443 related articles for article (PubMed ID: 17597094)
1. Frataxin is essential for extramitochondrial Fe-S cluster proteins in mammalian tissues.
Martelli A; Wattenhofer-Donzé M; Schmucker S; Bouvet S; Reutenauer L; Puccio H
Hum Mol Genet; 2007 Nov; 16(22):2651-8. PubMed ID: 17597094
[TBL] [Abstract][Full Text] [Related]
2. Mammalian frataxin controls sulfur production and iron entry during de novo Fe4S4 cluster assembly.
Colin F; Martelli A; Clémancey M; Latour JM; Gambarelli S; Zeppieri L; Birck C; Page A; Puccio H; Ollagnier de Choudens S
J Am Chem Soc; 2013 Jan; 135(2):733-40. PubMed ID: 23265191
[TBL] [Abstract][Full Text] [Related]
3. Iron-sulfur protein maturation in human cells: evidence for a function of frataxin.
Stehling O; Elsässer HP; Brückel B; Mühlenhoff U; Lill R
Hum Mol Genet; 2004 Dec; 13(23):3007-15. PubMed ID: 15509595
[TBL] [Abstract][Full Text] [Related]
4. Mitochondrial frataxin interacts with ISD11 of the NFS1/ISCU complex and multiple mitochondrial chaperones.
Shan Y; Napoli E; Cortopassi G
Hum Mol Genet; 2007 Apr; 16(8):929-41. PubMed ID: 17331979
[TBL] [Abstract][Full Text] [Related]
5. The in vivo mitochondrial two-step maturation of human frataxin.
Schmucker S; Argentini M; Carelle-Calmels N; Martelli A; Puccio H
Hum Mol Genet; 2008 Nov; 17(22):3521-31. PubMed ID: 18725397
[TBL] [Abstract][Full Text] [Related]
6. Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia.
Rötig A; de Lonlay P; Chretien D; Foury F; Koenig M; Sidi D; Munnich A; Rustin P
Nat Genet; 1997 Oct; 17(2):215-7. PubMed ID: 9326946
[TBL] [Abstract][Full Text] [Related]
7. Frataxin deficiency causes upregulation of mitochondrial Lon and ClpP proteases and severe loss of mitochondrial Fe-S proteins.
Guillon B; Bulteau AL; Wattenhofer-Donzé M; Schmucker S; Friguet B; Puccio H; Drapier JC; Bouton C
FEBS J; 2009 Feb; 276(4):1036-47. PubMed ID: 19154341
[TBL] [Abstract][Full Text] [Related]
8. How Escherichia coli and Saccharomyces cerevisiae build Fe/S proteins.
Barras F; Loiseau L; Py B
Adv Microb Physiol; 2005; 50():41-101. PubMed ID: 16221578
[TBL] [Abstract][Full Text] [Related]
9. Extra-mitochondrial localisation of frataxin and its association with IscU1 during enterocyte-like differentiation of the human colon adenocarcinoma cell line Caco-2.
Acquaviva F; De Biase I; Nezi L; Ruggiero G; Tatangelo F; Pisano C; Monticelli A; Garbi C; Acquaviva AM; Cocozza S
J Cell Sci; 2005 Sep; 118(Pt 17):3917-24. PubMed ID: 16091420
[TBL] [Abstract][Full Text] [Related]
10. Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits.
Puccio H; Simon D; Cossée M; Criqui-Filipe P; Tiziano F; Melki J; Hindelang C; Matyas R; Rustin P; Koenig M
Nat Genet; 2001 Feb; 27(2):181-6. PubMed ID: 11175786
[TBL] [Abstract][Full Text] [Related]
11. Idebenone delays the onset of cardiac functional alteration without correction of Fe-S enzymes deficit in a mouse model for Friedreich ataxia.
Seznec H; Simon D; Monassier L; Criqui-Filipe P; Gansmuller A; Rustin P; Koenig M; Puccio H
Hum Mol Genet; 2004 May; 13(10):1017-24. PubMed ID: 15028670
[TBL] [Abstract][Full Text] [Related]
12. Friedreich ataxia: the oxidative stress paradox.
Seznec H; Simon D; Bouton C; Reutenauer L; Hertzog A; Golik P; Procaccio V; Patel M; Drapier JC; Koenig M; Puccio H
Hum Mol Genet; 2005 Feb; 14(4):463-74. PubMed ID: 15615771
[TBL] [Abstract][Full Text] [Related]
13. Normal and Friedreich ataxia cells express different isoforms of frataxin with complementary roles in iron-sulfur cluster assembly.
Gakh O; Bedekovics T; Duncan SF; Smith DY; Berkholz DS; Isaya G
J Biol Chem; 2010 Dec; 285(49):38486-501. PubMed ID: 20889968
[TBL] [Abstract][Full Text] [Related]
14. Distinct iron-sulfur cluster assembly complexes exist in the cytosol and mitochondria of human cells.
Tong WH; Rouault T
EMBO J; 2000 Nov; 19(21):5692-700. PubMed ID: 11060020
[TBL] [Abstract][Full Text] [Related]
15. The yeast frataxin homolog Yfh1p plays a specific role in the maturation of cellular Fe/S proteins.
Mühlenhoff U; Richhardt N; Ristow M; Kispal G; Lill R
Hum Mol Genet; 2002 Aug; 11(17):2025-36. PubMed ID: 12165564
[TBL] [Abstract][Full Text] [Related]
16. Thio modification of yeast cytosolic tRNA is an iron-sulfur protein-dependent pathway.
Nakai Y; Nakai M; Lill R; Suzuki T; Hayashi H
Mol Cell Biol; 2007 Apr; 27(8):2841-7. PubMed ID: 17283054
[TBL] [Abstract][Full Text] [Related]
17. Localization and functionality of microsporidian iron-sulphur cluster assembly proteins.
Goldberg AV; Molik S; Tsaousis AD; Neumann K; Kuhnke G; Delbac F; Vivares CP; Hirt RP; Lill R; Embley TM
Nature; 2008 Apr; 452(7187):624-8. PubMed ID: 18311129
[TBL] [Abstract][Full Text] [Related]
18. Essential role of Isd11 in mitochondrial iron-sulfur cluster synthesis on Isu scaffold proteins.
Wiedemann N; Urzica E; Guiard B; Müller H; Lohaus C; Meyer HE; Ryan MT; Meisinger C; Mühlenhoff U; Lill R; Pfanner N
EMBO J; 2006 Jan; 25(1):184-95. PubMed ID: 16341089
[TBL] [Abstract][Full Text] [Related]
19. Interaction of frataxin, an iron binding protein, with IscU of Fe-S clusters biogenesis pathway and its upregulation in AmpB resistant Leishmania donovani.
Zaidi A; Singh KP; Anwar S; Suman SS; Equbal A; Singh K; Dikhit MR; Bimal S; Pandey K; Das P; Ali V
Biochimie; 2015 Aug; 115():120-35. PubMed ID: 26032732
[TBL] [Abstract][Full Text] [Related]
20. Mitochondrial iron-sulfur protein biogenesis and human disease.
Stehling O; Wilbrecht C; Lill R
Biochimie; 2014 May; 100():61-77. PubMed ID: 24462711
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
