These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
141 related articles for article (PubMed ID: 19386237)
1. Enhanced degradation of synaptophysin by the proteasome in mucopolysaccharidosis type IIIB. Vitry S; Ausseil J; Hocquemiller M; Bigou S; Dos Santos Coura R; Heard JM Mol Cell Neurosci; 2009 May; 41(1):8-18. PubMed ID: 19386237 [TBL] [Abstract][Full Text] [Related]
2. GAP43 overexpression and enhanced neurite outgrowth in mucopolysaccharidosis type IIIB cortical neuron cultures. Hocquemiller M; Vitry S; Bigou S; Bruyère J; Ausseil J; Heard JM J Neurosci Res; 2010 Jan; 88(1):202-13. PubMed ID: 19658197 [TBL] [Abstract][Full Text] [Related]
3. Modeling neuronal defects associated with a lysosomal disorder using patient-derived induced pluripotent stem cells. Lemonnier T; Blanchard S; Toli D; Roy E; Bigou S; Froissart R; Rouvet I; Vitry S; Heard JM; Bohl D Hum Mol Genet; 2011 Sep; 20(18):3653-66. PubMed ID: 21685203 [TBL] [Abstract][Full Text] [Related]
4. Mouse model of Sanfilippo syndrome type B: relation of phenotypic features to background strain. Gografe SI; Garbuzova-Davis S; Willing AE; Haas K; Chamizo W; Sanberg PR Comp Med; 2003 Dec; 53(6):622-32. PubMed ID: 14727810 [TBL] [Abstract][Full Text] [Related]
5. Retrovirally transduced bone marrow has a therapeutic effect on brain in the mouse model of mucopolysaccharidosis IIIB. Zheng Y; Ryazantsev S; Ohmi K; Zhao HZ; Rozengurt N; Kohn DB; Neufeld EF Mol Genet Metab; 2004 Aug; 82(4):286-95. PubMed ID: 15308126 [TBL] [Abstract][Full Text] [Related]
6. Attenuated plasticity in neurons and astrocytes in the mouse model of Sanfilippo syndrome type B. Li HH; Zhao HZ; Neufeld EF; Cai Y; Gómez-Pinilla F J Neurosci Res; 2002 Jul; 69(1):30-8. PubMed ID: 12111813 [TBL] [Abstract][Full Text] [Related]
7. Molecular genetics of mucopolysaccharidosis type IIIA and IIIB: Diagnostic, clinical, and biological implications. Yogalingam G; Hopwood JJ Hum Mutat; 2001 Oct; 18(4):264-81. PubMed ID: 11668611 [TBL] [Abstract][Full Text] [Related]
8. Intravenous administration of human umbilical cord blood cells in an animal model of MPS III B. Garbuzova-Davis S; Klasko SK; Sanberg PR J Comp Neurol; 2009 Jul; 515(1):93-101. PubMed ID: 19399896 [TBL] [Abstract][Full Text] [Related]
9. Short-term enzyme replacement in the murine model of Sanfilippo syndrome type B. Yu WH; Zhao KW; Ryazantsev S; Rozengurt N; Neufeld EF Mol Genet Metab; 2000 Dec; 71(4):573-80. PubMed ID: 11136549 [TBL] [Abstract][Full Text] [Related]
10. Lysosomal storage of heparan sulfate causes mitochondrial defects, altered autophagy, and neuronal death in the mouse model of mucopolysaccharidosis III type C. Pshezhetsky AV Autophagy; 2016 Jun; 12(6):1059-60. PubMed ID: 25998837 [TBL] [Abstract][Full Text] [Related]
11. Neurodevelopmental Changes in Excitatory Synaptic Structure and Function in the Cerebral Cortex of Sanfilippo Syndrome IIIA Mice. Dwyer CA; Scudder SL; Lin Y; Dozier LE; Phan D; Allen NJ; Patrick GN; Esko JD Sci Rep; 2017 Apr; 7():46576. PubMed ID: 28418018 [TBL] [Abstract][Full Text] [Related]
12. Neuropathology in mouse models of mucopolysaccharidosis type I, IIIA and IIIB. Wilkinson FL; Holley RJ; Langford-Smith KJ; Badrinath S; Liao A; Langford-Smith A; Cooper JD; Jones SA; Wraith JE; Wynn RF; Merry CL; Bigger BW PLoS One; 2012; 7(4):e35787. PubMed ID: 22558223 [TBL] [Abstract][Full Text] [Related]
13. Central nervous system pathology in preclinical MPS IIIB dogs reveals progressive changes in clinically relevant brain regions. Egeland MT; Tarczyluk-Wells MM; Asmar MM; Adintori EG; Lawrence R; Snella EM; Jens JK; Crawford BE; Wait JCM; McCullagh E; Pinkstaff J; Cooper JD; Ellinwood NM Sci Rep; 2020 Nov; 10(1):20365. PubMed ID: 33230178 [TBL] [Abstract][Full Text] [Related]
14. Improved behavior and neuropathology in the mouse model of Sanfilippo type IIIB disease after adeno-associated virus-mediated gene transfer in the striatum. Cressant A; Desmaris N; Verot L; Bréjot T; Froissart R; Vanier MT; Maire I; Heard JM J Neurosci; 2004 Nov; 24(45):10229-39. PubMed ID: 15537895 [TBL] [Abstract][Full Text] [Related]
15. Early neurodegeneration progresses independently of microglial activation by heparan sulfate in the brain of mucopolysaccharidosis IIIB mice. Ausseil J; Desmaris N; Bigou S; Attali R; Corbineau S; Vitry S; Parent M; Cheillan D; Fuller M; Maire I; Vanier MT; Heard JM PLoS One; 2008 May; 3(5):e2296. PubMed ID: 18509511 [TBL] [Abstract][Full Text] [Related]
16. A prospective one-year natural history study of mucopolysaccharidosis types IIIA and IIIB: Implications for clinical trial design. Truxal KV; Fu H; McCarty DM; McNally KA; Kunkler KL; Zumberge NA; Martin L; Aylward SC; Alfano LN; Berry KM; Lowes LP; Corridore M; McKee C; McBride KL; Flanigan KM Mol Genet Metab; 2016 Nov; 119(3):239-248. PubMed ID: 27590925 [TBL] [Abstract][Full Text] [Related]
17. Mouse model of Sanfilippo syndrome type B produced by targeted disruption of the gene encoding alpha-N-acetylglucosaminidase. Li HH; Yu WH; Rozengurt N; Zhao HZ; Lyons KM; Anagnostaras S; Fanselow MS; Suzuki K; Vanier MT; Neufeld EF Proc Natl Acad Sci U S A; 1999 Dec; 96(25):14505-10. PubMed ID: 10588735 [TBL] [Abstract][Full Text] [Related]
18. Interaction assays in yeast and cultured cells confirm known and identify novel partners of the synaptic vesicle protein synaptophysin. Felkl M; Leube RE Neuroscience; 2008 Oct; 156(2):344-52. PubMed ID: 18706977 [TBL] [Abstract][Full Text] [Related]
19. Oxidative stress is independent of inflammation in the neurodegenerative Sanfilippo syndrome type B. Trudel S; Trécherel E; Gomila C; Peltier M; Aubignat M; Gubler B; Morlière P; Heard JM; Ausseil J J Neurosci Res; 2015 Mar; 93(3):424-32. PubMed ID: 25332157 [TBL] [Abstract][Full Text] [Related]
20. Examination of intravenous and intra-CSF protein delivery for treatment of neurological disease. Hemsley KM; Luck AJ; Crawley AC; Hassiotis S; Beard H; King B; Rozek T; Rozaklis T; Fuller M; Hopwood JJ Eur J Neurosci; 2009 Mar; 29(6):1197-214. PubMed ID: 19302155 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]