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2. Mutations of ANT1, Twinkle, and POLG1 in sporadic progressive external ophthalmoplegia (PEO). Agostino A; Valletta L; Chinnery PF; Ferrari G; Carrara F; Taylor RW; Schaefer AM; Turnbull DM; Tiranti V; Zeviani M Neurology; 2003 Apr; 60(8):1354-6. PubMed ID: 12707443 [TBL] [Abstract][Full Text] [Related]
3. Progressive external ophthalmoplegia in southwestern Finland: a clinical and genetic study. Martikainen MH; Hinttala R; Röyttä M; Jääskeläinen S; Wendelin-Saarenhovi M; Parkkola R; Majamaa K Neuroepidemiology; 2012; 38(2):114-9. PubMed ID: 22377773 [TBL] [Abstract][Full Text] [Related]
4. Association of novel POLG mutations and multiple mitochondrial DNA deletions with variable clinical phenotypes in a Spanish population. González-Vioque E; Blázquez A; Fernández-Moreira D; Bornstein B; Bautista J; Arpa J; Navarro C; Campos Y; Fernández-Moreno MA; Garesse R; Arenas J; Martín MA Arch Neurol; 2006 Jan; 63(1):107-11. PubMed ID: 16401742 [TBL] [Abstract][Full Text] [Related]
5. POLG1, C10ORF2, and ANT1 mutations are uncommon in sporadic progressive external ophthalmoplegia with multiple mitochondrial DNA deletions. Hudson G; Deschauer M; Taylor RW; Hanna MG; Fialho D; Schaefer AM; He LP; Blakely E; Turnbull DM; Chinnery PF Neurology; 2006 May; 66(9):1439-41. PubMed ID: 16682683 [TBL] [Abstract][Full Text] [Related]
6. Familial parkinsonism and ophthalmoplegia from a mutation in the mitochondrial DNA helicase twinkle. Baloh RH; Salavaggione E; Milbrandt J; Pestronk A Arch Neurol; 2007 Jul; 64(7):998-1000. PubMed ID: 17620490 [TBL] [Abstract][Full Text] [Related]
7. Mutation of OPA1 causes dominant optic atrophy with external ophthalmoplegia, ataxia, deafness and multiple mitochondrial DNA deletions: a novel disorder of mtDNA maintenance. Hudson G; Amati-Bonneau P; Blakely EL; Stewart JD; He L; Schaefer AM; Griffiths PG; Ahlqvist K; Suomalainen A; Reynier P; McFarland R; Turnbull DM; Chinnery PF; Taylor RW Brain; 2008 Feb; 131(Pt 2):329-37. PubMed ID: 18065439 [TBL] [Abstract][Full Text] [Related]
8. Clinical and genetic heterogeneity in progressive external ophthalmoplegia due to mutations in polymerase gamma. Filosto M; Mancuso M; Nishigaki Y; Pancrudo J; Harati Y; Gooch C; Mankodi A; Bayne L; Bonilla E; Shanske S; Hirano M; DiMauro S Arch Neurol; 2003 Sep; 60(9):1279-84. PubMed ID: 12975295 [TBL] [Abstract][Full Text] [Related]
9. Progressive external ophthalmoplegia and multiple mitochondrial DNA deletions. Van Goethem G; Martin JJ; Van Broeckhoven C Acta Neurol Belg; 2002 Mar; 102(1):39-42. PubMed ID: 12094562 [TBL] [Abstract][Full Text] [Related]
10. Sporadic PEO caused by a novel POLG variation and a Twinkle mutation: digenic inheritance? Da Pozzo P; Rubegni A; Rufa A; Cardaioli E; Taglia I; Gallus GN; Malandrini A; Federico A Neurol Sci; 2015 Sep; 36(9):1713-5. PubMed ID: 26050231 [TBL] [Abstract][Full Text] [Related]
11. Molecular analysis of ANT1, TWINKLE and POLG in patients with multiple deletions or depletion of mitochondrial DNA by a dHPLC-based assay. Naïmi M; Bannwarth S; Procaccio V; Pouget J; Desnuelle C; Pellissier JF; Rötig A; Munnich A; Calvas P; Richelme C; Jonveaux P; Castelnovo G; Simon M; Clanet M; Wallace D; Paquis-Flucklinger V Eur J Hum Genet; 2006 Aug; 14(8):917-22. PubMed ID: 16639411 [TBL] [Abstract][Full Text] [Related]
12. Molecular analysis in a family presenting with a mild form of late-onset autosomal dominant chronic progressive external ophthalmoplegia. Negro R; Zoccolella S; Dell'aglio R; Amati A; Artuso L; Bisceglia L; Lavolpe V; Papa S; Serlenga L; Petruzzella V Neuromuscul Disord; 2009 Jun; 19(6):423-6. PubMed ID: 19428252 [TBL] [Abstract][Full Text] [Related]
13. A new POLG1 mutation with peo and severe axonal and demyelinating sensory-motor neuropathy. Santoro L; Manganelli F; Lanzillo R; Tessa A; Barbieri F; Pierelli F; Di Giacinto G; Nigro V; Santorelli FM J Neurol; 2006 Jul; 253(7):869-74. PubMed ID: 16715201 [TBL] [Abstract][Full Text] [Related]
14. The clinical, histochemical, and molecular spectrum of PEO1 (Twinkle)-linked adPEO. Fratter C; Gorman GS; Stewart JD; Buddles M; Smith C; Evans J; Seller A; Poulton J; Roberts M; Hanna MG; Rahman S; Omer SE; Klopstock T; Schoser B; Kornblum C; Czermin B; Lecky B; Blakely EL; Craig K; Chinnery PF; Turnbull DM; Horvath R; Taylor RW Neurology; 2010 May; 74(20):1619-26. PubMed ID: 20479361 [TBL] [Abstract][Full Text] [Related]
15. Two novel mutations in PEO1 (twinkle) gene associated with chronic external ophthalmoplegia. Ronchi D; Fassone E; Bordoni A; Sciacco M; Lucchini V; Di Fonzo A; Rizzuti M; Colombo I; Napoli L; Ciscato P; Moggio M; Cosi A; Collotta M; Corti S; Bresolin N; Comi GP J Neurol Sci; 2011 Sep; 308(1-2):173-6. PubMed ID: 21689831 [TBL] [Abstract][Full Text] [Related]
16. Twinkle and POLG defects enhance age-dependent accumulation of mutations in the control region of mtDNA. Wanrooij S; Luoma P; van Goethem G; van Broeckhoven C; Suomalainen A; Spelbrink JN Nucleic Acids Res; 2004; 32(10):3053-64. PubMed ID: 15181170 [TBL] [Abstract][Full Text] [Related]
19. Twinkle mutations associated with autosomal dominant progressive external ophthalmoplegia lead to impaired helicase function and in vivo mtDNA replication stalling. Goffart S; Cooper HM; Tyynismaa H; Wanrooij S; Suomalainen A; Spelbrink JN Hum Mol Genet; 2009 Jan; 18(2):328-40. PubMed ID: 18971204 [TBL] [Abstract][Full Text] [Related]
20. Remarkable infidelity of polymerase gammaA associated with mutations in POLG1 exonuclease domain. Del Bo R; Bordoni A; Sciacco M; Di Fonzo A; Galbiati S; Crimi M; Bresolin N; Comi GP Neurology; 2003 Oct; 61(7):903-8. PubMed ID: 14557557 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]