330 related articles for article (PubMed ID: 18077198)
1. Characterization of L-aminocarnitine, an inhibitor of fatty acid oxidation.
Chegary M; Te Brinke H; Doolaard M; Ijlst L; Wijburg FA; Wanders RJ; Houten SM
Mol Genet Metab; 2008 Apr; 93(4):403-10. PubMed ID: 18077198
[TBL] [Abstract][Full Text] [Related]
2. Differentiation of long-chain fatty acid oxidation disorders using alternative precursors and acylcarnitine profiling in fibroblasts.
Roe DS; Yang BZ; Vianey-Saban C; Struys E; Sweetman L; Roe CR
Mol Genet Metab; 2006 Jan; 87(1):40-7. PubMed ID: 16297647
[TBL] [Abstract][Full Text] [Related]
3. Fatty acid oxidation flux predicts the clinical severity of VLCAD deficiency.
Diekman EF; Ferdinandusse S; van der Pol L; Waterham HR; Ruiter JP; Ijlst L; Wanders RJ; Houten SM; Wijburg FA; Blank AC; Asselbergs FW; Houtkooper RH; Visser G
Genet Med; 2015 Dec; 17(12):989-94. PubMed ID: 25834949
[TBL] [Abstract][Full Text] [Related]
4. Effects of fasting, feeding and exercise on plasma acylcarnitines among subjects with CPT2D, VLCADD and LCHADD/TFPD.
Elizondo G; Matern D; Vockley J; Harding CO; Gillingham MB
Mol Genet Metab; 2020; 131(1-2):90-97. PubMed ID: 32928639
[TBL] [Abstract][Full Text] [Related]
5. Peroxisomes contribute to the acylcarnitine production when the carnitine shuttle is deficient.
Violante S; Ijlst L; Te Brinke H; Koster J; Tavares de Almeida I; Wanders RJ; Ventura FV; Houten SM
Biochim Biophys Acta; 2013 Sep; 1831(9):1467-74. PubMed ID: 23850792
[TBL] [Abstract][Full Text] [Related]
6. Effect of heat stress and bezafibrate on mitochondrial beta-oxidation: comparison between cultured cells from normal and mitochondrial fatty acid oxidation disorder children using in vitro probe acylcarnitine profiling assay.
Li H; Fukuda S; Hasegawa Y; Kobayashi H; Purevsuren J; Mushimoto Y; Yamaguchi S
Brain Dev; 2010 May; 32(5):362-70. PubMed ID: 19589653
[TBL] [Abstract][Full Text] [Related]
7. Differential induction of genes in liver and brown adipose tissue regulated by peroxisome proliferator-activated receptor-alpha during fasting and cold exposure in acyl-CoA dehydrogenase-deficient mice.
Goetzman ES; Tian L; Wood PA
Mol Genet Metab; 2005 Jan; 84(1):39-47. PubMed ID: 15639194
[TBL] [Abstract][Full Text] [Related]
8. Interactions between the consumption of a high-fat diet and fasting in the regulation of fatty acid oxidation enzyme gene expression: an evaluation of potential mechanisms.
Frier BC; Jacobs RL; Wright DC
Am J Physiol Regul Integr Comp Physiol; 2011 Feb; 300(2):R212-21. PubMed ID: 21084676
[TBL] [Abstract][Full Text] [Related]
9. Carnitine palmitoyltransferase 2 and carnitine/acylcarnitine translocase are involved in the mitochondrial synthesis and export of acylcarnitines.
Violante S; Ijlst L; Te Brinke H; Tavares de Almeida I; Wanders RJ; Ventura FV; Houten SM
FASEB J; 2013 May; 27(5):2039-44. PubMed ID: 23322164
[TBL] [Abstract][Full Text] [Related]
10. Bezafibrate can be a new treatment option for mitochondrial fatty acid oxidation disorders: evaluation by in vitro probe acylcarnitine assay.
Yamaguchi S; Li H; Purevsuren J; Yamada K; Furui M; Takahashi T; Mushimoto Y; Kobayashi H; Hasegawa Y; Taketani T; Fukao T; Fukuda S
Mol Genet Metab; 2012 Sep; 107(1-2):87-91. PubMed ID: 22841441
[TBL] [Abstract][Full Text] [Related]
11. Intracellular in vitro probe acylcarnitine assay for identifying deficiencies of carnitine transporter and carnitine palmitoyltransferase-1.
Purevsuren J; Kobayashi H; Hasegawa Y; Yamada K; Takahashi T; Takayanagi M; Fukao T; Fukuda S; Yamaguchi S
Anal Bioanal Chem; 2013 Feb; 405(4):1345-51. PubMed ID: 23143007
[TBL] [Abstract][Full Text] [Related]
12. Inborn Errors of Long-Chain Fatty Acid β-Oxidation Link Neural Stem Cell Self-Renewal to Autism.
Xie Z; Jones A; Deeney JT; Hur SK; Bankaitis VA
Cell Rep; 2016 Feb; 14(5):991-999. PubMed ID: 26832401
[TBL] [Abstract][Full Text] [Related]
13. Medium-chain fatty acids undergo elongation before beta-oxidation in fibroblasts.
Jones PM; Butt Y; Messmer B; Boriak R; Bennett MJ
Biochem Biophys Res Commun; 2006 Jul; 346(1):193-7. PubMed ID: 16750167
[TBL] [Abstract][Full Text] [Related]
14. Peroxisome proliferator activated receptor delta (PPARdelta) agonist but not PPARalpha corrects carnitine palmitoyl transferase 2 deficiency in human muscle cells.
Djouadi F; Aubey F; Schlemmer D; Bastin J
J Clin Endocrinol Metab; 2005 Mar; 90(3):1791-7. PubMed ID: 15613406
[TBL] [Abstract][Full Text] [Related]
15. Histidine-450 is the catalytic residue of L-3-hydroxyacyl coenzyme A dehydrogenase associated with the large alpha-subunit of the multienzyme complex of fatty acid oxidation from Escherichia coli.
He XY; Yang SY
Biochemistry; 1996 Jul; 35(29):9625-30. PubMed ID: 8755745
[TBL] [Abstract][Full Text] [Related]
16. Short communication: high insulin concentrations inhibit fatty acid oxidation-related gene expression in calf hepatocytes cultured in vitro.
Li P; Wu CC; Long M; Zhang Y; Li XB; He JB; Wang Z; Liu GW
J Dairy Sci; 2013 Jun; 96(6):3840-4. PubMed ID: 23567053
[TBL] [Abstract][Full Text] [Related]
17. MSC-induced lncRNA HCP5 drove fatty acid oxidation through miR-3619-5p/AMPK/PGC1α/CEBPB axis to promote stemness and chemo-resistance of gastric cancer.
Wu H; Liu B; Chen Z; Li G; Zhang Z
Cell Death Dis; 2020 Apr; 11(4):233. PubMed ID: 32300102
[TBL] [Abstract][Full Text] [Related]
18. Long-chain fatty acid oxidation during early human development.
Oey NA; den Boer ME; Wijburg FA; Vekemans M; Augé J; Steiner C; Wanders RJ; Waterham HR; Ruiter JP; Attié-Bitach T
Pediatr Res; 2005 Jun; 57(6):755-9. PubMed ID: 15845636
[TBL] [Abstract][Full Text] [Related]
19. Carnitine-acylcarnitine translocase deficiency, clinical, biochemical and genetic aspects.
Rubio-Gozalbo ME; Bakker JA; Waterham HR; Wanders RJ
Mol Aspects Med; 2004; 25(5-6):521-32. PubMed ID: 15363639
[TBL] [Abstract][Full Text] [Related]
20. Carnitine-acylcarnitine translocase deficiency: Two neonatal cases with common splicing mutation and in vitro bezafibrate response.
Vatanavicharn N; Yamada K; Aoyama Y; Fukao T; Densupsoontorn N; Jirapinyo P; Sathienkijkanchai A; Yamaguchi S; Wasant P
Brain Dev; 2015 Aug; 37(7):698-703. PubMed ID: 25459972
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]