195 related articles for article (PubMed ID: 1730724)
41. Structure of the gene encoding dihydrolipoyl transacylase (E2) component of human branched chain alpha-keto acid dehydrogenase complex and characterization of an E2 pseudogene.
Lau KS; Herring WJ; Chuang JL; McKean M; Danner DJ; Cox RP; Chuang DT
J Biol Chem; 1992 Nov; 267(33):24090-6. PubMed ID: 1429740
[TBL] [Abstract][Full Text] [Related]
42. Molecular studies of mammalian branched-chain alpha-keto acid dehydrogenase complexes: domain structures, expression, and inborn errors.
Chuang DT
Ann N Y Acad Sci; 1989; 573():137-54. PubMed ID: 2699394
[TBL] [Abstract][Full Text] [Related]
43. Purification of active E1 alpha 2 beta 2 of Pseudomonas putida branched-chain-oxoacid dehydrogenase.
Hester K; Luo J; Burns G; Braswell EH; Sokatch JR
Eur J Biochem; 1995 Nov; 233(3):828-36. PubMed ID: 8521848
[TBL] [Abstract][Full Text] [Related]
44. Maple syrup urine disease. Complete defect of the E1 beta subunit of the branched chain alpha-ketoacid dehydrogenase complex due to a deletion of an 11-bp repeat sequence which encodes a mitochondrial targeting leader peptide in a family with the disease.
Nobukuni Y; Mitsubuchi H; Akaboshi I; Indo Y; Endo F; Yoshioka A; Matsuda I
J Clin Invest; 1991 May; 87(5):1862-6. PubMed ID: 2022752
[TBL] [Abstract][Full Text] [Related]
45. The primary structure of branched-chain alpha-oxo acid dehydrogenase from Bacillus subtilis and its similarity to other alpha-oxo acid dehydrogenases.
Wang GF; Kuriki T; Roy KL; Kaneda T
Eur J Biochem; 1993 May; 213(3):1091-9. PubMed ID: 8504804
[TBL] [Abstract][Full Text] [Related]
46. Heterogeneity of mutations in maple syrup urine disease (MSUD): screening and identification of affected E1 alpha and E1 beta subunits of the branched-chain alpha-keto-acid dehydrogenase multienzyme complex.
Nobukuni Y; Mitsubuchi H; Hayashida Y; Ohta K; Indo Y; Ichiba Y; Endo F; Matsuda I
Biochim Biophys Acta; 1993 Nov; 1225(1):64-70. PubMed ID: 8161368
[TBL] [Abstract][Full Text] [Related]
47. Site-directed mutagenesis and functional analysis of the active-site residues of the E2 component of bovine branched-chain alpha-keto acid dehydrogenase complex.
Meng M; Chuang DT
Biochemistry; 1994 Nov; 33(43):12879-85. PubMed ID: 7947694
[TBL] [Abstract][Full Text] [Related]
48. Nucleotide sequence of the 5' end including the initiation codon of cDNA for the E1 alpha subunit of the human branched chain alpha-ketoacid dehydrogenase complex.
McKean MC; Winkeler KA; Danner DJ
Biochim Biophys Acta; 1992 Nov; 1171(1):109-12. PubMed ID: 1420356
[TBL] [Abstract][Full Text] [Related]
49. Cloning of genes for branched-chain keto acid dehydrogenase in Pseudomonas putida.
Sykes PJ; Sokatch JR
Methods Enzymol; 1988; 166():350-9. PubMed ID: 3071713
[No Abstract] [Full Text] [Related]
50. Mechanisms for GroEL/GroES-mediated folding of a large 86-kDa fusion polypeptide in vitro.
Huang YS; Chuang DT
J Biol Chem; 1999 Apr; 274(15):10405-12. PubMed ID: 10187830
[TBL] [Abstract][Full Text] [Related]
51. Production of recombinant E1 component of branched-chain alpha-keto acid dehydrogenase complex.
Hawes JW; Zhao Y; Popov KM; Shimomura Y; Harris RA
Methods Enzymol; 2000; 324():200-7. PubMed ID: 10989431
[No Abstract] [Full Text] [Related]
52. Roles of amino acid residues surrounding phosphorylation site 1 of branched-chain alpha-ketoacid dehydrogenase (BCKDH) in catalysis and phosphorylation site recognition by BCKDH kinase.
Hawes JW; Schnepf RJ; Jenkins AE; Shimomura Y; Popov KM; Harris RA
J Biol Chem; 1995 Dec; 270(52):31071-6. PubMed ID: 8537366
[TBL] [Abstract][Full Text] [Related]
53. Purification of Pseudomonas putida branched-chain keto acid dehydrogenase E1 component.
Hester KL; Luo J; Sokatch JR
Methods Enzymol; 2000; 324():129-38. PubMed ID: 10989425
[No Abstract] [Full Text] [Related]
54. Altered kinetic properties of the branched-chain alpha-keto acid dehydrogenase complex due to mutation of the beta-subunit of the branched-chain alpha-keto acid decarboxylase (E1) component in lymphoblastoid cells derived from patients with maple syrup urine disease.
Indo Y; Kitano A; Endo F; Akaboshi I; Matsuda I
J Clin Invest; 1987 Jul; 80(1):63-70. PubMed ID: 3597778
[TBL] [Abstract][Full Text] [Related]
55. Molecular cloning of the E1 beta subunit of the rat branched chain alpha-ketoacid dehydrogenase.
Zhao Y; Kuntz MJ; Harris RA; Crabb DW
Biochim Biophys Acta; 1992 Sep; 1132(2):207-10. PubMed ID: 1390893
[No Abstract] [Full Text] [Related]
56. Effect of dietary protein on the liver content and subunit composition of the branched-chain alpha-ketoacid dehydrogenase complex.
Zhao Y; Popov KM; Shimomura Y; Kedishvili NY; Jaskiewicz J; Kuntz MJ; Kain J; Zhang B; Harris RA
Arch Biochem Biophys; 1994 Feb; 308(2):446-53. PubMed ID: 8109974
[TBL] [Abstract][Full Text] [Related]
57. Multi-site phosphorylation of branched-chain 2-oxoacid dehydrogenase complex within mitochondria isolated from rat liver, kidney and heart.
Cook KG; Lawson R; Yeaman SJ
FEBS Lett; 1983 Nov; 164(1):85-8. PubMed ID: 6653787
[TBL] [Abstract][Full Text] [Related]
58. Isolation of branched-chain alpha-keto acid dehydrogenase as active complex from bovine liver.
Danner DJ; Heffelfinger SC
Methods Enzymol; 1988; 166():298-302. PubMed ID: 3071712
[No Abstract] [Full Text] [Related]
59. A T-to-A substitution in the E1 alpha subunit gene of the branched-chain alpha-ketoacid dehydrogenase complex in two cell lines derived from Menonite maple syrup urine disease patients.
Matsuda I; Nobukuni Y; Mitsubuchi H; Indo Y; Endo F; Asaka J; Harada A
Biochem Biophys Res Commun; 1990 Oct; 172(2):646-51. PubMed ID: 2241958
[TBL] [Abstract][Full Text] [Related]
60. Solution structure and dynamics of the lipoic acid-bearing domain of human mitochondrial branched-chain alpha-keto acid dehydrogenase complex.
Chang CF; Chou HT; Chuang JL; Chuang DT; Huang TH
J Biol Chem; 2002 May; 277(18):15865-73. PubMed ID: 11839747
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]
