BIOMARKERS

Molecular Biopsy of Human Tumors

- a resource for Precision Medicine *

389 related articles for article (PubMed ID: 18378094)

  • 1. Decreased expression of the mitochondrial matrix proteases Lon and ClpP in cells from a patient with hereditary spastic paraplegia (SPG13).
    Hansen J; Corydon TJ; Palmfeldt J; Dürr A; Fontaine B; Nielsen MN; Christensen JH; Gregersen N; Bross P
    Neuroscience; 2008 May; 153(2):474-82. PubMed ID: 18378094
    [TBL] [Abstract][Full Text] [Related]  

  • 2. Differential degradation of variant medium-chain acyl-CoA dehydrogenase by the protein quality control proteases Lon and ClpXP.
    Hansen J; Gregersen N; Bross P
    Biochem Biophys Res Commun; 2005 Aug; 333(4):1160-70. PubMed ID: 15978546
    [TBL] [Abstract][Full Text] [Related]  

  • 3. Late onset motoneuron disorder caused by mitochondrial Hsp60 chaperone deficiency in mice.
    Magnoni R; Palmfeldt J; Christensen JH; Sand M; Maltecca F; Corydon TJ; West M; Casari G; Bross P
    Neurobiol Dis; 2013 Jun; 54():12-23. PubMed ID: 23466696
    [TBL] [Abstract][Full Text] [Related]  

  • 4. Mitochondrial protein homeostasis: the cooperative roles of chaperones and proteases.
    Voos W
    Res Microbiol; 2009 Nov; 160(9):718-25. PubMed ID: 19723579
    [TBL] [Abstract][Full Text] [Related]  

  • 5. The Hsp60-(p.V98I) mutation associated with hereditary spastic paraplegia SPG13 compromises chaperonin function both in vitro and in vivo.
    Bross P; Naundrup S; Hansen J; Nielsen MN; Christensen JH; Kruhøffer M; Palmfeldt J; Corydon TJ; Gregersen N; Ang D; Georgopoulos C; Nielsen KL
    J Biol Chem; 2008 Jun; 283(23):15694-700. PubMed ID: 18400758
    [TBL] [Abstract][Full Text] [Related]  

  • 6. Hereditary spastic paraplegia SPG13 is associated with a mutation in the gene encoding the mitochondrial chaperonin Hsp60.
    Hansen JJ; Dürr A; Cournu-Rebeix I; Georgopoulos C; Ang D; Nielsen MN; Davoine CS; Brice A; Fontaine B; Gregersen N; Bross P
    Am J Hum Genet; 2002 May; 70(5):1328-32. PubMed ID: 11898127
    [TBL] [Abstract][Full Text] [Related]  

  • 7. Frataxin deficiency causes upregulation of mitochondrial Lon and ClpP proteases and severe loss of mitochondrial Fe-S proteins.
    Guillon B; Bulteau AL; Wattenhofer-Donzé M; Schmucker S; Friguet B; Puccio H; Drapier JC; Bouton C
    FEBS J; 2009 Feb; 276(4):1036-47. PubMed ID: 19154341
    [TBL] [Abstract][Full Text] [Related]  

  • 8. Compartment-specific perturbation of protein handling activates genes encoding mitochondrial chaperones.
    Yoneda T; Benedetti C; Urano F; Clark SG; Harding HP; Ron D
    J Cell Sci; 2004 Aug; 117(Pt 18):4055-66. PubMed ID: 15280428
    [TBL] [Abstract][Full Text] [Related]  

  • 9. Down-regulation of Hsp60 expression by RNAi impairs folding of medium-chain acyl-CoA dehydrogenase wild-type and disease-associated proteins.
    Corydon TJ; Hansen J; Bross P; Jensen TG
    Mol Genet Metab; 2005 Aug; 85(4):260-70. PubMed ID: 15927499
    [TBL] [Abstract][Full Text] [Related]  

  • 10. Bacterial inclusion bodies are cytotoxic in vivo in absence of functional chaperones DnaK or GroEL.
    González-Montalbán N; Carrió MM; Cuatrecasas S; Arís A; Villaverde A
    J Biotechnol; 2005 Sep; 118(4):406-12. PubMed ID: 16024126
    [TBL] [Abstract][Full Text] [Related]  

  • 11. Mitochondrial Lon regulates apoptosis through the association with Hsp60-mtHsp70 complex.
    Kao TY; Chiu YC; Fang WC; Cheng CW; Kuo CY; Juan HF; Wu SH; Lee AY
    Cell Death Dis; 2015 Feb; 6(2):e1642. PubMed ID: 25675302
    [TBL] [Abstract][Full Text] [Related]  

  • 12. Upregulation of the mitochondrial Lon Protease allows adaptation to acute oxidative stress but dysregulation is associated with chronic stress, disease, and aging.
    Ngo JK; Pomatto LC; Davies KJ
    Redox Biol; 2013 Feb; 1(1):258-64. PubMed ID: 24024159
    [TBL] [Abstract][Full Text] [Related]  

  • 13. Importance of the lon protease in mitochondrial maintenance and the significance of declining lon in aging.
    Ngo JK; Davies KJ
    Ann N Y Acad Sci; 2007 Nov; 1119():78-87. PubMed ID: 18056957
    [TBL] [Abstract][Full Text] [Related]  

  • 14. Lon and ClpP proteases participate in the physiological disintegration of bacterial inclusion bodies.
    Vera A; Arís A; Carrió M; González-Montalbán N; Villaverde A
    J Biotechnol; 2005 Sep; 119(2):163-71. PubMed ID: 15967532
    [TBL] [Abstract][Full Text] [Related]  

  • 15. The Hsp60 folding machinery is crucial for manganese superoxide dismutase folding and function.
    Magnoni R; Palmfeldt J; Hansen J; Christensen JH; Corydon TJ; Bross P
    Free Radic Res; 2014 Feb; 48(2):168-79. PubMed ID: 24151936
    [TBL] [Abstract][Full Text] [Related]  

  • 16. Downregulation of the human Lon protease impairs mitochondrial structure and function and causes cell death.
    Bota DA; Ngo JK; Davies KJ
    Free Radic Biol Med; 2005 Mar; 38(5):665-77. PubMed ID: 15683722
    [TBL] [Abstract][Full Text] [Related]  

  • 17. MitCHAP-60 and Hereditary Spastic Paraplegia SPG-13 Arise from an Inactive hsp60 Chaperonin that Fails to Fold the ATP Synthase β-Subunit.
    Wang J; Enriquez AS; Li J; Rodriguez A; Holguin B; Von Salzen D; Bhatt JM; Bernal RA
    Sci Rep; 2019 Aug; 9(1):12300. PubMed ID: 31444388
    [TBL] [Abstract][Full Text] [Related]  

  • 18. Effects of acclimation temperature and cadmium exposure on mitochondrial aconitase and LON protease from a model marine ectotherm, Crassostrea virginica.
    Sanni B; Williams K; Sokolov EP; Sokolova IM
    Comp Biochem Physiol C Toxicol Pharmacol; 2008 Jan; 147(1):101-12. PubMed ID: 17869588
    [TBL] [Abstract][Full Text] [Related]  

  • 19. Inactivation of the hereditary spastic paraplegia-associated Hspd1 gene encoding the Hsp60 chaperone results in early embryonic lethality in mice.
    Christensen JH; Nielsen MN; Hansen J; Füchtbauer A; Füchtbauer EM; West M; Corydon TJ; Gregersen N; Bross P
    Cell Stress Chaperones; 2010 Nov; 15(6):851-63. PubMed ID: 20393889
    [TBL] [Abstract][Full Text] [Related]  

  • 20. Comparative genomics and functional roles of the ATP-dependent proteases Lon and Clp during cytosolic protein degradation.
    Chandu D; Nandi D
    Res Microbiol; 2004 Nov; 155(9):710-9. PubMed ID: 15501647
    [TBL] [Abstract][Full Text] [Related]  

    [Next]    [New Search]
    of 20.