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4. Neonatal screening for biotinidase deficiency in east-Hungary. Havass Z J Inherit Metab Dis; 1991; 14(6):928-31. PubMed ID: 1779652 [TBL] [Abstract][Full Text] [Related]
5. Partial biotinidase deficiency: clinical and biochemical features. McVoy JR; Levy HL; Lawler M; Schmidt MA; Ebers DD; Hart PS; Pettit DD; Blitzer MG; Wolf B J Pediatr; 1990 Jan; 116(1):78-83. PubMed ID: 2295967 [TBL] [Abstract][Full Text] [Related]
6. [Prevalence study of biotinidase deficiency in newborns]. Pinto AL; Raymond KM; Bruck I; Antoniuk SA Rev Saude Publica; 1998 Apr; 32(2):148-52. PubMed ID: 9713119 [TBL] [Abstract][Full Text] [Related]
7. Clinical and neuropsychological outcome in 33 patients with biotinidase deficiency ascertained by nationwide newborn screening and family studies in Austria. Möslinger D; Stöckler-Ipsiroglu S; Scheibenreiter S; Tiefenthaler M; Mühl A; Seidl R; Strobl W; Plecko B; Suormala T; Baumgartner ER Eur J Pediatr; 2001 May; 160(5):277-82. PubMed ID: 11388594 [TBL] [Abstract][Full Text] [Related]
8. Mutations causing profound biotinidase deficiency in children ascertained by newborn screening in the United States occur at different frequencies than in symptomatic children. Norrgard KJ; Pomponio RJ; Hymes J; Wolf B Pediatr Res; 1999 Jul; 46(1):20-7. PubMed ID: 10400129 [TBL] [Abstract][Full Text] [Related]
9. Comparison of profound biotinidase deficiency in children ascertained clinically and by newborn screening using a simple method of accurately determining residual biotinidase activity. Hart PS; Barnstein BO; Secor McVoy JR; Matalon R; Wolf B Biochem Med Metab Biol; 1992 Aug; 48(1):41-5. PubMed ID: 1524870 [TBL] [Abstract][Full Text] [Related]
10. Partial biotinidase deficiency is usually due to the D444H mutation in the biotinidase gene. Swango KL; Demirkol M; Hüner G; Pronicka E; Sykut-Cegielska J; Schulze A; Mayatepek E; Wolf B Hum Genet; 1998 May; 102(5):571-5. PubMed ID: 9654207 [TBL] [Abstract][Full Text] [Related]
11. Mutation (Q456H) is the most common cause of profound biotinidase deficiency in children ascertained by newborn screening in the United States. Norrgard KJ; Pomponio RJ; Swango KL; Hymes J; Reynolds TR; Buck GA; Wolf B Biochem Mol Med; 1997 Jun; 61(1):22-7. PubMed ID: 9232193 [TBL] [Abstract][Full Text] [Related]
12. Newborn screening for biotinidase deficiency in Brazil: biochemical and molecular characterizations. Neto EC; Schulte J; Rubim R; Lewis E; DeMari J; Castilhos C; Brites A; Giugliani R; Jensen KP; Wolf B Braz J Med Biol Res; 2004 Mar; 37(3):295-9. PubMed ID: 15060693 [TBL] [Abstract][Full Text] [Related]
13. Two new mutations in children affected by partial biotinidase deficiency ascertained by newborn screening. Funghini S; Donati MA; Pasquini E; Gasperini S; Ciani F; Morrone A; Zammarchi E J Inherit Metab Dis; 2002 Aug; 25(4):328-30. PubMed ID: 12227467 [TBL] [Abstract][Full Text] [Related]
14. Neonatal screening for biotinidase deficiency: results of a 1-year pilot study. Heard GS; Wolf B; Jefferson LG; Weissbecker KA; Nance WE; McVoy JR; Napolitano A; Mitchell PL; Lambert FW; Linyear AS J Pediatr; 1986 Jan; 108(1):40-6. PubMed ID: 3944695 [TBL] [Abstract][Full Text] [Related]
15. Prospective ascertainment of complete and partial serum biotinidase deficiency in the newborn. Dunkel G; Scriver CR; Clow CL; Melançon S; Lemieux B; Grenier A; Laberge C J Inherit Metab Dis; 1989; 12(2):131-8. PubMed ID: 2502673 [TBL] [Abstract][Full Text] [Related]
16. A screening method for biotinidase deficiency in newborns. Heard GS; Secor McVoy JR; Wolf B Clin Chem; 1984 Jan; 30(1):125-7. PubMed ID: 6690118 [TBL] [Abstract][Full Text] [Related]
17. Neonatal screening for biotidinidase deficiency: results of a 1-year pilot study in four cities in central Anatolia. Tanzer F; Sancaktar M; Buyukkayhan D J Pediatr Endocrinol Metab; 2009 Dec; 22(12):1113-6. PubMed ID: 20333870 [TBL] [Abstract][Full Text] [Related]
18. Biochemical and immunologic characterization of serum biotinidase in partial biotinidase deficiency. Hart PS; Hymes J; Wolf B Pediatr Res; 1992 Mar; 31(3):261-5. PubMed ID: 1561012 [TBL] [Abstract][Full Text] [Related]
19. Neonatal screening for biotinidase deficiency in Hungary: clinical, biochemical and molecular studies. László A; Schuler EA; Sallay E; Endreffy E; Somogyi C; Várkonyi A; Havass Z; Jansen KP; Wolf B J Inherit Metab Dis; 2003; 26(7):693-8. PubMed ID: 14707518 [TBL] [Abstract][Full Text] [Related]
20. Biotinidase deficiency: Spectrum of molecular, enzymatic and clinical information from newborn screening Ontario, Canada (2007-2014). Gannavarapu S; Prasad C; DiRaimo J; Napier M; Goobie S; Potter M; Chakraborty P; Karaceper M; Munoz T; Schulze A; MacKenzie J; Li L; Geraghty MT; Al-Dirbashi OY; Rupar CA Mol Genet Metab; 2015 Nov; 116(3):146-51. PubMed ID: 26361991 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]