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22. Studies on the degradation of [U-3H]-phytanic acid and [U-3H]-pristanic acid in cultured fibroblasts from children with peroxisomal disorders. Kase BF; Björkhem I Scand J Clin Lab Invest; 1996 May; 56(3):211-7. PubMed ID: 8761525 [TBL] [Abstract][Full Text] [Related]
23. Infantile phytanic acid storage disease, a disorder of peroxisome biogenesis: a case report. Wanders RJ; Boltshauser E; Steinmann B; Spycher MA; Schutgens RB; van den Bosch H; Tager JM J Neurol Sci; 1990 Aug; 98(1):1-11. PubMed ID: 1700075 [TBL] [Abstract][Full Text] [Related]
24. Non-rhizomelic and rhizomelic chondrodysplasia punctata within a single complementation group. Motley AM; Tabak HF; Smeitink JA; Poll-The BT; Barth PG; Wanders RJ Biochim Biophys Acta; 1996 Apr; 1315(3):153-8. PubMed ID: 8611652 [TBL] [Abstract][Full Text] [Related]
25. X-linked dominant chondrodysplasia punctata with decreased dihydroxyacetone phosphate acyltransferase activity. Sato M; Ishikawa O; Miyachi Y Dermatology; 1996; 192(1):23-7. PubMed ID: 8832947 [TBL] [Abstract][Full Text] [Related]
26. Phytanic acid must be activated to phytanoyl-CoA prior to its alpha-oxidation in rat liver peroxisomes. Watkins PA; Howard AE; Mihalik SJ Biochim Biophys Acta; 1994 Oct; 1214(3):288-94. PubMed ID: 7918611 [TBL] [Abstract][Full Text] [Related]
27. Human dihydroxyacetonephosphate acyltransferase deficiency: a new peroxisomal disorder. Wanders RJ; Schumacher H; Heikoop J; Schutgens RB; Tager JM J Inherit Metab Dis; 1992; 15(3):389-91. PubMed ID: 1405476 [No Abstract] [Full Text] [Related]
28. Phytanic acid alpha-oxidation in rat liver peroxisomes. Production of alpha-hydroxyphytanoyl-CoA and formate is enhanced by dioxygenase cofactors. Mihalik SJ; Rainville AM; Watkins PA Eur J Biochem; 1995 Sep; 232(2):545-51. PubMed ID: 7556205 [TBL] [Abstract][Full Text] [Related]
30. In vivo study of phytanic acid alpha-oxidation in classic Refsum's disease and chondrodysplasia punctata. ten Brink HJ; Schor DS; Kok RM; Stellaard F; Kneer J; Poll-The BT; Saudubray JM; Jakobs C Pediatr Res; 1992 Nov; 32(5):566-70. PubMed ID: 1282700 [TBL] [Abstract][Full Text] [Related]
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36. Genetic and biochemical heterogeneity in patients with the rhizomelic form of chondrodysplasia punctata--a complementation study. Heikoop JC; Wanders RJ; Strijland A; Purvis R; Schutgens RB; Tager JM Hum Genet; 1992 Jun; 89(4):439-44. PubMed ID: 1618493 [TBL] [Abstract][Full Text] [Related]
37. Disorders related to the metabolism of phytanic acid. Stokke O; Skjeldal OH; Høie K Scand J Clin Lab Invest Suppl; 1986; 184():3-10. PubMed ID: 2438746 [TBL] [Abstract][Full Text] [Related]
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39. Plasmalogen biosynthesis in the diagnosis of peroxisomal disorders. Kremser K; Roscher A J Clin Chem Clin Biochem; 1989 May; 27(5):315-7. PubMed ID: 2760566 [TBL] [Abstract][Full Text] [Related]
40. Peroxisomal enzyme deficiency in the Conradi-Hunerman form of chondrodysplasia punctata. Holmes RD; Wilson GN; Hajra AK N Engl J Med; 1987 Jun; 316(25):1608. PubMed ID: 3587298 [No Abstract] [Full Text] [Related] [Previous] [Next] [New Search]