217 related articles for article (PubMed ID: 18192269)
1. Detergent-insoluble aggregates associated with amyotrophic lateral sclerosis in transgenic mice contain primarily full-length, unmodified superoxide dismutase-1.
Shaw BF; Lelie HL; Durazo A; Nersissian AM; Xu G; Chan PK; Gralla EB; Tiwari A; Hayward LJ; Borchelt DR; Valentine JS; Whitelegge JP
J Biol Chem; 2008 Mar; 283(13):8340-50. PubMed ID: 18192269
[TBL] [Abstract][Full Text] [Related]
2. Heat shock factor 1 over-expression protects against exposure of hydrophobic residues on mutant SOD1 and early mortality in a mouse model of amyotrophic lateral sclerosis.
Lin PY; Simon SM; Koh WK; Folorunso O; Umbaugh CS; Pierce A
Mol Neurodegener; 2013 Nov; 8():43. PubMed ID: 24256636
[TBL] [Abstract][Full Text] [Related]
3. Inducible superoxide dismutase 1 aggregation in transgenic amyotrophic lateral sclerosis mouse fibroblasts.
Turner BJ; Lopes EC; Cheema SS
J Cell Biochem; 2004 Apr; 91(5):1074-84. PubMed ID: 15034941
[TBL] [Abstract][Full Text] [Related]
4. Copper and zinc metallation status of copper-zinc superoxide dismutase from amyotrophic lateral sclerosis transgenic mice.
Lelie HL; Liba A; Bourassa MW; Chattopadhyay M; Chan PK; Gralla EB; Miller LM; Borchelt DR; Valentine JS; Whitelegge JP
J Biol Chem; 2011 Jan; 286(4):2795-806. PubMed ID: 21068388
[TBL] [Abstract][Full Text] [Related]
5. Overexpression of Abeta is associated with acceleration of onset of motor impairment and superoxide dismutase 1 aggregation in an amyotrophic lateral sclerosis mouse model.
Li QX; Mok SS; Laughton KM; McLean CA; Volitakis I; Cherny RA; Cheung NS; White AR; Masters CL
Aging Cell; 2006 Apr; 5(2):153-65. PubMed ID: 16626394
[TBL] [Abstract][Full Text] [Related]
6. Conversion to the amyotrophic lateral sclerosis phenotype is associated with intermolecular linked insoluble aggregates of SOD1 in mitochondria.
Deng HX; Shi Y; Furukawa Y; Zhai H; Fu R; Liu E; Gorrie GH; Khan MS; Hung WY; Bigio EH; Lukas T; Dal Canto MC; O'Halloran TV; Siddique T
Proc Natl Acad Sci U S A; 2006 May; 103(18):7142-7. PubMed ID: 16636275
[TBL] [Abstract][Full Text] [Related]
7. Proteins that bind to misfolded mutant superoxide dismutase-1 in spinal cords from transgenic amyotrophic lateral sclerosis (ALS) model mice.
Zetterström P; Graffmo KS; Andersen PM; Brännström T; Marklund SL
J Biol Chem; 2011 Jun; 286(23):20130-6. PubMed ID: 21493711
[TBL] [Abstract][Full Text] [Related]
8. Role of mutant SOD1 disulfide oxidation and aggregation in the pathogenesis of familial ALS.
Karch CM; Prudencio M; Winkler DD; Hart PJ; Borchelt DR
Proc Natl Acad Sci U S A; 2009 May; 106(19):7774-9. PubMed ID: 19416874
[TBL] [Abstract][Full Text] [Related]
9. Minute quantities of misfolded mutant superoxide dismutase-1 cause amyotrophic lateral sclerosis.
Jonsson PA; Ernhill K; Andersen PM; Bergemalm D; Brännström T; Gredal O; Nilsson P; Marklund SL
Brain; 2004 Jan; 127(Pt 1):73-88. PubMed ID: 14534160
[TBL] [Abstract][Full Text] [Related]
10. Amyotrophic lateral sclerosis-related mutant superoxide dismutase 1 aggregates inhibit 14-3-3-mediated cell survival by sequestration into the JUNQ compartment.
Park JH; Jang HR; Lee IY; Oh HK; Choi EJ; Rhim H; Kang S
Hum Mol Genet; 2017 Sep; 26(18):3615-3629. PubMed ID: 28666328
[TBL] [Abstract][Full Text] [Related]
11. Disulfide cross-linked protein represents a significant fraction of ALS-associated Cu, Zn-superoxide dismutase aggregates in spinal cords of model mice.
Furukawa Y; Fu R; Deng HX; Siddique T; O'Halloran TV
Proc Natl Acad Sci U S A; 2006 May; 103(18):7148-53. PubMed ID: 16636274
[TBL] [Abstract][Full Text] [Related]
12. Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues.
Watanabe M; Dykes-Hoberg M; Culotta VC; Price DL; Wong PC; Rothstein JD
Neurobiol Dis; 2001 Dec; 8(6):933-41. PubMed ID: 11741389
[TBL] [Abstract][Full Text] [Related]
13. Wild-type Cu/Zn superoxide dismutase (SOD1) does not facilitate, but impedes the formation of protein aggregates of amyotrophic lateral sclerosis causing mutant SOD1.
Witan H; Gorlovoy P; Kaya AM; Koziollek-Drechsler I; Neumann H; Behl C; Clement AM
Neurobiol Dis; 2009 Nov; 36(2):331-42. PubMed ID: 19660548
[TBL] [Abstract][Full Text] [Related]
14. Superoxide dismutase 1 mutants related to amyotrophic lateral sclerosis induce endoplasmic stress in neuro2a cells.
Oh YK; Shin KS; Yuan J; Kang SJ
J Neurochem; 2008 Feb; 104(4):993-1005. PubMed ID: 18233996
[TBL] [Abstract][Full Text] [Related]
15. A cysteine residue affects the conformational state and neuronal toxicity of mutant SOD1 in mice: relevance to the pathogenesis of ALS.
Nagano S; Takahashi Y; Yamamoto K; Masutani H; Fujiwara N; Urushitani M; Araki T
Hum Mol Genet; 2015 Jun; 24(12):3427-39. PubMed ID: 25762155
[TBL] [Abstract][Full Text] [Related]
16. Mutant superoxide dismutase aggregates from human spinal cord transmit amyotrophic lateral sclerosis.
Ekhtiari Bidhendi E; Bergh J; Zetterström P; Forsberg K; Pakkenberg B; Andersen PM; Marklund SL; Brännström T
Acta Neuropathol; 2018 Dec; 136(6):939-953. PubMed ID: 30284034
[TBL] [Abstract][Full Text] [Related]
17. Insoluble mutant SOD1 is partly oligoubiquitinated in amyotrophic lateral sclerosis mice.
Basso M; Massignan T; Samengo G; Cheroni C; De Biasi S; Salmona M; Bendotti C; Bonetto V
J Biol Chem; 2006 Nov; 281(44):33325-35. PubMed ID: 16943203
[TBL] [Abstract][Full Text] [Related]
18. Aggregates of mutant protein appear progressively in dendrites, in periaxonal processes of oligodendrocytes, and in neuronal and astrocytic perikarya of mice expressing the SOD1(G93A) mutation of familial amyotrophic lateral sclerosis.
Stieber A; Gonatas JO; Gonatas NK
J Neurol Sci; 2000 Aug; 177(2):114-23. PubMed ID: 10980307
[TBL] [Abstract][Full Text] [Related]
19. An examination of wild-type SOD1 in modulating the toxicity and aggregation of ALS-associated mutant SOD1.
Prudencio M; Durazo A; Whitelegge JP; Borchelt DR
Hum Mol Genet; 2010 Dec; 19(24):4774-89. PubMed ID: 20871097
[TBL] [Abstract][Full Text] [Related]
20. Alteration of familial ALS-linked mutant SOD1 solubility with disease progression: its modulation by the proteasome and Hsp70.
Koyama S; Arawaka S; Chang-Hong R; Wada M; Kawanami T; Kurita K; Kato M; Nagai M; Aoki M; Itoyama Y; Sobue G; Chan PH; Kato T
Biochem Biophys Res Commun; 2006 May; 343(3):719-30. PubMed ID: 16563356
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
