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2. Cystatin B: mutation detection, alternative splicing and expression in progressive myclonus epilepsy of Unverricht-Lundborg type (EPM1) patients. Joensuu T; Kuronen M; Alakurtti K; Tegelberg S; Hakala P; Aalto A; Huopaniemi L; Aula N; Michellucci R; Eriksson K; Lehesjoki AE Eur J Hum Genet; 2007 Feb; 15(2):185-93. PubMed ID: 17003839 [TBL] [Abstract][Full Text] [Related]
3. Altered tryptophan metabolism in the brain of cystatin B-deficient mice: a model system for progressive myoclonus epilepsy. Vaarmann A; Kaasik A; Zharkovsky A Epilepsia; 2006 Oct; 47(10):1650-4. PubMed ID: 17054687 [TBL] [Abstract][Full Text] [Related]
4. Loss of lysosomal association of cystatin B proteins representing progressive myoclonus epilepsy, EPM1, mutations. Alakurtti K; Weber E; Rinne R; Theil G; de Haan GJ; Lindhout D; Salmikangas P; Saukko P; Lahtinen U; Lehesjoki AE Eur J Hum Genet; 2005 Feb; 13(2):208-15. PubMed ID: 15483648 [TBL] [Abstract][Full Text] [Related]
6. Protein aggregation as a possible cause for pathology in a subset of familial Unverricht-Lundborg disease. Ceru S; Rabzelj S; Kopitar-Jerala N; Turk V; Zerovnik E Med Hypotheses; 2005; 64(5):955-9. PubMed ID: 15780491 [TBL] [Abstract][Full Text] [Related]
7. A pathogenetic hypothesis of Unverricht-Lundborg disease onset and progression. Franceschetti S; Sancini G; Buzzi A; Zucchini S; Paradiso B; Magnaghi G; Frassoni C; Chikhladze M; Avanzini G; Simonato M Neurobiol Dis; 2007 Mar; 25(3):675-85. PubMed ID: 17188503 [TBL] [Abstract][Full Text] [Related]
8. [From gene to disease; progressive myoclonus epilepsy of Unverricht-Lundborg and mutations in the cystatin B gene]. de Haan GJ; Halley DJ; Deelen WH; Lindhout D Ned Tijdschr Geneeskd; 2002 May; 146(18):846-8. PubMed ID: 12038222 [TBL] [Abstract][Full Text] [Related]
13. DNA deamination enables direct PCR amplification of the cystatin B (CSTB) gene-associated dodecamer repeat expansion in myoclonus epilepsy type Unverricht-Lundborg. Weinhaeusel A; Morris MA; Antonarakis SE; Haas OA Hum Mutat; 2003 Nov; 22(5):404-8. PubMed ID: 14517952 [TBL] [Abstract][Full Text] [Related]
14. Severer phenotype in Unverricht-Lundborg disease (EPM1) patients compound heterozygous for the dodecamer repeat expansion and the c.202C>T mutation in the CSTB gene. Koskenkorva P; Hyppönen J; Aikiä M; Mervaala E; Kiviranta T; Eriksson K; Lehesjoki AE; Vanninen R; Kälviäinen R Neurodegener Dis; 2011; 8(6):515-22. PubMed ID: 21757863 [TBL] [Abstract][Full Text] [Related]
15. Early microglial activation precedes neuronal loss in the brain of the Cstb-/- mouse model of progressive myoclonus epilepsy, EPM1. Tegelberg S; Kopra O; Joensuu T; Cooper JD; Lehesjoki AE J Neuropathol Exp Neurol; 2012 Jan; 71(1):40-53. PubMed ID: 22157618 [TBL] [Abstract][Full Text] [Related]
16. Dodecamer repeat expansion in cystatin B gene in progressive myoclonus epilepsy. Lalioti MD; Scott HS; Buresi C; Rossier C; Bottani A; Morris MA; Malafosse A; Antonarakis SE Nature; 1997 Apr; 386(6627):847-51. PubMed ID: 9126745 [TBL] [Abstract][Full Text] [Related]
17. Clinical features and genetics of Unverricht-Lundborg disease. Lehesjoki AE Adv Neurol; 2002; 89():193-7. PubMed ID: 11968445 [No Abstract] [Full Text] [Related]
18. Unstable insertion in the 5' flanking region of the cystatin B gene is the most common mutation in progressive myoclonus epilepsy type 1, EPM1. Lafrenière RG; Rochefort DL; Chrétien N; Rommens JM; Cochius JI; Kälviäinen R; Nousiainen U; Patry G; Farrell K; Söderfeldt B; Federico A; Hale BR; Cossio OH; Sørensen T; Pouliot MA; Kmiec T; Uldall P; Janszky J; Pranzatelli MR; Andermann F; Andermann E; Rouleau GA Nat Genet; 1997 Mar; 15(3):298-302. PubMed ID: 9054946 [TBL] [Abstract][Full Text] [Related]