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5. Unique morphological spectrum of lymphomas in Nijmegen breakage syndrome (NBS) patients with high frequency of consecutive lymphoma formation. Gładkowska-Dura M; Dzierzanowska-Fangrat K; Dura WT; van Krieken JH; Chrzanowska KH; van Dongen JJ; Langerak AW J Pathol; 2008 Nov; 216(3):337-44. PubMed ID: 18788073 [TBL] [Abstract][Full Text] [Related]
6. An inducible null mutant murine model of Nijmegen breakage syndrome proves the essential function of NBS1 in chromosomal stability and cell viability. Demuth I; Frappart PO; Hildebrand G; Melchers A; Lobitz S; Stöckl L; Varon R; Herceg Z; Sperling K; Wang ZQ; Digweed M Hum Mol Genet; 2004 Oct; 13(20):2385-97. PubMed ID: 15333589 [TBL] [Abstract][Full Text] [Related]
7. Nijmegen breakage syndrome: clinical manifestation of defective response to DNA double-strand breaks. Digweed M; Sperling K DNA Repair (Amst); 2004; 3(8-9):1207-17. PubMed ID: 15279809 [TBL] [Abstract][Full Text] [Related]
8. Clinical variability and expression of the NBN c.657del5 allele in Nijmegen Breakage Syndrome. Lins S; Kim R; Krüger L; Chrzanowska KH; Seemanova E; Digweed M Gene; 2009 Nov; 447(1):12-7. PubMed ID: 19635536 [TBL] [Abstract][Full Text] [Related]
9. The clinical manifestation of a defective response to DNA double-strand breaks as exemplified by Nijmegen breakage syndrome. Demuth I; Digweed M Oncogene; 2007 Dec; 26(56):7792-8. PubMed ID: 18066092 [TBL] [Abstract][Full Text] [Related]
10. Nijmegen breakage syndrome: consequences of defective DNA double strand break repair. Digweed M; Reis A; Sperling K Bioessays; 1999 Aug; 21(8):649-56. PubMed ID: 10440861 [TBL] [Abstract][Full Text] [Related]
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12. Mutations in the Nijmegen breakage syndrome gene in medulloblastomas. Huang J; Grotzer MA; Watanabe T; Hewer E; Pietsch T; Rutkowski S; Ohgaki H Clin Cancer Res; 2008 Jul; 14(13):4053-8. PubMed ID: 18593981 [TBL] [Abstract][Full Text] [Related]
13. Radiation-induced DNA damage and repair in peripheral blood mononuclear cells from Nijmegen breakage syndrome patients and carriers assessed by the Comet assay. Bürger S; Schindler D; Fehn M; Mühl B; Mahrhofer H; Flentje M; Hoehn H; Seemanová E; Djuzenova CS Environ Mol Mutagen; 2006 May; 47(4):260-70. PubMed ID: 16470524 [TBL] [Abstract][Full Text] [Related]
14. Regulation of the Nijmegen breakage syndrome 1 gene NBS1 by c-myc, p53 and coactivators mediates estrogen protection from DNA damage in breast cancer cells. Wan R; Wu J; Baloue KK; Crowe DL Int J Oncol; 2013 Feb; 42(2):712-20. PubMed ID: 23291854 [TBL] [Abstract][Full Text] [Related]
15. Cancer risk of heterozygotes with the NBN founder mutation. Seemanová E; Jarolim P; Seeman P; Varon R; Digweed M; Swift M; Sperling K J Natl Cancer Inst; 2007 Dec; 99(24):1875-80. PubMed ID: 18073374 [TBL] [Abstract][Full Text] [Related]
16. Mutational inactivation of the nijmegen breakage syndrome gene (NBS1) in glioblastomas is associated with multiple TP53 mutations. Watanabe T; Nobusawa S; Lu S; Huang J; Mittelbronn M; Ohgaki H J Neuropathol Exp Neurol; 2009 Feb; 68(2):210-5. PubMed ID: 19151620 [TBL] [Abstract][Full Text] [Related]
17. Reduced expression of SRC family kinases decreases PI3K activity in NBS1-/- lymphoblasts. Sagan D; Eckardt-Schupp F; Eichholtz-Wirth H Biochem Biophys Res Commun; 2008 Dec; 377(1):181-6. PubMed ID: 18835245 [TBL] [Abstract][Full Text] [Related]
18. The defect in humoral immunity in patients with Nijmegen breakage syndrome is explained by defects in peripheral B lymphocyte maturation. Piątosa B; van der Burg M; Siewiera K; Pac M; van Dongen JJ; Langerak AW; Chrzanowska KH; Bernatowska E Cytometry A; 2012 Oct; 81(10):835-42. PubMed ID: 22851427 [TBL] [Abstract][Full Text] [Related]
19. Nijmegen breakage syndrome (NBS) with neurological abnormalities and without chromosomal instability. Seemanová E; Sperling K; Neitzel H; Varon R; Hadac J; Butova O; Schröck E; Seeman P; Digweed M J Med Genet; 2006 Mar; 43(3):218-24. PubMed ID: 16033915 [TBL] [Abstract][Full Text] [Related]
20. DNA double-strand break and chromosomal rejoining defects with misrejoining in Nijmegen breakage syndrome cells. Pluth JM; Yamazaki V; Cooper BA; Rydberg BE; Kirchgessner CU; Cooper PK DNA Repair (Amst); 2008 Jan; 7(1):108-18. PubMed ID: 17919995 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]