246 related articles for article (PubMed ID: 19126203)
1. Dynamic simulations on the mitochondrial fatty acid beta-oxidation network.
Modre-Osprian R; Osprian I; Tilg B; Schreier G; Weinberger KM; Graber A
BMC Syst Biol; 2009 Jan; 3():2. PubMed ID: 19126203
[TBL] [Abstract][Full Text] [Related]
2. New genetic defects in mitochondrial fatty acid oxidation and carnitine deficiency.
Stanley CA
Adv Pediatr; 1987; 34():59-88. PubMed ID: 3318304
[TBL] [Abstract][Full Text] [Related]
3. Mitochondrial β-oxidation of saturated fatty acids in humans.
Adeva-Andany MM; Carneiro-Freire N; Seco-Filgueira M; Fernández-Fernández C; Mouriño-Bayolo D
Mitochondrion; 2019 May; 46():73-90. PubMed ID: 29551309
[TBL] [Abstract][Full Text] [Related]
4. Diagnosis of mitochondrial fatty acid oxidation defects.
Duran M; Bruinvis L; Ketting D; Dorland L
Padiatr Padol; 1993; 28(1):19-25. PubMed ID: 8446424
[TBL] [Abstract][Full Text] [Related]
5. Mouse models for disorders of mitochondrial fatty acid beta-oxidation.
Schuler AM; Wood PA
ILAR J; 2002; 43(2):57-65. PubMed ID: 11917157
[TBL] [Abstract][Full Text] [Related]
6. Mutation analysis in mitochondrial fatty acid oxidation defects: Exemplified by acyl-CoA dehydrogenase deficiencies, with special focus on genotype-phenotype relationship.
Gregersen N; Andresen BS; Corydon MJ; Corydon TJ; Olsen RK; Bolund L; Bross P
Hum Mutat; 2001 Sep; 18(3):169-89. PubMed ID: 11524729
[TBL] [Abstract][Full Text] [Related]
7. Biochemical competition makes fatty-acid β-oxidation vulnerable to substrate overload.
van Eunen K; Simons SM; Gerding A; Bleeker A; den Besten G; Touw CM; Houten SM; Groen BK; Krab K; Reijngoud DJ; Bakker BM
PLoS Comput Biol; 2013; 9(8):e1003186. PubMed ID: 23966849
[TBL] [Abstract][Full Text] [Related]
8. Mitochondrial fatty acid oxidation disorders: pathophysiological studies in mouse models.
Spiekerkoetter U; Wood PA
J Inherit Metab Dis; 2010 Oct; 33(5):539-46. PubMed ID: 20532823
[TBL] [Abstract][Full Text] [Related]
9. Living on the edge: substrate competition explains loss of robustness in mitochondrial fatty-acid oxidation disorders.
van Eunen K; Volker-Touw CM; Gerding A; Bleeker A; Wolters JC; van Rijt WJ; Martines AM; Niezen-Koning KE; Heiner RM; Permentier H; Groen AK; Reijngoud DJ; Derks TG; Bakker BM
BMC Biol; 2016 Dec; 14(1):107. PubMed ID: 27927213
[TBL] [Abstract][Full Text] [Related]
10. The fatty acid oxidation enzyme long-chain acyl-CoA dehydrogenase can be a source of mitochondrial hydrogen peroxide.
Zhang Y; Bharathi SS; Beck ME; Goetzman ES
Redox Biol; 2019 Sep; 26():101253. PubMed ID: 31234015
[TBL] [Abstract][Full Text] [Related]
11. Mitochondrial dysfunction in fatty acid oxidation disorders: insights from human and animal studies.
Wajner M; Amaral AU
Biosci Rep; 2015 Nov; 36(1):e00281. PubMed ID: 26589966
[TBL] [Abstract][Full Text] [Related]
12. 2,6-Dimethylheptanoyl-CoA is a specific substrate for long-chain acyl-CoA dehydrogenase (LCAD): evidence for a major role of LCAD in branched-chain fatty acid oxidation.
Wanders RJ; Denis S; Ruiter JP; IJlst L; Dacremont G
Biochim Biophys Acta; 1998 Jul; 1393(1):35-40. PubMed ID: 9714723
[TBL] [Abstract][Full Text] [Related]
13. Is autism a disorder of fatty acid metabolism? Possible dysfunction of mitochondrial beta-oxidation by long chain acyl-CoA dehydrogenase.
Clark-Taylor T; Clark-Taylor BE
Med Hypotheses; 2004; 62(6):970-5. PubMed ID: 15142659
[TBL] [Abstract][Full Text] [Related]
14. Influence of dietary fatty acid chain-length on metabolic tolerance in mouse models of inherited defects in mitochondrial fatty acid beta-oxidation.
Schuler AM; Gower BA; Matern D; Rinaldo P; Wood PA
Mol Genet Metab; 2004 Dec; 83(4):322-9. PubMed ID: 15589119
[TBL] [Abstract][Full Text] [Related]
15. Participation of peroxisomes in the metabolism of xenobiotic acyl compounds: comparison between peroxisomal and mitochondrial beta-oxidation of omega-phenyl fatty acids in rat liver.
Yamada J; Ogawa S; Horie S; Watanabe T; Suga T
Biochim Biophys Acta; 1987 Sep; 921(2):292-301. PubMed ID: 3651489
[TBL] [Abstract][Full Text] [Related]
16. Evidence that Oxidative Disbalance and Mitochondrial Dysfunction are Involved in the Pathophysiology of Fatty Acid Oxidation Disorders.
Ribas GS; Vargas CR
Cell Mol Neurobiol; 2022 Apr; 42(3):521-532. PubMed ID: 32876899
[TBL] [Abstract][Full Text] [Related]
17. Regulation of mitochondrial fatty acid β-oxidation in human: what can we learn from inborn fatty acid β-oxidation deficiencies?
Bastin J
Biochimie; 2014 Jan; 96():113-20. PubMed ID: 23764392
[TBL] [Abstract][Full Text] [Related]
18. Fetal fatty acid oxidation disorders, their effect on maternal health and neonatal outcome: impact of expanded newborn screening on their diagnosis and management.
Shekhawat PS; Matern D; Strauss AW
Pediatr Res; 2005 May; 57(5 Pt 2):78R-86R. PubMed ID: 15817498
[TBL] [Abstract][Full Text] [Related]
19. Role of mitochondrial acyl-CoA dehydrogenases in the metabolism of dicarboxylic fatty acids.
Bharathi SS; Zhang Y; Gong Z; Muzumdar R; Goetzman ES
Biochem Biophys Res Commun; 2020 Jun; 527(1):162-166. PubMed ID: 32446361
[TBL] [Abstract][Full Text] [Related]
20. Leaky beta-oxidation of a trans-fatty acid: incomplete beta-oxidation of elaidic acid is due to the accumulation of 5-trans-tetradecenoyl-CoA and its hydrolysis and conversion to 5-trans-tetradecenoylcarnitine in the matrix of rat mitochondria.
Yu W; Liang X; Ensenauer RE; Vockley J; Sweetman L; Schulz H
J Biol Chem; 2004 Dec; 279(50):52160-7. PubMed ID: 15466478
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
