177 related articles for article (PubMed ID: 19131642)
1. A cystic fibrosis respiratory epithelial cell chronically treated by miglustat acquires a non-cystic fibrosis-like phenotype.
Norez C; Antigny F; Noel S; Vandebrouck C; Becq F
Am J Respir Cell Mol Biol; 2009 Aug; 41(2):217-25. PubMed ID: 19131642
[TBL] [Abstract][Full Text] [Related]
2. Parallel improvement of sodium and chloride transport defects by miglustat (n-butyldeoxynojyrimicin) in cystic fibrosis epithelial cells.
Noël S; Wilke M; Bot AG; De Jonge HR; Becq F
J Pharmacol Exp Ther; 2008 Jun; 325(3):1016-23. PubMed ID: 18309088
[TBL] [Abstract][Full Text] [Related]
3. Anti-inflammatory effect of miglustat in bronchial epithelial cells.
Dechecchi MC; Nicolis E; Norez C; Bezzerri V; Borgatti M; Mancini I; Rizzotti P; Ribeiro CM; Gambari R; Becq F; Cabrini G
J Cyst Fibros; 2008 Nov; 7(6):555-65. PubMed ID: 18815075
[TBL] [Abstract][Full Text] [Related]
4. Abnormal spatial diffusion of Ca2+ in F508del-CFTR airway epithelial cells.
Antigny F; Norez C; Cantereau A; Becq F; Vandebrouck C
Respir Res; 2008 Oct; 9(1):70. PubMed ID: 18973672
[TBL] [Abstract][Full Text] [Related]
5. Rescue of functional delF508-CFTR channels in cystic fibrosis epithelial cells by the alpha-glucosidase inhibitor miglustat.
Norez C; Noel S; Wilke M; Bijvelds M; Jorna H; Melin P; DeJonge H; Becq F
FEBS Lett; 2006 Apr; 580(8):2081-6. PubMed ID: 16546175
[TBL] [Abstract][Full Text] [Related]
6. Transient receptor potential canonical channel 6 links Ca2+ mishandling to cystic fibrosis transmembrane conductance regulator channel dysfunction in cystic fibrosis.
Antigny F; Norez C; Dannhoffer L; Bertrand J; Raveau D; Corbi P; Jayle C; Becq F; Vandebrouck C
Am J Respir Cell Mol Biol; 2011 Jan; 44(1):83-90. PubMed ID: 20203293
[TBL] [Abstract][Full Text] [Related]
7. Airway delivery of low-dose miglustat normalizes nasal potential difference in F508del cystic fibrosis mice.
Lubamba B; Lebacq J; Lebecque P; Vanbever R; Leonard A; Wallemacq P; Leal T
Am J Respir Crit Care Med; 2009 Jun; 179(11):1022-8. PubMed ID: 19299496
[TBL] [Abstract][Full Text] [Related]
8. Calcium homeostasis is abnormal in cystic fibrosis airway epithelial cells but is normalized after rescue of F508del-CFTR.
Antigny F; Norez C; Becq F; Vandebrouck C
Cell Calcium; 2008 Feb; 43(2):175-83. PubMed ID: 17590432
[TBL] [Abstract][Full Text] [Related]
9. Enhanced F508del-CFTR channel activity ameliorates bone pathology in murine cystic fibrosis.
Le Henaff C; Haÿ E; Velard F; Marty C; Tabary O; Marie PJ; Jacquot JP
Am J Pathol; 2014 Apr; 184(4):1132-1141. PubMed ID: 24529904
[TBL] [Abstract][Full Text] [Related]
10. Maintaining low Ca2+ level in the endoplasmic reticulum restores abnormal endogenous F508del-CFTR trafficking in airway epithelial cells.
Norez C; Antigny F; Becq F; Vandebrouck C
Traffic; 2006 May; 7(5):562-73. PubMed ID: 16643279
[TBL] [Abstract][Full Text] [Related]
11. Reduced expression of Tis7/IFRD1 protein in murine and human cystic fibrosis airway epithelial cell models homozygous for the F508del-CFTR mutation.
Blanchard E; Marie S; Riffault L; Bonora M; Tabary O; Clement A; Jacquot J
Biochem Biophys Res Commun; 2011 Aug; 411(3):471-6. PubMed ID: 21723850
[TBL] [Abstract][Full Text] [Related]
12. Discovery of alpha-aminoazaheterocycle-methylglyoxal adducts as a new class of high-affinity inhibitors of cystic fibrosis transmembrane conductance regulator chloride channels.
Routaboul C; Norez C; Melin P; Molina MC; Boucherle B; Bossard F; Noel S; Robert R; Gauthier C; Becq F; Décout JL
J Pharmacol Exp Ther; 2007 Sep; 322(3):1023-35. PubMed ID: 17578899
[TBL] [Abstract][Full Text] [Related]
13. Purinergic signaling underlies CFTR control of human airway epithelial cell volume.
Braunstein GM; Zsembery A; Tucker TA; Schwiebert EM
J Cyst Fibros; 2004 Jun; 3(2):99-117. PubMed ID: 15463893
[TBL] [Abstract][Full Text] [Related]
14. Proteasome-dependent pharmacological rescue of cystic fibrosis transmembrane conductance regulator revealed by mutation of glycine 622.
Norez C; Bilan F; Kitzis A; Mettey Y; Becq F
J Pharmacol Exp Ther; 2008 Apr; 325(1):89-99. PubMed ID: 18230692
[TBL] [Abstract][Full Text] [Related]
15. Cystic fibrosis transmembrane conductance regulator (CFTR)-mediated residual chloride secretion does not protect against early chronic Pseudomonas aeruginosa infection in F508del homozygous cystic fibrosis patients.
Derichs N; Mekus F; Bronsveld I; Bijman J; Veeze HJ; von der Hardt H; Tummler B; Ballmann M
Pediatr Res; 2004 Jan; 55(1):69-75. PubMed ID: 14605249
[TBL] [Abstract][Full Text] [Related]
16. Identification of a NBD1-binding pharmacological chaperone that corrects the trafficking defect of F508del-CFTR.
Sampson HM; Robert R; Liao J; Matthes E; Carlile GW; Hanrahan JW; Thomas DY
Chem Biol; 2011 Feb; 18(2):231-42. PubMed ID: 21338920
[TBL] [Abstract][Full Text] [Related]
17. Guanabenz, an alpha2-selective adrenergic agonist, activates Ca2+-dependent chloride currents in cystic fibrosis human airway epithelial cells.
Norez C; Vandebrouck C; Antigny F; Dannhoffer L; Blondel M; Becq F
Eur J Pharmacol; 2008 Sep; 592(1-3):33-40. PubMed ID: 18640110
[TBL] [Abstract][Full Text] [Related]
18. Defective formation of PKA/CnA-dependent annexin 2-S100A10/CFTR complex in DeltaF508 cystic fibrosis cells.
Borthwick LA; Riemen C; Goddard C; Colledge WH; Mehta A; Gerke V; Muimo R
Cell Signal; 2008 Jun; 20(6):1073-83. PubMed ID: 18346874
[TBL] [Abstract][Full Text] [Related]
19. Impact of the cystic fibrosis mutation F508del-CFTR on renal cyst formation and growth.
Li H; Yang W; Mendes F; Amaral MD; Sheppard DN
Am J Physiol Renal Physiol; 2012 Oct; 303(8):F1176-86. PubMed ID: 22874761
[TBL] [Abstract][Full Text] [Related]
20. Defective CFTR induces aggresome formation and lung inflammation in cystic fibrosis through ROS-mediated autophagy inhibition.
Luciani A; Villella VR; Esposito S; Brunetti-Pierri N; Medina D; Settembre C; Gavina M; Pulze L; Giardino I; Pettoello-Mantovani M; D'Apolito M; Guido S; Masliah E; Spencer B; Quaratino S; Raia V; Ballabio A; Maiuri L
Nat Cell Biol; 2010 Sep; 12(9):863-75. PubMed ID: 20711182
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
