Rich DP; Anderson MP; Gregory RJ; Cheng SH; Paul S; Jefferson DM; McCann JD; Klinger KW; Smith AE; Welsh MJ
Nature; 1990 Sep; 347(6291):358-63. PubMed ID: 1699126
[TBL] [Abstract][Full Text] [Related]
6. Altered chloride ion channel kinetics associated with the delta F508 cystic fibrosis mutation.
Dalemans W; Barbry P; Champigny G; Jallat S; Dott K; Dreyer D; Crystal RG; Pavirani A; Lecocq JP; Lazdunski M
Nature; 1991 Dec 19-26; 354(6354):526-8. PubMed ID: 1722027
[TBL] [Abstract][Full Text] [Related]
7. The basic defect in cystic fibrosis.
Widdicombe JH; Wine JJ
Trends Biochem Sci; 1991 Dec; 16(12):474-7. PubMed ID: 1723552
[TBL] [Abstract][Full Text] [Related]
8. Correction of the apical membrane chloride permeability defect in polarized cystic fibrosis airway epithelia following retroviral-mediated gene transfer.
Olsen JC; Johnson LG; Stutts MJ; Sarkadi B; Yankaskas JR; Swanstrom R; Boucher RC
Hum Gene Ther; 1992 Jun; 3(3):253-66. PubMed ID: 1379473
[TBL] [Abstract][Full Text] [Related]
9. Two cystic fibrosis transmembrane conductance regulator mutations have different effects on both pulmonary phenotype and regulation of outwardly rectified chloride currents.
Fulmer SB; Schwiebert EM; Morales MM; Guggino WB; Cutting GR
Proc Natl Acad Sci U S A; 1995 Jul; 92(15):6832-6. PubMed ID: 7542778
[TBL] [Abstract][Full Text] [Related]
10. Relationship of a non-cystic fibrosis transmembrane conductance regulator-mediated chloride conductance to organ-level disease in Cftr(-/-) mice.
Clarke LL; Grubb BR; Yankaskas JR; Cotton CU; McKenzie A; Boucher RC
Proc Natl Acad Sci U S A; 1994 Jan; 91(2):479-83. PubMed ID: 7507247
[TBL] [Abstract][Full Text] [Related]
11. Cystic fibrosis. Sickly channels in mild disease.
Miller C
Nature; 1993 Mar; 362(6416):106. PubMed ID: 7680767
[No Abstract] [Full Text] [Related]
12. Cystic fibrosis, the CFTR, and rectifying Cl- channels.
Wine JJ; Brayden DJ; Hagiwara G; Krouse ME; Law TC; Müller UJ; Solc CK; Ward CL; Widdicombe JH; Xia Y
Adv Exp Med Biol; 1991; 290():253-69; discussion 269-72. PubMed ID: 1719763
[TBL] [Abstract][Full Text] [Related]
13. Mutations in CFTR associated with mild-disease-form Cl- channels with altered pore properties.
Sheppard DN; Rich DP; Ostedgaard LS; Gregory RJ; Smith AE; Welsh MJ
Nature; 1993 Mar; 362(6416):160-4. PubMed ID: 7680769
[TBL] [Abstract][Full Text] [Related]
14. Demonstration that CFTR is a chloride channel by alteration of its anion selectivity.
Anderson MP; Gregory RJ; Thompson S; Souza DW; Paul S; Mulligan RC; Smith AE; Welsh MJ
Science; 1991 Jul; 253(5016):202-5. PubMed ID: 1712984
[TBL] [Abstract][Full Text] [Related]
15. Understanding how cystic fibrosis mutations cause a loss of Cl- channel function.
Sheppard DN; Ostedgaard LS
Mol Med Today; 1996 Jul; 2(7):290-7. PubMed ID: 8796909
[TBL] [Abstract][Full Text] [Related]
16. Chloride conductance expressed by delta F508 and other mutant CFTRs in Xenopus oocytes.
Drumm ML; Wilkinson DJ; Smit LS; Worrell RT; Strong TV; Frizzell RA; Dawson DC; Collins FS
Science; 1991 Dec; 254(5039):1797-9. PubMed ID: 1722350
[TBL] [Abstract][Full Text] [Related]
17. Chloride channel and chloride conductance regulator domains of CFTR, the cystic fibrosis transmembrane conductance regulator.
Schwiebert EM; Morales MM; Devidas S; Egan ME; Guggino WB
Proc Natl Acad Sci U S A; 1998 Mar; 95(5):2674-9. PubMed ID: 9482946
[TBL] [Abstract][Full Text] [Related]
18. Identification and regulation of the cystic fibrosis transmembrane conductance regulator-generated chloride channel.
Berger HA; Anderson MP; Gregory RJ; Thompson S; Howard PW; Maurer RA; Mulligan R; Smith AE; Welsh MJ
J Clin Invest; 1991 Oct; 88(4):1422-31. PubMed ID: 1717515
[TBL] [Abstract][Full Text] [Related]
19. Outwardly rectifying chloride channels and CF: a divorce and remarriage.
Guggino WB
J Bioenerg Biomembr; 1993 Feb; 25(1):27-35. PubMed ID: 7680029
[TBL] [Abstract][Full Text] [Related]
20. Toward defining the function of the cystic fibrosis gene product.
Forstner GG
J Pediatr Gastroenterol Nutr; 1991 Nov; 13(4):432-3. PubMed ID: 1723427
[No Abstract] [Full Text] [Related]
[Next] [New Search]