410 related articles for article (PubMed ID: 17295076)
1. Synaptic plasma membrane Na(+), K (+)-ATPase activity is significantly reduced by the alpha-keto acids accumulating in maple syrup urine disease in rat cerebral cortex.
Wajner A; Bürger C; Dutra-Filho CS; Wajner M; de Souza Wyse AT; Wannmacher CM
Metab Brain Dis; 2007 Mar; 22(1):77-88. PubMed ID: 17295076
[TBL] [Abstract][Full Text] [Related]
2. Evidence that the branched-chain alpha-keto acids accumulating in maple syrup urine disease induce morphological alterations and death in cultured astrocytes from rat cerebral cortex.
Funchal C; Gottfried C; De Almeida LM; Wajner M; Pessoa-Pureur R
Glia; 2004 Nov; 48(3):230-40. PubMed ID: 15390119
[TBL] [Abstract][Full Text] [Related]
3. Inhibition of glutamate uptake into synaptic vesicles of rat brain by the metabolites accumulating in maple syrup urine disease.
Tavares RG; Santos CE; Tasca CI; Wajner M; Souza DO; Dutra-Filho CS
J Neurol Sci; 2000 Dec; 181(1-2):44-9. PubMed ID: 11099711
[TBL] [Abstract][Full Text] [Related]
4. alpha-keto acids accumulating in maple syrup urine disease stimulate lipid peroxidation and reduce antioxidant defences in cerebral cortex from young rats.
Bridi R; Braun CA; Zorzi GK; Wannmacher CM; Wajner M; Lissi EG; Dutra-Filho CS
Metab Brain Dis; 2005 Jun; 20(2):155-67. PubMed ID: 15938133
[TBL] [Abstract][Full Text] [Related]
5. Reduction of glutamate uptake into cerebral cortex of developing rats by the branched-chain alpha-keto acids accumulating in maple syrup urine disease.
Funchal C; Rosa AM; Wajner M; Wofchuk S; Pureur RP
Neurochem Res; 2004 Apr; 29(4):747-53. PubMed ID: 15098937
[TBL] [Abstract][Full Text] [Related]
6. Morphological alterations and induction of oxidative stress in glial cells caused by the branched-chain alpha-keto acids accumulating in maple syrup urine disease.
Funchal C; Latini A; Jacques-Silva MC; Dos Santos AQ; Buzin L; Gottfried C; Wajner M; Pessoa-Pureur R
Neurochem Int; 2006 Dec; 49(7):640-50. PubMed ID: 16822590
[TBL] [Abstract][Full Text] [Related]
7. Cerebral Oedema, Blood-Brain Barrier Breakdown and the Decrease in Na(+),K(+)-ATPase Activity in the Cerebral Cortex and Hippocampus are Prevented by Dexamethasone in an Animal Model of Maple Syrup Urine Disease.
Rosa L; Galant LS; Dall'Igna DM; Kolling J; Siebert C; Schuck PF; Ferreira GC; Wyse ATS; Dal-Pizzol F; Scaini G; Streck EL
Mol Neurobiol; 2016 Aug; 53(6):3714-3723. PubMed ID: 26133302
[TBL] [Abstract][Full Text] [Related]
8. Inhibition of brain energy metabolism by the alpha-keto acids accumulating in maple syrup urine disease.
Sgaravatti AM; Rosa RB; Schuck PF; Ribeiro CA; Wannmacher CM; Wyse AT; Dutra-Filho CS; Wajner M
Biochim Biophys Acta; 2003 Nov; 1639(3):232-8. PubMed ID: 14636955
[TBL] [Abstract][Full Text] [Related]
9. Effect of the branched-chain alpha-keto acids accumulating in maple syrup urine disease on S100B release from glial cells.
Funchal C; Tramontina F; Quincozes dos Santos A; Fraga de Souza D; Gonçalves CA; Pessoa-Pureur R; Wajner M
J Neurol Sci; 2007 Sep; 260(1-2):87-94. PubMed ID: 17499767
[TBL] [Abstract][Full Text] [Related]
10. Pathophysiology of maple syrup urine disease: Focus on the neurotoxic role of the accumulated branched-chain amino acids and branched-chain α-keto acids.
Amaral AU; Wajner M
Neurochem Int; 2022 Jul; 157():105360. PubMed ID: 35577033
[TBL] [Abstract][Full Text] [Related]
11. Prevention of DNA damage by L-carnitine induced by metabolites accumulated in maple syrup urine disease in human peripheral leukocytes in vitro.
Mescka CP; Wayhs CA; Guerreiro G; Manfredini V; Dutra-Filho CS; Vargas CR
Gene; 2014 Sep; 548(2):294-8. PubMed ID: 25046137
[TBL] [Abstract][Full Text] [Related]
12. Blood and tissue branched-chain amino and alpha-keto acid concentrations: effect of diet, starvation, and disease.
Hutson SM; Harper AE
Am J Clin Nutr; 1981 Feb; 34(2):173-83. PubMed ID: 7211722
[TBL] [Abstract][Full Text] [Related]
13. Creatine and antioxidant treatment prevent the inhibition of creatine kinase activity and the morphological alterations of C6 glioma cells induced by the branched-chain alpha-keto acids accumulating in maple syrup urine disease.
Funchal C; Schuck PF; Santos AQ; Jacques-Silva MC; Gottfried C; Pessoa-Pureur R; Wajner M
Cell Mol Neurobiol; 2006 Feb; 26(1):67-79. PubMed ID: 16633902
[TBL] [Abstract][Full Text] [Related]
14. Stimulation of lipid peroxidation in vitro in rat brain by the metabolites accumulating in maple syrup urine disease.
Fontella FU; Gassen E; Pulrolnik V; Wannmacher CM; Klein AB; Wajner M; Dutra-Filho CS
Metab Brain Dis; 2002 Mar; 17(1):47-54. PubMed ID: 11894849
[TBL] [Abstract][Full Text] [Related]
15. Effect of the branched-chain alpha-ketoacids accumulating in maple syrup urine disease on the high molecular weight neurofilament subunit (NF-H) in rat cerebral cortex.
Pessoa-Pureur R; Funchal C; de Lima Pelaez P; Vivian L; Oliveira Loureiro S; de Freitas Miranda R; Wajner M
Metab Brain Dis; 2002 Jun; 17(2):65-75. PubMed ID: 12083338
[TBL] [Abstract][Full Text] [Related]
16. Apoptotic signaling pathways induced by acute administration of branched-chain amino acids in an animal model of maple syrup urine disease.
Vilela TC; Scaini G; Furlanetto CB; Pasquali MA; Santos JP; Gelain DP; Moreira JC; Schuck PF; Ferreira GC; Streck EL
Metab Brain Dis; 2017 Feb; 32(1):115-122. PubMed ID: 27510712
[TBL] [Abstract][Full Text] [Related]
17. Branched-chain alpha-keto acids accumulating in maple syrup urine disease induce reorganization of phosphorylated GFAP in C6-glioma cells.
Funchal C; Dos Santos AQ; Jacques-Silva MC; Zamoner A; Gottfried C; Wajner M; Pessoa-Pureur R
Metab Brain Dis; 2005 Sep; 20(3):205-17. PubMed ID: 16167198
[TBL] [Abstract][Full Text] [Related]
18. Chloride-dependent inhibition of vesicular glutamate uptake by alpha-keto acids accumulated in maple syrup urine disease.
Reis M; Farage M; Wolosker H
Biochim Biophys Acta; 2000 Jul; 1475(2):114-8. PubMed ID: 10832024
[TBL] [Abstract][Full Text] [Related]
19. Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane depolarization or cytochrome c release: implications for neurological impairment associated with maple syrup urine disease.
Jouvet P; Rustin P; Taylor DL; Pocock JM; Felderhoff-Mueser U; Mazarakis ND; Sarraf C; Joashi U; Kozma M; Greenwood K; Edwards AD; Mehmet H
Mol Biol Cell; 2000 May; 11(5):1919-32. PubMed ID: 10793161
[TBL] [Abstract][Full Text] [Related]
20. Acute effects of intracerebroventricular administration of α-ketoisocaproic acid in young rats on inflammatory parameters.
Rabelo F; Lemos IDS; Dal Toé CP; Casagrande DD; Freitas MLS; Quadra MR; Lima IR; Generoso JS; Michels M; Silveira PCL; Pizzol FD; Streck EL
Metab Brain Dis; 2023 Jun; 38(5):1573-1579. PubMed ID: 36897514
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
